Version 2.76


Elevated levels of 2-oxoisovalerate are associated with maple syrup disease, pyruvate dehydrogenase deficiciency, and lactic acidosis. Slight decreases may occur with deficiencies of lipoic acid or thiamine. (Information from: Kumps A, Duez P, Mardens Y. Metabolic, Nutritional, Iatrogenic, and Artifactual Sources of Urinary Organic Acids: A Comprehensive Table. Clinical Chemistry 2002, 48:708-717.) Source: Regenstrief Institute

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Language Variants Get Info

Tag Language Translation
zh-CN Chinese (China) 2-氧代异戊酸
Synonyms: 2-酮基异戊酸;2-酮异戊酸
fr-CA French (Canada) 2-oxoisovalérate
et-EE Estonian (Estonia) 2-oksoisovaleraat
es-ES Spanish (Spain) 2-Oxoisovalerato
it-IT Italian (Italy) 2-Ossoisovalerato
tr-TR Turkish (Turkey) 2-Okzoizovalerat
ru-RU Russian (Russian Federation) 2-Оксоизовалерат
nl-NL Dutch (Netherlands) 2-oxoisovaleraat
fr-BE French (Belgium) 2-oxoisovalérate