Version 2.78

Part Descriptions

LP14022-5   Beta-N-acetylhexosaminidase
An enzyme hydrolyzing terminal non-reducing N-acetyl-D-hexosamine residues in N-acetyl-beta-D-hexosaminides. It acts on GLUCOSIDES; GALACTOSIDES; and several OLIGOSACCHARIDES. Hexosaminidase A cleaves GM2, GA2, globosides, and hexosamine oligosaccharides. Hexosaminidase B cleaves all the above substrates except GM2. Deficiency of Hexosaminidase A causes TAY-SACHS DISEASE, while deficiency of both A and B isozymes causes SANDHOFF DISEASE. The enzyme has also been used as a tumor marker to distinguish between malignant and benign disease. Source: National Library of Medicine, MeSH 2006

LP14022-5   Beta-N-acetylhexosaminidase
Beta-N-acetylhexosaminidase is also known as hexosaminidase and has two forms, A and B. Hexosaminidase B is used to screen for Tay-Sachs disease. Source: Regenstrief Institute

Fully-Specified Name

Component
Beta-N-acetylhexosaminidase
Property
CCnc
Time
Pt
System
Platelets
Scale
Qn
Method

Additional Names

Short Name
B-NAH Plts-cCnc
Display Name
Beta-N-acetylhexosaminidase (Plts) [Catalytic activity/Vol]
Consumer Name Alpha Get Info
Beta-N-acetylhexosaminidase, Platelets

Basic Attributes

Class
CHEM
Type
Laboratory
First Released
Version 1.0l
Last Updated
Version 2.73
Order vs. Observation
Both
Common Test Rank Get Info
18074

Language Variants Get Info

Tag Language Translation
es-AR Spanish (Argentina) beta-N-acetilhexosaminidasa:concentración catalítica:punto en el tiempo:plaquetas:cuantitativo:
es-ES Spanish (Spain) Beta-N-acetilhexosaminidasa:Concentración Catalítica:Punto temporal:Plaquetas:Qn:
Synonyms: Cuantitativo
es-MX Spanish (Mexico) Beta-N-acetilhexosaminidasa:Concentración catalítica:Punto temporal:Plaquetas:Cuantitativo:
et-EE Estonian (Estonia) Beeta-N-atsetüülheksosaminidaas:CCnc:Pt:PLT:Qn:
Synonyms: Juhuslik Kvantitatiivne Trombotsüüdid
fr-CA French (Canada) Bêta-N-acétylhexosaminidase:Concentration catalytique:Temps ponctuel:Plaquettes:Quantitatif:
fr-FR French (France) Bêta N-hexosaminidase:Catalytique/Volume:Ponctuel:Plaquettes:Numérique:
fr-BE French (Belgium) Béta-N-acétylhexosaminidase:Concentration catalytique:Temps ponctuel:Plaquettes:Quantitatif:
it-IT Italian (Italy) Beta-N-acetilesosaminidasi:CCnC:Pt:Piastrine:Qn:
Synonyms: Chimica Concentrazione Catalitica Punto nel tempo (episodio) Trombociti
ko-KR Korean (Korea, Republic Of) 베타-N-아세틸헥소스아미니다아제:촉매농도:검사시점:혈소판:정량:
nl-NL Dutch (Netherlands) bèta-N-acetylhexosaminidase:enzymatische activiteit/volume:moment:trombocyten:kwantitatief:
Synonyms: Beta-N-acetylhexosaminidase plaatjes; bloedplaatjes
pt-BR Portuguese (Brazil) Beta-N-acetilhexosaminidase:CCnc:Pt:Plaquetas:Qn:
Synonyms: ; B-NAH; GM2-gangliosidosis; Hexosaminidase; Catalytic Concentration; Point in time; Random; Thrb; Plt; Platelet; Thrombocytes; Thrombocyte; Quantitative; QNT; Quant; Quan; B; Chemistry
ru-RU Russian (Russian Federation) Бета-N-ацетилгексозаминидаза:КаталКонц:ТчкВрм:Пластинки:Колич:
Synonyms: Каталитическая концентрация Количественный Точка во времени;Момент Тромбоциты
tr-TR Turkish (Turkey) Beta-N-asetilhekzosaminidaz:KtlKons:Zmlı:Trombositler:Kant:
zh-CN Chinese (China) Beta-N-乙酰己糖胺酶:催化浓度:时间点:血小板:定量型:
Synonyms: B Beta-N-乙酰氨基己糖苷酶;B-NAH;GM2-神经节苷脂沉积症;GM2-神经节苷脂贮积病;β-N-乙酰己糖胺酶;β-N-乙酰氨基己糖苷酶;己糖胺酶;氨基己糖苷酶 N 型 β 催化浓度(单位体积);单位体积内酶的单位数 凝血细胞;血栓细胞;血小板类 化学;化学检验项目;化学检验项目类;化学类;化学试验;非刺激耐受型化学检验项目;非刺激耐受型化学检验项目类;非刺激耐受型化学试验;非刺激耐受型化学试验类 可用数量表示的;定量性;数值型;数量型;连续数值型标尺 时刻;随机;随意;瞬间 贝塔

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CodeSystem lookup
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