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2-Ketoglutaric acid (alpha ketoglutarate) is an important nitrogen transporter and a key intermediate in the Krebs cycle.Amino groups of amino acids are attached to it by transamination and carried to the liver where the urea cycle takes place. Increased levels found with 2-ketoglutaric DH deficiency, GA I, 2-amino/2-ketoadipate acidemia, dihdrolipoyl DH(E3) deficiency, glycogen storage disorders I, 2-hydroxyglutaric aciduria(D-form), and fumarase deficiency. Very low values are sometimes encountered in chronic fatigue syndrome.(Information from: Kumps A, Duez P, Mardens Y. Metabolic, Nutritional, Iatrogenic, and Artifactual Sources of Urinary Organic Acids: A Comprehensive Table. Clinical Chemistry 2002, 48:708-717.) Source: Regenstrief Institute

Basic Part Properties

Part Display Name
Alpha ketoglutarate
Part Type
Component (Describes the core component or analyte measured)
Created On
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Language Variants Get Info

Tag Language Translation
zh-CN Chinese (China) Alpha 酮戊二酸
Synonyms: 2-酮戊二酸;2-酮戊二酸根;2-酮戊二酸盐;2-酮戊二酸酯;A-Ketoglut;AKG;Alpha 酮戊二酸根;Alpha 酮戊二酸盐;Alpha 酮戊二酸酯;Alpha-酮戊二酸;Alpha-酮戊二酸根;Alpha-酮戊二酸盐;Alpha-酮戊二酸酯;A-酮戊二酸;A-酮戊二酸根;A-酮戊二酸盐;A-酮戊二酸酯;α酮戊二酸;α-酮戊二酸;α酮戊二酸根;α-酮戊二酸根;α酮戊二酸盐;α-酮戊二酸盐;α酮戊二酸酯;α-酮戊二酸酯
fr-CA French (Canada) Alpha-ketoglutarate
et-EE Estonian (Estonia) Alfaketoglutaraat
es-ES Spanish (Spain) Alfa Cetoglutarato
it-IT Italian (Italy) Alfa chetoglutarato
tr-TR Turkish (Turkey) Alfa ketoglutarat
ru-RU Russian (Russian Federation) Альфа кетоглутарат
Synonyms: Альфа-кетоглутарат
nl-NL Dutch (Netherlands) alfa-ketoglutaraat
fr-BE French (Belgium) Alpha-kétoglutarate
Synonyms: Alpha-cétoglutarate