Version 2.78

24437-6 Butyrylglycine/Creatinine [Molar ratio] in Urine

Part Descriptions

LP32035-5   Creatinine
Creatinine or creatine anhydride, is a breakdown product of creatine phosphate in muscle. The loss of water molecule from creatine results in the formation of creatinine. It is transferred to the kidneys by blood plasma, whereupon it is eliminated by glomular filtration and partial tubular excretion. Creatinine is usually produced at a fairly constant rate and measuring its serum level is a simple test. A rise in blood creatinine levels is observed only with marked damage to functioning nephrons; therefore this test is not suitable for detecting early kidney disease. Creatine and creatinine are metabolized in the kidneys, muscle, liver and pancreas. Copyright Copyright ©2005-2009 Genome Alberta (Reference to original publication: Wishart DS, Knox C, Guo AC, et al. HMDB: a knowledgebase for the human metabolome. Nucleic Acids Res. 2009 37(Database issue):D603-610.) Source: Human Metabolome Database, Creatinine

Fully-Specified Name

Component
Butyrylglycine/Creatinine
Property
SRto
Time
Pt
System
Urine
Scale
Qn
Method

Additional Names

Short Name
Butyrylgly/Creat Ur-sRto
Display Name
Butyrylglycine/Creatinine (U) [Molar ratio]
Consumer Name Alpha Get Info
Butyrylglycine/Creatinine, Urine

Basic Attributes

Class
CHEM
Type
Laboratory
First Released
Version 1.0o
Last Updated
Version 2.73
Order vs. Observation
Observation
Common Test Rank Get Info
9210

Member of these Panels

LOINC Long Common Name
74914-3 Acylglycines panel [Molar ratio] - Urine

Language Variants Get Info

Tag Language Translation
es-AR Spanish (Argentina) butiriloglicina/creatinina:relación de concentración de la sustancia:punto en el tiempo:orina:cuantitativo:
es-ES Spanish (Spain) Butirilglicina/Creatinina:Relacion de Sustancia:Punto temporal:Orina:Qn:
Synonyms: Cuantitativo
es-MX Spanish (Mexico) Butirilglicina / Creatinina:Proporción de sustancia:Punto temporal:Orina:Cuantitativo:
fr-CA French (Canada) Butyrylglycine/Créatinine:Ratio de substance:Temps ponctuel:Urine:Quantitatif:
fr-FR French (France) Butyrylglycine/créatinine:Moles ratio:Ponctuel:Urine:Numérique:
fr-BE French (Belgium) Butyrylglycine/Créatinine:Ratio de substance:Temps ponctuel:Urine:Quantitatif:
it-IT Italian (Italy) Butirrilglicina/Creatinina:Srto:Pt:Urine:Qn:
Synonyms: Chimica Punto nel tempo (episodio) Rapporto di sostanza
ko-KR Korean (Korea, Republic Of) 부티릴글리신/크레아티닌:물질구성비:검사시점:뇨:정량:
nl-NL Dutch (Netherlands) butyrylglycine/creatinine:molaire verhouding:moment:urine:kwantitatief:
Synonyms: kreatinine
pt-BR Portuguese (Brazil) Butirilglicina/Creatinina:SCrto:Pt:Urina:Qn:
Synonyms: ; Butyrylgly; Creat; CR; sRto; Substance concentration ratio; Point in time; Random; Ur; UR; Urn; UA; Quantitative; QNT; Quant; Quan; Chemistry; UCr
ru-RU Russian (Russian Federation) Бутирилглицин/Креатинин:МольОтн:ТчкВрм:Моча:Колич:
Synonyms: Количественный Мольная доля;Молярная доля;Отношение концентраций Точка во времени;Момент
tr-TR Turkish (Turkey) Bütirilglisin/Kreatinin:SOrn:Zmlı:İdrar:Kant:
Synonyms: SubsOranı
uk-UA Ukrainian (Ukraine) Бутирилгліцин/Креатинін:Молярне Співвідношення:МоментЧасу:Сеча:Кількісно:
Synonyms: Chemistry; CR; Crea; Creat; Point in time; QNT; Quan; Quant; Quantitative; Random; Scrto; Substance concentration ratio; Substance ratio; UA; UCr; UR; Urn
zh-CN Chinese (China) 丁酰甘氨酸/肌酐:物质的量比率:时间点:尿液:定量型:
Synonyms: CR;Creat;肌氨酸酐;肌酸内酰胺;肌酸酐 UCr 化学;化学检验项目;化学检验项目类;化学类;化学试验;非刺激耐受型化学检验项目;非刺激耐受型化学检验项目类;非刺激耐受型化学试验;非刺激耐受型化学试验类 可用数量表示的;定量性;数值型;数量型;连续数值型标尺 尿;小便;下泉 尿液肌酐 尿液肌酸酐 尿肌酸酐 时刻;随机;随意;瞬间 物质的量比值;物质的量比;摩尔比;摩尔比率;摩尔比值 肌酸内酰胺

Example Units

Unit Source
umol/mol{creat} Example UCUM Units
mmol/mol eCHN

24438-4 Hexanoylglycine/Creatinine [Molar ratio] in Urine

Part Descriptions

LP14514-1   Hexanoylglycine
Urinary hexanoylglycine is a specific marker for the diagnosis of Medium-chain acyl-CoA dehydrogenase (MCAD) deficiency. PMID: 3054550 Source: Regenstrief LOINC

LP32035-5   Creatinine
Creatinine or creatine anhydride, is a breakdown product of creatine phosphate in muscle. The loss of water molecule from creatine results in the formation of creatinine. It is transferred to the kidneys by blood plasma, whereupon it is eliminated by glomular filtration and partial tubular excretion. Creatinine is usually produced at a fairly constant rate and measuring its serum level is a simple test. A rise in blood creatinine levels is observed only with marked damage to functioning nephrons; therefore this test is not suitable for detecting early kidney disease. Creatine and creatinine are metabolized in the kidneys, muscle, liver and pancreas. Copyright Copyright ©2005-2009 Genome Alberta (Reference to original publication: Wishart DS, Knox C, Guo AC, et al. HMDB: a knowledgebase for the human metabolome. Nucleic Acids Res. 2009 37(Database issue):D603-610.) Source: Human Metabolome Database, Creatinine

Fully-Specified Name

Component
Hexanoylglycine/Creatinine
Property
SRto
Time
Pt
System
Urine
Scale
Qn
Method

Additional Names

Short Name
Hexanoylgly/Creat Ur-sRto
Display Name
Hexanoylglycine/Creatinine (U) [Molar ratio]
Consumer Name Alpha Get Info
Hexanoylglycine/Creatinine, Urine

Basic Attributes

Class
CHEM
Type
Laboratory
First Released
Version 1.0o
Last Updated
Version 2.73
Order vs. Observation
Both
Common Test Rank Get Info
8922

Member of these Panels

LOINC Long Common Name
74914-3 Acylglycines panel [Molar ratio] - Urine
48797-5 Organic acids panel - Urine

Member of these Groups Get Info

LOINC Group Group Name
LG35266-2 Hexanoylglycine/Creatinine|SRto|Urine

Language Variants Get Info

Tag Language Translation
de-DE German (Germany) Hexanoylglycin/Creatinin:Stoffmengenverhältnis:Zeitpunkt:Urin:Quantitativ:
de-AT German (Austria) Synonyms: Hexanoylglycin/Kreatinin-Ratio /U
es-AR Spanish (Argentina) hexanoiloglicina/creatinina:relación de concentración de la sustancia:punto en el tiempo:orina:cuantitativo:
es-ES Spanish (Spain) Hexanoilglicina/Creatinina:Relacion de Sustancia:Punto temporal:Orina:Qn:
Synonyms: Cuantitativo
es-MX Spanish (Mexico) Hexanoilglicina / Creatinina:Proporción de sustancia:Punto temporal:Orina:Cuantitativo:
fr-CA French (Canada) Hexanoylglycine/Créatinine:Ratio de substance:Temps ponctuel:Urine:Quantitatif:
fr-FR French (France) Hexanoylglycine/créatinine:Moles ratio:Ponctuel:Urine:Numérique:
fr-BE French (Belgium) Hexanoylglycine/Créatinine:Ratio de substance:Temps ponctuel:Urine:Quantitatif:
it-IT Italian (Italy) Esanoilglicina/Creatinina:Srto:Pt:Urine:Qn:
Synonyms: Chimica Punto nel tempo (episodio) Rapporto di sostanza
ko-KR Korean (Korea, Republic Of) 헥사노일글리신/크레아티닌:물질구성비:검사시점:뇨:정량:
nl-NL Dutch (Netherlands) hexanoylglycine/creatinine:molaire verhouding:moment:urine:kwantitatief:
Synonyms: kreatinine
pt-BR Portuguese (Brazil) Hexanoilglicina/Creatinina:SCrto:Pt:Urina:Qn:
Synonyms: ; Hexanoylgly; N-caproylglycine; Hexanoyl-glycine; Creat; CR; sRto; Substance concentration ratio; Point in time; Random; Ur; UR; Urn; UA; Quantitative; QNT; Quant; Quan; Chemistry; UCr
ru-RU Russian (Russian Federation) Гексаноилглицин/Креатинин:МольОтн:ТчкВрм:Моча:Колич:
Synonyms: Количественный Мольная доля;Молярная доля;Отношение концентраций Точка во времени;Момент
tr-TR Turkish (Turkey) Hekzanoilglisin/Kreatinin:SOrn:Zmlı:İdrar:Kant:
Synonyms: SubsOranı
uk-UA Ukrainian (Ukraine) Гексаноїлгліцин/Креатинін:Молярне Співвідношення:МоментЧасу:Сеча:Кількісно:
Synonyms: Chemistry; CR; Crea; Creat; Hexanoyl-glycine; N-caproylglycine; Point in time; QNT; Quan; Quant; Quantitative; Random; Scrto; Substance concentration ratio; Substance ratio; UA; UCr; UR; Urn
zh-CN Chinese (China) 己酰甘氨酸/肌酐:物质的量比率:时间点:尿液:定量型:
Synonyms: CR;Creat;肌氨酸酐;肌酸内酰胺;肌酸酐 N-己酰基甘氨酸;N-己酰甘氨酸 UCr 化学;化学检验项目;化学检验项目类;化学类;化学试验;非刺激耐受型化学检验项目;非刺激耐受型化学检验项目类;非刺激耐受型化学试验;非刺激耐受型化学试验类 可用数量表示的;定量性;数值型;数量型;连续数值型标尺 尿;小便;下泉 尿液肌酐 尿液肌酸酐 尿肌酸酐 时刻;随机;随意;瞬间 物质的量比值;物质的量比;摩尔比;摩尔比率;摩尔比值 肌酸内酰胺

Example Units

Unit Source
umol/mol{creat} Example UCUM Units
mmol/mol cr REGENSTRIEF

24439-2 Isobutyrylglycine/Creatinine [Molar ratio] in Urine

Part Descriptions

LP14515-8   Isobutyrylglycine
Isobutyrylglycine is an acyl glycine. Acyl glycines are normally minor metabolites of fatty acids. However, the excretion of certain acyl glycines is increased in several inborn errors of metabolism. In certain cases the measurement of these metabolites in body fluids can be used to diagnose disorders associated with mitochondrial fatty acid beta-oxidation. Acyl glycines are produced through the action of glycine N-acyltransferase (EC 2.3.1.13) which is an enzyme that catalyzes the chemical reaction: acyl-CoA + glycine < -- > CoA + N-acylglycine Isobutyrylglycine is identified in large amount in urine of patients with isobutyryl-CoA dehydrogenase deficiency. Isobutyryl-CoA dehydrogenase deficiency is a disorder caused by the deficiency of isobutyryl-CoA dehydrogenase that is involved in the catabolism of the branched-chain amino acid valine PMID: 15505379. Copyright Copyright ©2005-2009 Genome Alberta (Reference to original publication: Wishart DS, Knox C, Guo AC, et al. HMDB: a knowledgebase for the human metabolome. Nucleic Acids Res. 2009 37(Database issue):D603-610.) Source: Human Metabolome Database, Isobutyrylglycine

LP32035-5   Creatinine
Creatinine or creatine anhydride, is a breakdown product of creatine phosphate in muscle. The loss of water molecule from creatine results in the formation of creatinine. It is transferred to the kidneys by blood plasma, whereupon it is eliminated by glomular filtration and partial tubular excretion. Creatinine is usually produced at a fairly constant rate and measuring its serum level is a simple test. A rise in blood creatinine levels is observed only with marked damage to functioning nephrons; therefore this test is not suitable for detecting early kidney disease. Creatine and creatinine are metabolized in the kidneys, muscle, liver and pancreas. Copyright Copyright ©2005-2009 Genome Alberta (Reference to original publication: Wishart DS, Knox C, Guo AC, et al. HMDB: a knowledgebase for the human metabolome. Nucleic Acids Res. 2009 37(Database issue):D603-610.) Source: Human Metabolome Database, Creatinine

Fully-Specified Name

Component
Isobutyrylglycine/Creatinine
Property
SRto
Time
Pt
System
Urine
Scale
Qn
Method

Additional Names

Short Name
Isobutyrylgly/Creat Ur-sRto
Display Name
Isobutyrylglycine/Creatinine (U) [Molar ratio]
Consumer Name Alpha Get Info
Isobutyrylglycine/Creatinine, Urine

Basic Attributes

Class
CHEM
Type
Laboratory
First Released
Version 1.0o
Last Updated
Version 2.73
Order vs. Observation
Observation
Common Test Rank Get Info
9432

Member of these Panels

LOINC Long Common Name
74914-3 Acylglycines panel [Molar ratio] - Urine

Language Variants Get Info

Tag Language Translation
es-AR Spanish (Argentina) isobutirilglicina/creatinina:relación de concentración de la sustancia:punto en el tiempo:orina:cuantitativo:
es-ES Spanish (Spain) Isobutirilglicina/Creatinina:Relacion de Sustancia:Punto temporal:Orina:Qn:
Synonyms: Cuantitativo
es-MX Spanish (Mexico) Isobutirilglicina / Creatinina:Proporción de sustancia:Punto temporal:Orina:Cuantitativo:
fr-CA French (Canada) Isobutyrylglycine/Créatinine:Ratio de substance:Temps ponctuel:Urine:Quantitatif:
fr-FR French (France) Isobutyrylglycine/créatinine:Moles ratio:Ponctuel:Urine:Numérique:
fr-BE French (Belgium) Isobutyrylglycine/Créatinine:Ratio de substance:Temps ponctuel:Urine:Quantitatif:
it-IT Italian (Italy) Isobutirilglicina/Creatinina:Srto:Pt:Urine:Qn:
Synonyms: Chimica Punto nel tempo (episodio) Rapporto di sostanza
ko-KR Korean (Korea, Republic Of) 이소부틸글리신/크레아티닌:물질구성비:검사시점:뇨:정량:
nl-NL Dutch (Netherlands) isobutyrylglycine/creatinine:molaire verhouding:moment:urine:kwantitatief:
Synonyms: kreatinine
pt-BR Portuguese (Brazil) Isobutirilglicina/Creatinina:SCrto:Pt:Urina:Qn:
Synonyms: ; Isobutyrylgly; Creat; CR; sRto; Substance concentration ratio; Point in time; Random; Ur; UR; Urn; UA; Quantitative; QNT; Quant; Quan; Chemistry; UCr
ru-RU Russian (Russian Federation) Изобутирилглицин/Креатинин:МольОтн:ТчкВрм:Моча:Колич:
Synonyms: Количественный Мольная доля;Молярная доля;Отношение концентраций Точка во времени;Момент
tr-TR Turkish (Turkey) İzobütirilglisin/Kreatinin:SOrn:Zmlı:İdrar:Kant:
Synonyms: SubsOranı
uk-UA Ukrainian (Ukraine) Ізобутирилгліцин/Креатинін:Молярне Співвідношення:МоментЧасу:Сеча:Кількісно:
Synonyms: Chemistry; CR; Crea; Creat; Point in time; QNT; Quan; Quant; Quantitative; Random; Scrto; Substance concentration ratio; Substance ratio; UA; UCr; UR; Urn
zh-CN Chinese (China) 异丁酰甘氨酸/肌酐:物质的量比率:时间点:尿液:定量型:
Synonyms: CR;Creat;肌氨酸酐;肌酸内酰胺;肌酸酐 UCr 化学;化学检验项目;化学检验项目类;化学类;化学试验;非刺激耐受型化学检验项目;非刺激耐受型化学检验项目类;非刺激耐受型化学试验;非刺激耐受型化学试验类 可用数量表示的;定量性;数值型;数量型;连续数值型标尺 尿;小便;下泉 尿液肌酐 尿液肌酸酐 尿肌酸酐 时刻;随机;随意;瞬间 物质的量比值;物质的量比;摩尔比;摩尔比率;摩尔比值 肌酸内酰胺

Example Units

Unit Source
umol/mol{creat} Example UCUM Units
mmol/mol eCHN

24440-0 Isovalerylglycine/Creatinine [Molar ratio] in Urine

Part Descriptions

LP14516-6   Isovalerylglycine
Isovalerylglycine is an acyl glycine. Acyl glycines are normally minor metabolites of fatty acids. However, the excretion of certain acyl glycines is increased in several inborn errors of metabolism. In certain cases the measurement of these metabolites in body fluids can be used to diagnose disorders associated with mitochondrial fatty acid beta-oxidation. Acyl glycines are produced through the action of glycine N-acyltransferase (EC 2.3.1.13) which is an enzyme that catalyzes the chemical reaction: acyl-CoA + glycine < -- > CoA + N-acylglycine Isovalerylglycine is a byproduct of the catabolism of the aminoacid leucine. Accumulation of isovalerylglycine occurs in Isovaleric Acidemia (IVA). IVA (OMIM/ McKusick 243500) is an autosomal recessive disorder caused by mutations in the isovaleryl-CoA dehydrogenase (EC 1.3.99.10) gene. The deficiency of this enzyme in the metabolism of leucine leads to the accumulation of a series of isovaleryl-CoA metabolites, such as isovalerylglycine (IVG). It is very important to caution for false positive results when screening for isovaleric acidemia by tandem mass spectrometry based on dried blood-spot levels of C5-acylcarnitines, including isovalerylcarnitine and its isomer, pivaloylcarnitine; pivaloylcarnitine is derived from pivalate-generating antibiotics, and has caused many false-positive results. PMID: 17850781. Copyright Copyright ©2005-2009 Genome Alberta (Reference to original publication: Wishart DS, Knox C, Guo AC, et al. HMDB: a knowledgebase for the human metabolome. Nucleic Acids Res. 2009 37(Database issue):D603-610.) Source: Human Metabolome Database, Isovalerylglycine

LP32035-5   Creatinine
Creatinine or creatine anhydride, is a breakdown product of creatine phosphate in muscle. The loss of water molecule from creatine results in the formation of creatinine. It is transferred to the kidneys by blood plasma, whereupon it is eliminated by glomular filtration and partial tubular excretion. Creatinine is usually produced at a fairly constant rate and measuring its serum level is a simple test. A rise in blood creatinine levels is observed only with marked damage to functioning nephrons; therefore this test is not suitable for detecting early kidney disease. Creatine and creatinine are metabolized in the kidneys, muscle, liver and pancreas. Copyright Copyright ©2005-2009 Genome Alberta (Reference to original publication: Wishart DS, Knox C, Guo AC, et al. HMDB: a knowledgebase for the human metabolome. Nucleic Acids Res. 2009 37(Database issue):D603-610.) Source: Human Metabolome Database, Creatinine

Fully-Specified Name

Component
Isovalerylglycine/Creatinine
Property
SRto
Time
Pt
System
Urine
Scale
Qn
Method

Additional Names

Short Name
Isovalerylgly/Creat Ur-sRto
Display Name
Isovalerylglycine/Creatinine (U) [Molar ratio]
Consumer Name Alpha Get Info
Isovalerylglycine/Creatinine, Urine

Basic Attributes

Class
CHEM
Type
Laboratory
First Released
Version 1.0o
Last Updated
Version 2.73
Order vs. Observation
Observation
Common Test Rank Get Info
8849

Member of these Panels

LOINC Long Common Name
74914-3 Acylglycines panel [Molar ratio] - Urine
48797-5 Organic acids panel - Urine

Member of these Groups Get Info

LOINC Group Group Name
LG35268-8 Isovalerylglycine/Creatinine|SRto|Urine

Language Variants Get Info

Tag Language Translation
de-DE German (Germany) Isovalerylglycin/Creatinin:Stoffmengenverhältnis:Zeitpunkt:Urin:Quantitativ:
es-AR Spanish (Argentina) isovalerilglicina/creatinina:relación de concentración de la sustancia:punto en el tiempo:orina:cuantitativo:
es-ES Spanish (Spain) Isovalerilglicina/Creatinina:Relacion de Sustancia:Punto temporal:Orina:Qn:
Synonyms: Cuantitativo
es-MX Spanish (Mexico) Isovalerilglicina / Creatinina:Proporción de sustancia:Punto temporal:Orina:Cuantitativo:
fr-CA French (Canada) Isovalérylglycine/Créatinine:Ratio de substance:Temps ponctuel:Urine:Quantitatif:
fr-FR French (France) Isovalérylglycine/créatinine:Moles ratio:Ponctuel:Urine:Numérique:
fr-BE French (Belgium) Isovalérylglycine/Créatinine:Ratio de substance:Temps ponctuel:Urine:Quantitatif:
it-IT Italian (Italy) Isovalerilglicina/Creatinina:Srto:Pt:Urine:Qn:
Synonyms: Chimica Punto nel tempo (episodio) Rapporto di sostanza
ko-KR Korean (Korea, Republic Of) 이소발레릴글리신/크레아티닌:물질구성비:검사시점:뇨:정량:
nl-NL Dutch (Netherlands) isovalerylglycine/creatinine:molaire verhouding:moment:urine:kwantitatief:
Synonyms: kreatinine
pt-BR Portuguese (Brazil) Isovalerilglicina/Creatinina:SCrto:Pt:Urina:Qn:
Synonyms: ; Isovalerylgly; Creat; CR; sRto; Substance concentration ratio; Point in time; Random; Ur; UR; Urn; UA; Quantitative; QNT; Quant; Quan; Chemistry; UCr
ru-RU Russian (Russian Federation) Изовалерилглицин/Креатинин:МольОтн:ТчкВрм:Моча:Колич:
Synonyms: Количественный Мольная доля;Молярная доля;Отношение концентраций Точка во времени;Момент
tr-TR Turkish (Turkey) İzovalerilglisin/Kreatinin:SOrn:Zmlı:İdrar:Kant:
Synonyms: SubsOranı
uk-UA Ukrainian (Ukraine) Ізовалерилгліцин/Креатинін:Молярне Співвідношення:МоментЧасу:Сеча:Кількісно:
Synonyms: Chemistry; CR; Crea; Creat; Point in time; QNT; Quan; Quant; Quantitative; Random; Scrto; Substance concentration ratio; Substance ratio; UA; UCr; UR; Urn
zh-CN Chinese (China) 异戊酰甘氨酸/肌酐:物质的量比率:时间点:尿液:定量型:
Synonyms: CR;Creat;肌氨酸酐;肌酸内酰胺;肌酸酐 UCr 化学;化学检验项目;化学检验项目类;化学类;化学试验;非刺激耐受型化学检验项目;非刺激耐受型化学检验项目类;非刺激耐受型化学试验;非刺激耐受型化学试验类 可用数量表示的;定量性;数值型;数量型;连续数值型标尺 尿;小便;下泉 尿液肌酐 尿液肌酸酐 尿肌酸酐 时刻;随机;随意;瞬间 物质的量比值;物质的量比;摩尔比;摩尔比率;摩尔比值 肌酸内酰胺

Example Units

Unit Source
umol/mol{creat} Example UCUM Units
mmol/mol cr REGENSTRIEF

24435-0 2-Methylbutyrylglycine/Creatinine [Molar ratio] in Urine

Part Descriptions

LP14511-7   2-Methylbutyrylglycine
2-Methylbutyrylglycine (2-MBG) is an acyl glycine generated by the L-isoleucine oxidation pathway. Increased levels of 2-MBG is a hallmark in short/branched-chain acyl-CoA dehydrogenase deficiency (SBCADD), an autosomal recessive inherited condition caused by a defect in isoleucine catabolism. PMID: 15615815 Source: Regenstrief LOINC, PMID: 15615815

LP32035-5   Creatinine
Creatinine or creatine anhydride, is a breakdown product of creatine phosphate in muscle. The loss of water molecule from creatine results in the formation of creatinine. It is transferred to the kidneys by blood plasma, whereupon it is eliminated by glomular filtration and partial tubular excretion. Creatinine is usually produced at a fairly constant rate and measuring its serum level is a simple test. A rise in blood creatinine levels is observed only with marked damage to functioning nephrons; therefore this test is not suitable for detecting early kidney disease. Creatine and creatinine are metabolized in the kidneys, muscle, liver and pancreas. Copyright Copyright ©2005-2009 Genome Alberta (Reference to original publication: Wishart DS, Knox C, Guo AC, et al. HMDB: a knowledgebase for the human metabolome. Nucleic Acids Res. 2009 37(Database issue):D603-610.) Source: Human Metabolome Database, Creatinine

Fully-Specified Name

Component
2-Methylbutyrylglycine/Creatinine
Property
SRto
Time
Pt
System
Urine
Scale
Qn
Method

Additional Names

Short Name
2Me-butyrylglycine/Creat Ur-sRto
Display Name
2-Methylbutyrylglycine/Creatinine (U) [Molar ratio]
Consumer Name Alpha Get Info
2-Methylbutyrylglycine/Creatinine, Urine

Basic Attributes

Class
CHEM
Type
Laboratory
First Released
Version 1.0o
Last Updated
Version 2.73
Order vs. Observation
Observation
Common Test Rank Get Info
9430

Member of these Panels

LOINC Long Common Name
74914-3 Acylglycines panel [Molar ratio] - Urine

Language Variants Get Info

Tag Language Translation
de-DE German (Germany) 2-Methylbutyrylglycin/Creatinin:Stoffmengenverhältnis:Zeitpunkt:Urin:Quantitativ:
es-AR Spanish (Argentina) 2-metilbutirilglicina/creatinina:relación de concentración de la sustancia:punto en el tiempo:orina:cuantitativo:
es-ES Spanish (Spain) 2-Metilbutirilglicina/Creatinina:Relacion de Sustancia:Punto temporal:Orina:Qn:
Synonyms: Cuantitativo
es-MX Spanish (Mexico) 2-metilbutirilglicina / creatinina:Proporción de sustancia:Punto temporal:Orina:Cuantitativo:
fr-CA French (Canada) 2-méthylbutyrylglycine/Créatinine:Ratio de substance:Temps ponctuel:Urine:Quantitatif:
fr-FR French (France) 2-méthylbutyrylglycine/créatinine:Moles ratio:Ponctuel:Urine:Numérique:
fr-BE French (Belgium) 2-méthylbutyrylglycine/Créatinine:Ratio de substance:Temps ponctuel:Urine:Quantitatif:
it-IT Italian (Italy) 2-Metilbutirrilglicina/Creatinina:Srto:Pt:Urine:Qn:
Synonyms: Chimica Punto nel tempo (episodio) Rapporto di sostanza
ko-KR Korean (Korea, Republic Of) 2-메틸부티릴글라이신/크레아티닌:물질구성비:검사시점:뇨:정량:
nl-NL Dutch (Netherlands) 2-methylbutyrylglycine/creatinine:molaire verhouding:moment:urine:kwantitatief:
Synonyms: kreatinine
pt-BR Portuguese (Brazil) 2-Metilbutirilglicina/Creatinina:SCrto:Pt:Urina:Qn:
Synonyms: ; 2Me-butyrylglycine; Creat; CR; 2Me-butyrylglycine; sRto; Substance concentration ratio; Point in time; Random; Ur; UR; Urn; UA; Quantitative; QNT; Quant; Quan; II; Chemistry; UCr
ru-RU Russian (Russian Federation) 2-Метилбутирилглицин/Креатинин:МольОтн:ТчкВрм:Моча:Колич:
Synonyms: Количественный Мольная доля;Молярная доля;Отношение концентраций Точка во времени;Момент
tr-TR Turkish (Turkey) 2-Metilbütirilglisin/Kreatinin:SOrn:Zmlı:İdrar:Kant:
Synonyms: SubsOranı
uk-UA Ukrainian (Ukraine) 2-Метилбутирилгліцин/Креатинін:Молярне Співвідношення:МоментЧасу:Сеча:Кількісно:
Synonyms: 2-MBG; 2Me-butyrylglycine; Chemistry; CR; Crea; Creat; II; Point in time; QNT; Quan; Quant; Quantitative; Random; Scrto; Substance concentration ratio; Substance ratio; UA; UCr; UR; Urn
zh-CN Chinese (China) 2-甲基丁酰甘氨酸/肌酐:物质的量比率:时间点:尿液:定量型:
Synonyms: 2Me-丁酰甘氨酸 Ⅱ CR;Creat;肌氨酸酐;肌酸内酰胺;肌酸酐 II UCr 化学;化学检验项目;化学检验项目类;化学类;化学试验;非刺激耐受型化学检验项目;非刺激耐受型化学检验项目类;非刺激耐受型化学试验;非刺激耐受型化学试验类 可用数量表示的;定量性;数值型;数量型;连续数值型标尺 尿;小便;下泉 尿液肌酐 尿液肌酸酐 尿肌酸酐 时刻;随机;随意;瞬间 物质的量比值;物质的量比;摩尔比;摩尔比率;摩尔比值 肌酸内酰胺

Example Units

Unit Source
mmol/mol{creat} Example UCUM Units
mmol/mol eCHN

24441-8 Phenylpropionylglycine/Creatinine [Molar ratio] in Urine

Part Descriptions

LP14517-4   Phenylpropionylglycine
Phenylpropionylglycine is an acyl glycine. Acyl glycines are normally minor metabolites of fatty acids. However, the excretion of certain acyl glycines is increased in several inborn errors of metabolism. In certain cases the measurement of these metabolites in body fluids can be used to diagnose disorders associated with mitochondrial fatty acid beta-oxidation. Acyl glycines are produced through the action of glycine N-acyltransferase (EC 2.3.1.13), which is an enzyme that catalyzes the chemical reaction:acyl-CoA + glycine < -- > CoA + N-acylglycine. The detection of phenylpropionylglycine in urine after an oral load of phenylpropionic acid can be used to diagnose deficiency of medium-chain acyl-CoA dehydrogenase, a frequent and treatable metabolic defect. PMID: 9234867 Copyright Copyright ©2005-2009 Genome Alberta (Reference to original publication: Wishart DS, Knox C, Guo AC, et al. HMDB: a knowledgebase for the human metabolome. Nucleic Acids Res. 2009 37(Database issue):D603-610.) Source: Human Metabolome Database, Phenylpropionylglycine

LP32035-5   Creatinine
Creatinine or creatine anhydride, is a breakdown product of creatine phosphate in muscle. The loss of water molecule from creatine results in the formation of creatinine. It is transferred to the kidneys by blood plasma, whereupon it is eliminated by glomular filtration and partial tubular excretion. Creatinine is usually produced at a fairly constant rate and measuring its serum level is a simple test. A rise in blood creatinine levels is observed only with marked damage to functioning nephrons; therefore this test is not suitable for detecting early kidney disease. Creatine and creatinine are metabolized in the kidneys, muscle, liver and pancreas. Copyright Copyright ©2005-2009 Genome Alberta (Reference to original publication: Wishart DS, Knox C, Guo AC, et al. HMDB: a knowledgebase for the human metabolome. Nucleic Acids Res. 2009 37(Database issue):D603-610.) Source: Human Metabolome Database, Creatinine

Fully-Specified Name

Component
Phenylpropionylglycine/Creatinine
Property
SRto
Time
Pt
System
Urine
Scale
Qn
Method

Additional Names

Short Name
PPG/Creat Ur-sRto
Display Name
Phenylpropionylglycine/Creatinine (U) [Molar ratio]
Consumer Name Alpha Get Info
Phenylpropionylglycine/Creatinine, Urine

Basic Attributes

Class
CHEM
Type
Laboratory
First Released
Version 1.0o
Last Updated
Version 2.73
Order vs. Observation
Both
Common Test Rank Get Info
8875

Member of these Panels

LOINC Long Common Name
74914-3 Acylglycines panel [Molar ratio] - Urine
48797-5 Organic acids panel - Urine

Member of these Groups Get Info

LOINC Group Group Name
LG35269-6 Phenylpropionylglycine/Creatinine|SRto|Urine

Language Variants Get Info

Tag Language Translation
de-DE German (Germany) Phenylpropionylglycin/Creatinin:Stoffmengenverhältnis:Zeitpunkt:Urin:Quantitativ:
es-AR Spanish (Argentina) fenilpropionilglicina/creatinina:relación de concentración de la sustancia:punto en el tiempo:orina:cuantitativo:
es-ES Spanish (Spain) Fenilpropionilglicina/Creatinina:Relacion de Sustancia:Punto temporal:Orina:Qn:
Synonyms: Cuantitativo
es-MX Spanish (Mexico) Fenilpropionilglicina / Creatinina:Proporción de sustancia:Punto temporal:Orina:Cuantitativo:
fr-CA French (Canada) Phénylpropionylglycine/Créatinine:Ratio de substance:Temps ponctuel:Urine:Quantitatif:
fr-FR French (France) Phénylpropionylglycine/créatinine:Moles ratio:Ponctuel:Urine:Numérique:
fr-BE French (Belgium) Phénylpropionylglycine/Créatinine:Ratio de substance:Temps ponctuel:Urine:Quantitatif:
it-IT Italian (Italy) Fenilpropionilglicina/Creatinina:Srto:Pt:Urine:Qn:
Synonyms: Chimica Punto nel tempo (episodio) Rapporto di sostanza
ko-KR Korean (Korea, Republic Of) 페닐프로피오닐글리신/크레아티닌:물질구성비:검사시점:뇨:정량:
nl-NL Dutch (Netherlands) fenylpropionylglycine/creatinine:molaire verhouding:moment:urine:kwantitatief:
Synonyms: kreatinine
pl-PL Polish (Poland) Fenylopropionyloglicyna/kreatynina:współczynnik molowy:punkt w czasie:mocz:ilościowy:
pt-BR Portuguese (Brazil) Fenilpropionilglicina/Creatinina:SCrto:Pt:Urina:Qn:
Synonyms: ; PPG; Creat; CR; sRto; Substance concentration ratio; Point in time; Random; Ur; UR; Urn; UA; Quantitative; QNT; Quant; Quan; Chemistry; UCr
ru-RU Russian (Russian Federation) Фенилпропионилглицин/Креатинин:МольОтн:ТчкВрм:Моча:Колич:
Synonyms: Количественный Мольная доля;Молярная доля;Отношение концентраций Точка во времени;Момент
tr-TR Turkish (Turkey) Fenilpropiyonilglisin/Kreatinin:SOrn:Zmlı:İdrar:Kant:
Synonyms: SubsOranı
uk-UA Ukrainian (Ukraine) Фенілпропіонілгліцин/Креатинін:Молярне Співвідношення:МоментЧасу:Сеча:Кількісно:
Synonyms: Chemistry; CR; Crea; Creat; Point in time; PPG; QNT; Quan; Quant; Quantitative; Random; Scrto; Substance concentration ratio; Substance ratio; UA; UCr; UR; Urn
zh-CN Chinese (China) 苯丙酰甘氨酸/肌酐:物质的量比率:时间点:尿液:定量型:
Synonyms: CR;Creat;肌氨酸酐;肌酸内酰胺;肌酸酐 PPG UCr 化学;化学检验项目;化学检验项目类;化学类;化学试验;非刺激耐受型化学检验项目;非刺激耐受型化学检验项目类;非刺激耐受型化学试验;非刺激耐受型化学试验类 可用数量表示的;定量性;数值型;数量型;连续数值型标尺 尿;小便;下泉 尿液肌酐 尿液肌酸酐 尿肌酸酐 时刻;随机;随意;瞬间 物质的量比值;物质的量比;摩尔比;摩尔比率;摩尔比值 肌酸内酰胺

Example Units

Unit Source
umol/mol{creat} Example UCUM Units
mmol/mol cr REGENSTRIEF

24443-4 Suberylglycine/Creatinine [Molar ratio] in Urine

Part Descriptions

LP14519-0   Suberylglycine
Suberylglycine is a dicarboxylic acid. It is formed by glycine-N-acylase catalyzed conjugation. PMID: 947635 It can be used for the diagnosis of hereditary medium-chain acyl-CoA dehydrogenase deficiency. PMID: 2775902 Copyright Copyright ©2005-2009 Genome Alberta (Reference to original publication: Wishart DS, Knox C, Guo AC, et al. HMDB: a knowledgebase for the human metabolome. Nucleic Acids Res. 2009 37(Database issue):D603-610.) Source: Human Metabolome Database, Suberylglycine

LP32035-5   Creatinine
Creatinine or creatine anhydride, is a breakdown product of creatine phosphate in muscle. The loss of water molecule from creatine results in the formation of creatinine. It is transferred to the kidneys by blood plasma, whereupon it is eliminated by glomular filtration and partial tubular excretion. Creatinine is usually produced at a fairly constant rate and measuring its serum level is a simple test. A rise in blood creatinine levels is observed only with marked damage to functioning nephrons; therefore this test is not suitable for detecting early kidney disease. Creatine and creatinine are metabolized in the kidneys, muscle, liver and pancreas. Copyright Copyright ©2005-2009 Genome Alberta (Reference to original publication: Wishart DS, Knox C, Guo AC, et al. HMDB: a knowledgebase for the human metabolome. Nucleic Acids Res. 2009 37(Database issue):D603-610.) Source: Human Metabolome Database, Creatinine

Fully-Specified Name

Component
Suberylglycine/Creatinine
Property
SRto
Time
Pt
System
Urine
Scale
Qn
Method

Additional Names

Short Name
Suberylgly/Creat Ur-sRto
Display Name
Suberylglycine/Creatinine (U) [Molar ratio]
Consumer Name Alpha Get Info
Suberylglycine/Creatinine, Urine

Basic Attributes

Class
CHEM
Type
Laboratory
First Released
Version 1.0o
Last Updated
Version 2.73
Order vs. Observation
Observation
Common Test Rank Get Info
8945

Member of these Panels

LOINC Long Common Name
74914-3 Acylglycines panel [Molar ratio] - Urine
48797-5 Organic acids panel - Urine

Language Variants Get Info

Tag Language Translation
de-DE German (Germany) Suberylglycin/Creatinin:Stoffmengenverhältnis:Zeitpunkt:Urin:Quantitativ:
es-AR Spanish (Argentina) suberiloglicina/creatinina:relación de concentración de la sustancia:punto en el tiempo:orina:cuantitativo:
es-ES Spanish (Spain) Suberilglicina/Creatinina:Relacion de Sustancia:Punto temporal:Orina:Qn:
Synonyms: Cuantitativo
es-MX Spanish (Mexico) Suberilglicina / Creatinina:Proporción de sustancia:Punto temporal:Orina:Cuantitativo:
fr-CA French (Canada) Subérylglycine/Créatinine:Ratio de substance:Temps ponctuel:Urine:Quantitatif:
fr-FR French (France) Subérylglycine/créatinine:Moles ratio:Ponctuel:Urine:Numérique:
fr-BE French (Belgium) Subérylglycine/Créatinine:Ratio de substance:Temps ponctuel:Urine:Quantitatif:
it-IT Italian (Italy) Suberilglicina/Creatinina:Srto:Pt:Urine:Qn:
Synonyms: Chimica Punto nel tempo (episodio) Rapporto di sostanza
ko-KR Korean (Korea, Republic Of) 수베릴글리신/크레아티닌:물질구성비:검사시점:뇨:정량:
nl-NL Dutch (Netherlands) suberylglycine/creatinine:molaire verhouding:moment:urine:kwantitatief:
Synonyms: kreatinine
pt-BR Portuguese (Brazil) Suberilglicina/Creatinina:SCrto:Pt:Urina:Qn:
Synonyms: ; Suberylgly; Creat; CR; sRto; Substance concentration ratio; Point in time; Random; Ur; UR; Urn; UA; Quantitative; QNT; Quant; Quan; Chemistry; UCr
ru-RU Russian (Russian Federation) Суберилглицин/Креатинин:МольОтн:ТчкВрм:Моча:Колич:
Synonyms: Количественный Мольная доля;Молярная доля;Отношение концентраций Точка во времени;Момент
tr-TR Turkish (Turkey) Suberilglisin/Kreatinin:SOrn:Zmlı:İdrar:Kant:
Synonyms: SubsOranı
uk-UA Ukrainian (Ukraine) Суберилгліцин/Креатинін:Молярне Співвідношення:МоментЧасу:Сеча:Кількісно:
Synonyms: Chemistry; CR; Crea; Creat; Point in time; QNT; Quan; Quant; Quantitative; Random; Scrto; Substance concentration ratio; Substance ratio; UA; UCr; UR; Urn
zh-CN Chinese (China) 环庚基甘氨酸/肌酐:物质的量比率:时间点:尿液:定量型:
Synonyms: CR;Creat;肌氨酸酐;肌酸内酰胺;肌酸酐 UCr 化学;化学检验项目;化学检验项目类;化学类;化学试验;非刺激耐受型化学检验项目;非刺激耐受型化学检验项目类;非刺激耐受型化学试验;非刺激耐受型化学试验类 可用数量表示的;定量性;数值型;数量型;连续数值型标尺 尿;小便;下泉 尿液肌酐 尿液肌酸酐 尿肌酸酐 时刻;随机;随意;瞬间 物质的量比值;物质的量比;摩尔比;摩尔比率;摩尔比值 肌酸内酰胺

Example Units

Unit Source
umol/mol{creat} Example UCUM Units
mmol/mol cr REGENSTRIEF

53718-3 Acylglycines [Interpretation] in Urine Narrative

Fully-Specified Name

Component
Acylglycines
Property
Imp
Time
Pt
System
Urine
Scale
Nar
Method

Additional Names

Short Name
Acylglycines Ur-Imp
Display Name
Acylglycines Nar (U) [Interp]
Consumer Name Alpha Get Info
Interpretation of Acylglycines test result, Urine

Basic Attributes

Class
CHEM
Type
Laboratory
First Released
Version 2.26
Last Updated
Version 2.73
Order vs. Observation
Observation
Common Test Rank Get Info
11280

Member of these Panels

LOINC Long Common Name
50334-2 Acylglycines panel [Mass Ratio] - Urine
74914-3 Acylglycines panel [Molar ratio] - Urine

Language Variants Get Info

Tag Language Translation
es-ES Spanish (Spain) Acilglicina:Impresión/interpretación del estudio:Punto temporal:Orina:Narrativo:
es-MX Spanish (Mexico) Acilglicinas:Impresión / interpretación del estudio:Punto temporal:Orina:Narrativo:
fr-CA French (Canada) Acylglycines:Impression:Temps ponctuel:Urine:Narratif:
fr-FR French (France) Acylglycines:Interprétation:Ponctuel:Urine:Résultat textuel:
fr-BE French (Belgium) Acylglycines:Impression/interprétation d'étude:Temps ponctuel:Urine:Narratif:
it-IT Italian (Italy) Acilglicini:Imp:Pt:Urine:Nar:
Synonyms: Chimica Impressione/interpretazione di studio Punto nel tempo (episodio)
nl-NL Dutch (Netherlands) acylglycines:interpretatie:moment:urine:tekstueel:
pt-BR Portuguese (Brazil) Acilglicinas:Imp:Pt:Urina:Nar:
Synonyms: Interpretation; Interp; Impression; Impressions; Point in time; Random; Ur; UR; Urn; UA; Narrative; Report; Chemistry
ru-RU Russian (Russian Federation) Ацилглицины:Впчт:ТчкВрм:Моча:Опис:
Synonyms: Впечатление/интерпретация исследования Описательный Точка во времени;Момент
tr-TR Turkish (Turkey) Açilglisin:İzlnm:Zmlı:İdrar:Öykü:
zh-CN Chinese (China) 酰基甘氨酸类:印象:时间点:尿液:叙述型:
Synonyms: 化学;化学检验项目;化学检验项目类;化学类;化学试验;非刺激耐受型化学检验项目;非刺激耐受型化学检验项目类;非刺激耐受型化学试验;非刺激耐受型化学试验类 印象是一种诊断陈述,始终是对其他某种观察指标的解释或抽象(一系列检验项目结果、一幅图像或者整个某位病人),而且几乎总是由某位专业人员产生。;检查印象;检查印象/解释;检查的印象/解释;检查解释;解释;阐释 叙述;叙述性文字;报告;报告型;文字叙述;文本叙述型;文本描述;文本描述型 尿;小便;下泉 时刻;随机;随意;瞬间 酰基甘氨酸