Description

Elevated levels of 2-oxoisovalerate are associated with maple syrup disease, pyruvate dehydrogenase deficiciency, and lactic acidosis. Slight decreases may occur with deficiencies of lipoic acid or thiamine. (Information from: Kumps A, Duez P, Mardens Y. Metabolic, Nutritional, Iatrogenic, and Artifactual Sources of Urinary Organic Acids: A Comprehensive Table. Clinical Chemistry 2002, 48:708-717.) Source: Regenstrief Institute

Basic Part Properties

Part Name
2-Oxoisovalerate
Part Display Name
2-Oxoisovalerate
Part Type
Component (Describes the core component or analyte measured)
Created On
2000-05-04
Construct for LOINC Short Name
2Oxoisovalerate

LOINC Terminology Service (API) using HL7® FHIR® Get Info

CodeSystem lookup
https://fhir.loinc.org/CodeSystem/$lookup?system=http://loinc.org&code=LP18410-8
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https://fhir.loinc.org/ConceptMap/$translate?system=http://loinc.org&code=LP18410-8

Language Variants Get Info

TagLanguageTranslation
zh-CNChinese (China)2-氧代异戊酸
Synonyms: 2-酮基异戊酸;2-酮异戊酸
fr-CAFrench (Canada)2-oxoisovalérate
et-EEEstonian (Estonia)2-oksoisovaleraat
es-ESSpanish (Spain)2-Oxoisovalerato
it-ITItalian (Italy)2-Ossoisovalerato
tr-TRTurkish (Turkey)2-Okzoizovalerat
ru-RURussian (Russian Federation)2-Оксоизовалерат
nl-NLDutch (Netherlands)2-oxoisovaleraat
fr-BEFrench (Belgium)2-oxoisovalérate
fr-FRFrench (France)2-oxoisovalérate
pl-PLPolish (Poland)2-Oksoizowalerian
el-GRGreek (Greece)2-οξοϊσοβαλερικό
Synonyms: 2-οξοϊσοβαλερικό