Part Descriptions

LP15432-5   Beta aminoisobutyrate
3-Aminoisobutyric acid is a product formed by the catabolism of thymine. Copyright Text is available under the Creative Commons Attribution/Share-Alike License. See http://creativecommons.org/licenses/by-sa/3.0/ for details. Source: Wikipedia, Wikipedia

LP15432-5   Beta aminoisobutyrate
Beta aminoisobutyric acid (BAIB) is a nonprotein amino acid that is an end product of pyrimidine metabolism. The R and S enantiomers (previously named D-(minus)-BAIB and L-plus-BAIB) are produced from thymine and L-valine, respectively. Under normal circumstances, urine contains predominantly R-BAIB (from thymine) because it is eliminated by filtration and tubular secretion, while plasma contains about 80% S-BAIB (from valine), which is reabsorbed in the kidneys. In patients with dihydropyrimidine dehydrogenase deficiency, thymine catabolism is decreased, which results in moderately decreased CSF concentration and markedly decreased plasma concentration of BAIB. On the other hand, urine BAIB is elevated despite decreased breakdown of thymine, which indicates that there must be cross-over in the thymine and valine degradation pathways. PMID: 14705962 Deficiency of D-beta-aminoisobutyrate:pyruvate aminotransferase (EC 2.6.1.40) , an enzyme that is involved in the catabolism R-BAIB, also results in elevated urine BAIB and is associated with hyperuricemia. [OMIM: 210100] Source: Regenstrief LOINC, PMID: 14705962

LOINC Names Get Info

Fully-Specified Name
Beta aminoisobutyrate:SCnc:24H:Urine:Qn:
Long Common Name
Beta aminoisobutyrate [Moles/volume] in 24 hour Urine
Short Name
B-AIB 24h Ur-sCnc
Display Name
Beta aminoisobutyrate (24H U) [Moles/Vol]
Consumer Name Alpha Get Info
Beta aminoisobutyrate, Urine

Part Model Get Info

  • Component
    Beta aminoisobutyrate
    LP15432-5
    • Analyte
      Beta aminoisobutyrate
      LP15432-5
      • Component Numerator
        Beta aminoisobutyrate
        LP15432-5
        • Component Numerator Core
          Beta aminoisobutyrate
          LP15432-5
        • Component Numerator Core Suffix
          NULL
           
      • Component Denominator
        NULL
         
        • Component Denominator Core
          NULL
           
        • Component Denominator Core Suffix
          NULL
           
    • Challenge
      NULL
       
    • Adjustment
      NULL
       
    • Count
      NULL
       
  • Property
    SCnc
    LP6860-3
  • Time
    24H
    LP6924-7
  • System
    Urine
    LP7681-2
    • System Core
      Urine
      LP7681-2
    • Super System
      NULL
       
  • Scale
    Qn
    LP7753-9
  • Method
    NULL
     

Basic Attributes

Class
CHEM
Type
Laboratory
First Released
Version 2.00
Last Updated
Version 2.42 (MIN)
Order vs. Observation
Observation

Member of these Groups Get Info

LOINC GroupGroup Name
LG35423-9Beta aminoisobutyrate|SCnc|Urine

Language Variants Get Info

TagLanguageTranslation
cs-CZCzech (Czechia)Beta-aminoizobutyrát:Látková koncentrace:24 hodin:Moč:Kvantitativní:
el-GRGreek (Greece)β-αμινοϊσοβουτυρικό:SCnc:24H:Ούρα:Qn:
Synonyms: 24H CHEM Qn SCnc β-αμινοϊσοβουτυρικό Ούρα
es-ARSpanish (Argentina)beta aminoisobutirato:concentración de sustancia:24 horas:orina:cuantitativo:
es-ESSpanish (Spain)Beta aminoisobutirato:Concentración de sustancia:24 horas:Orina:Qn:
Synonyms: Cuantitativo
es-MXSpanish (Mexico)Beta aminoisobutirato:Concentración de sustancias:24H:Orina:Cuantitativo:
et-EEEstonian (Estonia)Beetaaminoisobutüraat:SCnc:24 tunni:U:Qn:
Synonyms: Aine kontsentratsioon Kvantitatiivne Uriin
fr-CAFrench (Canada)Bêta-aminoisobutyrate:Concentration de substance:24 h:Urine:Quantitatif:
fr-FRFrench (France)Bêta aminoisobutyrate:Moles/Volume:24H:Urine:Numérique:
fr-BEFrench (Belgium)Béta-aminoisobutyrate:Concentration de substance:24 h:Urine:Quantitatif:
it-ITItalian (Italy)Beta aminoisobutirrato:SCnc:24h:Urine:Qn:
Synonyms: 24 Ore Chimica Concentrazione di Sostanza
ko-KRKorean (Korea, Republic Of)베타 아미노이소뷰티레이트:물질농도:24시간:뇨:정량:
nl-NLDutch (Netherlands)bèta-amino-isobutyraat:mol/volume:24 uur:urine:kwantitatief:
Synonyms: 24U
pl-PLPolish (Poland)Beta aminoizomaślan:stężenie molowe:24h:mocz:ilościowy:
Synonyms: 24 godziny
pt-BRPortuguese (Brazil)Beta aminoisobutirato:SCnc:24H:Urina:Qn:
Synonyms: ; B-AIB; 3-aminoisobutyrate; 3-aminoisobutyric acid; Substance concentration; Level; 1 day; 24 hours; 24HR; Ur; UR; Urn; UA; Quantitative; QNT; Quant; Quan; B; Chemistry
ru-RURussian (Russian Federation)Бета аминоизобутират:МолКонц:24 часа:Моча:Колич:
Synonyms: Бета-аминоизобутират Количественный Молярность;Молярная объёмная концентрация
tr-TRTurkish (Turkey)Beta aminoizobütirat:SubKons:24Sa:İdrar:Kant:
zh-CNChinese (China)Beta 氨基异丁酸:物质的量浓度:24小时:尿液:定量型:
Synonyms: 1天;1日;24.0小时;一天;一日;二十四个小时;二十四小时 3-氨基异丁酸;B-AIB;Beta-氨基异丁酸;β氨基异丁酸;β-氨基异丁酸 B β 克分子浓度;克分子浓度(单位体积);摩尔浓度;摩尔浓度(单位体积);物质的量浓度(单位体积) 化学;化学检验项目;化学检验项目类;化学类;化学试验;非刺激耐受型化学检验项目;非刺激耐受型化学检验项目类;非刺激耐受型化学试验;非刺激耐受型化学试验类 可用数量表示的;定量性;数值型;数量型;连续数值型标尺 尿;小便;下泉 贝塔

Example Units

UnitSource
nmol/mLExample UCUM Units

LOINC Terminology Service (API) using HL7® FHIR® Get Info

CodeSystem lookup
https://fhir.loinc.org/CodeSystem/$lookup?system=http://loinc.org&code=25870-7