2444-8
Hydroxymethylglutaryl CoA lyase [Enzymatic activity/volume] in Serum
Active
Part Description
LP15649-4 Hydroxymethylglutaryl CoA lyase
Hydroxymethylglutaryl CoA lyase deficiency (HMG; also known as 3-hydroxy-3-methylglutaryl-coenzyme A lyase deficiency and 3-Hydroxy-3-methylglutaric aciduria) is an inherited disorder in which the body is unable to process the amino acid leucine or make ketones properly. Within the first year of life, this condition causes episodes of vomiting, diarrhea, dehydration, lethargy, hypotonia, hypoglycemia, and metabolic acidosis. If untreated, this disorder can lead to breathing problems, convulsions, coma, and death. HMG deficiency is caused by mutations in the HMGCL gene and has an autosomal recessive pattern of inheritance.
Source: Regenstrief LOINC
Fully-Specified Name
- Component
- Hydroxymethylglutaryl CoA lyase
- Property
- CCnc
- Time
- Pt
- System
- Ser
- Scale
- Qn
- Method
Additional Names
- Long Common Name
- Hydroxymethylglutaryl CoA lyase [Enzymatic activity/volume] in Serum
- Short Name
- HMG-CoA Lyase Ser-cCnc
- Display Name
- Hydroxymethylglutaryl CoA lyase (S) [Catalytic activity/Vol]
- Consumer Name Alpha Get Info
- Hydroxymethylglutaryl coA lyase, Blood
Basic Attributes
- Class
- CHEM
- Type
- Laboratory
- First Released
- Version 1.0
- Last Updated
- Version 2.68 (MIN)
- Order vs. Observation
- Both
Language Variants Get Info
Tag | Language | Translation |
---|---|---|
el-GR | Greek (Greece) | Υδροξυ-μεθυλο-γλουτάρυλο-CoA λυάση: Synonyms: CCnc |
es-AR | Spanish (Argentina) | hidroximetilglutaril CoA liasa: |
es-ES | Spanish (Spain) | Hidroximetilglutaril CoA liasa: Synonyms: Cuantitativo |
es-MX | Spanish (Mexico) | Hidroximetilglutaril CoA liasa: |
fr-CA | French (Canada) | Hydroxymethylglutaryl-CoA lyase: |
fr-FR | French (France) | Hydroxyméthylglutaryl CoA lyase: |
fr-BE | French (Belgium) | Hydroxymethylglutaryl-CoA lyase: |
it-IT | Italian (Italy) | Idrossimetilglutaril CoA liasi: Synonyms: Chimica Concentrazione Catalitica Punto nel tempo (episodio) Siero |
ko-KR | Korean (Korea, Republic Of) | 하이드록시메틸글루타릴 CoA 분해효소: |
nl-NL | Dutch (Netherlands) | hydroxymethylglutaryl-CoA-lyase: |
pt-BR | Portuguese (Brazil) | Hidroximetilglutaril CoA liase: Synonyms: ; |
ru-RU | Russian (Russian Federation) | Гидроксиметилглутарил КоА лиаза: Synonyms: Гидроксиметилглутарил-КоА-лиаза; |
tr-TR | Turkish (Turkey) | Hidroksimetilglutaril KoA liyaz: |
zh-CN | Chinese (China) | 羟甲基戊二酰 CoA 裂解酶: Synonyms: 3-羟基-3-甲基戊二酰 CoA 裂解酶; |
Example Units
Unit | Source |
---|---|
U/L | Example UCUM Units |
LOINC Terminology Service (API) using HL7® FHIR® Get Info
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- CodeSystem lookup
- https:
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