Term Description

Propionylcarnitine/Carnitine.free is a secondary marker for Propionic acidemia, Methylmalonic acidemia (mut), Methylmalonic acidemia (Cbl A, B), Methylmalonic aciduria and homocystinuria, Succinyl-CoA ligase deficiency, and Multiple carboxylase deficiency.
Source: Regenstrief LOINC

Part Descriptions

LP19303-4   Propionylcarnitine (C3)
Propionylcarnitine is a primary marker for Propionic acidemia, Methylmalonic acidemia (mut), Methylmalonic acidemia (Cbl A, B), Methylmalonic aciduria and homocystinuria, and Succinyl-CoA ligase deficiency. Secondary marker for Multiple carboxylase deficiency. Source: Regenstrief LOINC

LP32015-7   Carnitine.free (C0)
Carnitine.free is a primary marker for carnitine uptake defect, propionic acidemia, maternal carnitine uptake defect, carnitine palmitoyltransferase I deficiency and primary lactic acidemia (various types). It is also a secondary marker for maternal glutaric acidemia type I. Source: Regenstrief LOINC

LOINC Names Get Info

Fully-Specified Name
Propionylcarnitine (C3)/Carnitine.free (C0):SRto:Pt:Bld.dot:Qn:
Long Common Name
Propionylcarnitine (C3)/Carnitine.free (C0) [Molar ratio] in DBS
Short Name
Propionylcarn/C0 DBS-sRto
Display Name
C3/Carnitine.free (C0) (DBS) [Molar ratio]
Consumer Name Alpha Get Info
C3/Free Carnitine (C0), Dried blood spot

Part Model Get Info

  • Component
    Propionylcarnitine (C3)/Carnitine.free (C0)
    LP286918-0
    • Analyte
      Propionylcarnitine (C3)/Carnitine.free (C0)
      LP286918-0
      • Component Numerator
        Propionylcarnitine (C3)
        LP19303-4
        • Component Numerator Core
          Propionylcarnitine (C3)
          LP19303-4
        • Component Numerator Core Suffix
          NULL
           
      • Component Denominator
        Carnitine.free (C0)
        LP32015-7
        • Component Denominator Core
          Carnitine.free (C0)
          LP32015-7
        • Component Denominator Core Suffix
          NULL
           
    • Challenge
      NULL
       
    • Adjustment
      NULL
       
    • Count
      NULL
       
  • Property
    SRto
    LP6868-6
  • Time
    Pt
    LP6960-1
  • System
    Bld.dot
    LP21304-8
    • System Core
      Bld.dot
      LP21304-8
    • Super System
      NULL
       
  • Scale
    Qn
    LP7753-9
  • Method
    NULL
     

Basic Attributes

Class
CHEM
Type
Laboratory
First Released
Version 2.24
Last Updated
Version 2.73 (MIN)
Order vs. Observation
Both

Member of these Panels

LOINCLong Common Name
58092-8Acylcarnitine newborn screen panel
53262-2Carnitine newborn screen panel
54089-8Newborn screening panel American Health Information Community (AHIC)

Language Variants Get Info

TagLanguageTranslation
cs-CZCzech (Czechia)Propionylkarnitin (C3)/karnitin.volný (C0):Látkový poměr:Časový bod:Suchá krevní kapka (DBS):Kvantitativní:
el-GRGreek (Greece)Προπιονυλ-L-καρνιτίνη (C3)/Καρνιτίνη.ελεύθερη (C0):SRto:Pt:Bld.dot:Qn:
Synonyms: Bld.dot CHEM Pt Qn SRto Αίμα Καρνιτίνη Καρνιτίνη.ελεύθερη (C0) Προπιονυλ-L-καρνιτίνη (C3)
es-ESSpanish (Spain)Propionilcarnitina (C3)/Carnitina libre:Relacion de Sustancia:Punto temporal:gota de sangre (papel de filtro):Qn:
Synonyms: Cuantitativo
es-MXSpanish (Mexico)Propionilcarnitina (C3) / Carnitina.libre (C0):Proporción de sustancia:Punto temporal:DBS:Cuantitativo:
fr-CAFrench (Canada)Propionylcarnitine (C3)/Carnitine.libre (C0):Ratio de substance:Temps ponctuel:Sang sur papier filtre:Quantitatif:
fr-FRFrench (France)Propionylcarnitine (C3)/carnitine libre (C0):Moles ratio:Ponctuel:Sang buvard:Numérique:
fr-BEFrench (Belgium)Propionylcarnitine (C3)/Carnitine.libre (C0):Ratio de substance:Temps ponctuel:Sang sur papier filtre:Quantitatif:
it-ITItalian (Italy)Propionilcarnitina (C3)/Carnitina.libera (C0):Srto:Pt:Sangue.su carta da filtro:Qn:
Synonyms: Carnitina libera (C0) Chimica Punto nel tempo (episodio) Rapporto di sostanza Sangue Spot sangue secco
nl-NLDutch (Netherlands)propionylcarnitine (C3)/carnitine.vrij (C0):molaire verhouding:moment:gedroogde bloedspot:kwantitatief:
pt-BRPortuguese (Brazil)Propionilcarnitina (C3)/Carnitina.livre (C0):SCrto:Pt:SgPapel:Qn:
Synonyms: ; Propionylcarn; Propanoylcarnitine; C3-carntitine; sRto; Substance concentration ratio; Point in time; Random; DBS; Filter paper; FP; Dried blood spot; Blood; WB; Whole blood; Quantitative; QNT; Quant; Quan; FR; Non-protein bound; Chemistry
ru-RURussian (Russian Federation)Пропионилкарнитин (C3)/Карнитин.свободный(С0):МольОтн:ТчкВрм:Кр.Сух.капл:Колич:
Synonyms: Количественный Кровь Кровь сухая капля Мольная доля;Молярная доля;Отношение концентраций Точка во времени;Момент
tr-TRTurkish (Turkey)Propiyonilkarnitin (C3)/Karnitin.serb (C0):SOrn:Zmlı:Kan.nokta:Kant:
Synonyms: SubsOranı
zh-CNChinese (China)丙酰肉碱 (C3)/肉碱.游离型 (C0):物质的量比率:时间点:全血.斑点:定量型:
Synonyms: 丙酰肉碱(肉毒碱、三甲基羟基丁酰甜菜碱、卡尼丁) (C3);C3;C3-肉碱;丙酰基肉碱;丙酰肉碱, C3 全血斑点(滤纸);滤纸;血液.斑点;血液斑点(滤纸) 化学;化学检验项目;化学检验项目类;化学类;化学试验;非刺激耐受型化学检验项目;非刺激耐受型化学检验项目类;非刺激耐受型化学试验;非刺激耐受型化学试验类 可用数量表示的;定量性;数值型;数量型;连续数值型标尺 时刻;随机;随意;瞬间 游离 物质的量比值;物质的量比;摩尔比;摩尔比率;摩尔比值 肉碱(肉毒碱、三甲基羟基丁酰甜菜碱、卡尼丁).游离型 (C0);肉毒碱.游离型 (C0) 肉碱(肉毒碱、三甲基羟基丁酰甜菜碱、卡尼丁).游离型 (C0);肉毒碱.游离型 (C0);三甲基羟基丁酰甜菜碱.游离型 (C0);游离三甲基羟基丁酰甜菜碱 (C0);游离型三甲基羟基丁酰甜菜碱 (C0);游离型肉毒碱 (C0);游离型肉碱 (C0);游离肉毒碱 (C0);游离肉碱 (C0);肉碱.游离型 (C0) 肉碱(肉毒碱、三甲基羟基丁酰甜菜碱、卡尼丁);三甲基羟基丁酰甜菜碱;卡尼丁;总肉毒碱;总肉碱;肉毒碱;肉毒碱.总;肉毒碱.总计;肉碱.总;肉碱.总计 血;血液 非蛋白结合型 非蛋白质结合型

Example Units

UnitSource
{Ratio}Example UCUM Units

LOINC Terminology Service (API) using HL7® FHIR® Get Info

CodeSystem lookup
https://fhir.loinc.org/CodeSystem/$lookup?system=http://loinc.org&code=53162-4