74978-8
Cerebroside sulfatase and N-Acetylgalactosamine-4-Sulfatase panel [Enzymatic activity/mass] - Leukocytes
Active
24094-5 N-Acetylgalactosamine-4-Sulfatase [Enzymatic activity/mass] in Leukocytes
Part Descriptions
LP14031-6 N-Acetylgalactosamine-4-Sulfatase
An arylsulfatase that catalyzes the hydrolysis of the 4-sulfate groups of the N-acetyl-D-galactosamine 4-sulfate units of chondroitin sulfate and dermatan sulfate. A deficiency of this enzyme is responsible for the inherited lysosomal disease, Maroteaux-Lamy syndrome (MUCOPOLYSACCHARIDOSIS VI). EC 3.1.6.12.
Source: National Library of Medicine, MeSH 2006
Fully-Specified Name
- Component
- N-Acetylgalactosamine-4-Sulfatase
- Property
- CCnt
- Time
- Pt
- System
- WBC
- Scale
- Qn
- Method
Additional Names
- Short Name
- Arylsulfatase B WBC-cCnt
- Display Name
- N-Acetylgalactosamine-4-Sulfatase (WBC) [Catalytic activity/Mass]
- Consumer Name Alpha Get Info
- N-Acetylgalactosamine-4-Sulfatase, White blood cells
Basic Attributes
- Class
- CHEM
- Type
- Laboratory
- First Released
- Version 1.0o
- Last Updated
- Version 2.70
- Order vs. Observation
- Both
Member of these Panels
| LOINC | Long Common Name |
|---|---|
| 74978-8 | Cerebroside sulfatase and N-Acetylgalactosamine-4-Sulfatase panel [Enzymatic activity/mass] - Leukocytes |
| 104072-4 | Mucopolysaccharidosis enzymes panel - Leukocytes |
Language Variants Get Info
| Tag | Language | Translation |
|---|---|---|
| de-AT | German (Austria) | Synonyms: Arylsulfatase B /Leukozyten |
| es-MX | Spanish (Mexico) | N-acetilgalactosamina-4-sulfatasa: |
| es-ES | Spanish (Spain) | N-Acetilgalactosamina-4-sulfatasa: Synonyms: Cuantitativo |
| es-AR | Spanish (Argentina) | N-acetilgalactosamina-4-sulfatasa: |
| et-EE | Estonian (Estonia) | N-atsetüülgalaktosamiin-4-sulfataas: Synonyms: Juhuslik Kvantitatiivne Leukotsüüdid |
| fr-BE | French (Belgium) | N-acétylgalactosamine-4-sulfatase: |
| fr-FR | French (France) | Arylsulfatase B: |
| fr-CA | French (Canada) | N-acétylgalactosamine-4-sulfatase: |
| it-IT | Italian (Italy) | N-Acetilgalattosammina-4-Solfatasi: Synonyms: Chimica Contenuto Catalitico Globuli bianchi Punto nel tempo (episodio) |
| ko-KR | Korean (Korea, Republic Of) | N-아세틸갈락토스아민-4-술파타아제: |
| nl-NL | Dutch (Netherlands) | N-acetylgalactosamine-4-sulfatase: Synonyms: witte bloedcellen |
| pt-BR | Portuguese (Brazil) | N-Acetilgalactosamina-4-Sulfatase: Synonyms: ; |
| ru-RU | Russian (Russian Federation) | N-Ацетилгалактозамин-4-Сульфатаза: Synonyms: Каталитическое содержание Количественный Точка во времени; |
| tr-TR | Turkish (Turkey) | N-asetilgalaktozamin-4-Sülfataz: Synonyms: WBC |
| zh-CN | Chinese (China) | N-乙酰半乳糖胺-4-硫酸酯酶: Synonyms: Maroteaux-Llamy 氏病; |
Example Units
| Unit | Source |
|---|---|
| nmol/h/mg{protein} | Example UCUM Units |
| nmol/hr/mg of protein | eCHN |
24078-8 Cerebroside sulfatase [Enzymatic activity/mass] in Leukocytes
Part Descriptions
LP14023-3 Cerebroside sulfatase
Arylsulfatase A (or cerebroside-sulfatase) is an enzyme which breaks down cerebroside 3-sulfate. A deficiency is associated with metachromatic leukodystrophy.
Copyright Text is available under the Creative Commons Attribution/Share-Alike License. See http://creativecommons.org/licenses/by-sa/3.0/ for details.
Source: Wikipedia, Cerebroside sulfatase (Wikipedia)
LP14023-3 Cerebroside sulfatase
Cerebroside sulfatase measures enzyme activity released per mg protein per hr. Used to detext metachromatic leukodystrophy and its carrier state. Usually seen as part of a battery of lysomal enzymes.
Source: Regenstrief Institute
Fully-Specified Name
- Component
- Cerebroside sulfatase
- Property
- CCnt
- Time
- Pt
- System
- WBC
- Scale
- Qn
- Method
Additional Names
- Short Name
- Arylsulfatase A WBC-cCnt
- Display Name
- Cerebroside sulfatase (WBC) [Catalytic activity/Mass]
- Consumer Name Alpha Get Info
- Cerebroside sulfatase, White blood cells
Basic Attributes
- Class
- CHEM
- Type
- Laboratory
- First Released
- Version 1.0o
- Last Updated
- Version 2.73
- Order vs. Observation
- Both
- Common Test Rank Get Info
- 10178
Member of these Panels
| LOINC | Long Common Name |
|---|---|
| 74978-8 | Cerebroside sulfatase and N-Acetylgalactosamine-4-Sulfatase panel [Enzymatic activity/mass] - Leukocytes |
Language Variants Get Info
| Tag | Language | Translation |
|---|---|---|
| de-AT | German (Austria) | Synonyms: Arylsufatase A /Leukozyten |
| es-AR | Spanish (Argentina) | cerebrósido sulfatasa: |
| es-MX | Spanish (Mexico) | Cerebrósido sulfatasa: |
| es-ES | Spanish (Spain) | Cerebrósido sulfatasa: Synonyms: Cuantitativo |
| et-EE | Estonian (Estonia) | Tserebrosiidi sulfataas: Synonyms: Juhuslik Kvantitatiivne Leukotsüüdid |
| fr-FR | French (France) | Arylsulfatase A: |
| fr-CA | French (Canada) | Cérébroside-sulfatase: |
| fr-BE | French (Belgium) | Cérébroside-sulfatase: |
| it-IT | Italian (Italy) | Cerebroside solfatasi: Synonyms: Chimica Contenuto Catalitico Globuli bianchi Punto nel tempo (episodio) |
| ko-KR | Korean (Korea, Republic Of) | 세레브로시드 술파타아제: |
| nl-NL | Dutch (Netherlands) | cerebrosidesulfatase: Synonyms: witte bloedcellen |
| pt-BR | Portuguese (Brazil) | Cerebrosideo sulfatase: Synonyms: ; |
| ru-RU | Russian (Russian Federation) | Цереброзид сульфатаза: Synonyms: Каталитическое содержание Количественный Точка во времени; |
| tr-TR | Turkish (Turkey) | Serebrozid sülfataz: Synonyms: WBC |
| uk-UA | Ukrainian (Ukraine) | Цереброзид сульфатаза: Synonyms: Aryl sulfatase A; |
| zh-CN | Chinese (China) | 脑苷脂硫酸酯酶: Synonyms: WBC; |
Example Units
| Unit | Source |
|---|---|
| nmol/h/mg{protein} | Example UCUM Units |
| nmol/mg prot/H | REGENSTRIEF |