Version 2.77


Uroporphyrin is the porphyrin produced by oxidation of the methylene bridges in uroporphyrinogen. They have four acetic acid and four propionic acid side chains attached to the pyrrole rings. Uroporphyrinogen I and III is formed from polypyrryl methane in the presence of uroporphyrinogen III cosynthetase and uroporphyrin I synthetase, respectively. They can yield uroporphyrins by autooxidation or coproporphyrinogens by decarboxylation. Excessive amounts of uroporphyrin I are excreted in congenital erythropoietic porphyria, and both types I and III are excreted in porphyria cutanea tarda. Uroporphyrin I and III are the most common isomers. Copyright Copyright ©2005-2009 Genome Alberta (Reference to original publication: Wishart DS, Knox C, Guo AC, et al. HMDB: a knowledgebase for the human metabolome. Nucleic Acids Res. 2009 37(Database issue):D603-610.) Source: Human Metabolome Database, Uroporphyrin I

Basic Part Properties

Part Display Name
Uroporphyrin 1 isomer
Part Type
Component (Describes the core component or analyte measured)
Created On
Construct for LOINC Short Name

LOINC Terminology Service (API) using HL7® FHIR® Get Info

CodeSystem lookup$lookup?system=
ConceptMap translate$translate?system=

Language Variants Get Info

Tag Language Translation
zh-CN Chinese (China) 尿卟啉 I 同分异构体
Synonyms: Uropor1;尿卟啉 1 异构体;尿卟啉 1 同分异构体;尿卟啉 I 异构体;尿卟啉Ⅰ同分异构体;尿卟啉Ⅰ异构体
fr-CA French (Canada) Uroporphyrine 1 isomère
es-ES Spanish (Spain) Isómero Uroporfirina I
it-IT Italian (Italy) Uroporfirina 1, isomero
Synonyms: Isomero di uroporfirina 1
tr-TR Turkish (Turkey) Üroporfirin 1 izomer
ru-RU Russian (Russian Federation) Уропорфирин 1 изомер
nl-NL Dutch (Netherlands) uroporfyrine 1 isomeer
fr-BE French (Belgium) Uroporphyrine 1 isomère
pl-PL Polish (Poland) Uroporfiryna I