Version 2.80

Part Description

LP15810-2   Porphobilinogen deaminase
Porphobilinogen (PBG) deaminase testing is used in the diagnosis of acute intermittent porphyria. Source: Regenstrief Institute

Fully-Specified Name

Component
Porphobilinogen deaminase
Property
CCnt
Time
Pt
System
RBC
Scale
Qn
Method

Additional Names

Long Common Name
Porphobilinogen deaminase [Enzymatic activity/mass] in Red Blood Cells
Short Name
PBG Deaminase RBC-cCnt
Display Name
Porphobilinogen deaminase (RBC) [Catalytic activity/Mass]
Consumer Name Alpha Get Info
Porphobilinogen deaminase, Red blood cells

Basic Attributes

Class
CHEM
Type
Laboratory
First Released
Version 2.21
Last Updated
Version 2.73 (MIN)
Order vs. Observation
Both
Common Test Rank Get Info
7975

Language Variants Get Info

Tag Language Translation
el-GR Greek (Greece) Δεαμινάση πορφοχολινογόνου:CCnt:Pt:Ερυθρά αιμοσφαίρια:Qn:
Synonyms: CCnt Δεαμινάση πορφοχολινογόνου Πορφοχολινογόνο
es-ES Spanish (Spain) Porfobilinogeno desaminasa:Contenido catalítico:Punto temporal:Glóbulos rojos:Qn:
Synonyms: Cuantitativo
es-MX Spanish (Mexico) Desaminasa de porfobilinógeno:Contenido catalítico:Punto temporal:Eritrocitos:Cuantitativo:
et-EE Estonian (Estonia) Porfobilinogeeni deaminaas:CCnt:Pt:RBC:Qn:
Synonyms: Erütrotsüüdid Juhuslik Kvantitatiivne
fr-CA French (Canada) Porphobilinogène-désaminase:Contenu catalytique:Temps ponctuel:GR:Quantitatif:
fr-FR French (France) Porphobilinogène déaminase:Catalytique/Masse:Ponctuel:Érythrocytes:Numérique:
fr-BE French (Belgium) Porphobilinogène-désaminase:Contenu catalytique:Temps ponctuel:GR:Quantitatif:
it-IT Italian (Italy) Porfobilinogeno deaminasi:CCnt:Pt:RBC:Qn:
Synonyms: Chimica Contenuto Catalitico Globuli rossi Punto nel tempo (episodio)
nl-NL Dutch (Netherlands) porfobilinogeendeaminase:enzymatische activiteit/massa:moment:erytrocyten:kwantitatief:
Synonyms: rode bloedcellen
pt-BR Portuguese (Brazil) Porfobilinogênio deaminase:CCnt:Pt:Eritroc:Qn:
Synonyms: ; PBG Deaminase; Hydroxymethylbilane Synthase; Uroporphyrinogen I Synthase; PBG-D; Porphoblngn; Porpoblngn; Porph; Porphobili; Catalytic Content; Point in time; Random; Erythrocytes; Red blood corpusles; Red blood cells; Quantitative; QNT; Quant; Quan; Chemistry
ru-RU Russian (Russian Federation) Порфобилиноген деаминаза:КаталСод:ТчкВрм:Эритроциты:Колич:
Synonyms: Каталитическое содержание Количественный Порфобилиноген дезаминаза Точка во времени;Момент
tr-TR Turkish (Turkey) Porfobilinojen deaminaz:Ktlİçrk:Zmlı:Eritrosit:Kant:
Synonyms: RBC
uk-UA Ukrainian (Ukraine) Порфобіліноген дезаміназа:Каталітичний Вміст:МоментЧасу:Еритроцити:Кількісно:
Synonyms: Catalytic Content; Chemistry; Erythrocytes; Hematology; Heme; Hydroxymethylbilane Synthase; PBG; PBG Deaminase; PBGD; PBG-D; Point in time; Porph; Porphobili; Porphoblngn; Porpoblngn; QNT; Quan; Quant; Quantitative; Random; Red blood cells; Red blood corpusles; Uroporphyrinogen I Synthase
zh-CN Chinese (China) 胆色素原脱氨酶:催化含量:时间点:红细胞:定量型:
Synonyms: PBG Deaminase;PBG 脱氨酶;PBG-D;尿卟啉原 I 合酶;羟甲基胆色烷合酶;胆色素脱色氨酶 PBG;Porph;卟吩胆色素原;胆素原 RBC;RBCS;红血球;红血细胞;赤血球 催化含量(单位质量);单位质量的酶单位数 化学;化学检验项目;化学检验项目类;化学类;化学试验;非刺激耐受型化学检验项目;非刺激耐受型化学检验项目类;非刺激耐受型化学试验;非刺激耐受型化学试验类 可用数量表示的;定量性;数值型;数量型;连续数值型标尺 时刻;随机;随意;瞬间

Example Units

Unit Source
mU/g{Hb} Example UCUM Units
mUnits/g Hgb REGENSTRIEF

LOINC Terminology Service (API) using HL7® FHIR® Get Info

CodeSystem lookup
https://fhir.loinc.org/CodeSystem/$lookup?system=http://loinc.org&code=49228-0