Version 2.78

Part Description

LP15810-2   Porphobilinogen deaminase
Porphobilinogen (PBG) deaminase testing is used in the diagnosis of acute intermittent porphyria. Source: Regenstrief Institute

Fully-Specified Name

Component
Porphobilinogen deaminase
Property
CCnc
Time
Pt
System
Bld
Scale
Qn
Method

Additional Names

Short Name
PBG Deaminase Bld-cCnc
Display Name
Porphobilinogen deaminase (Bld) [Catalytic activity/Vol]
Consumer Name Alpha Get Info
Porphobilinogen deaminase, Blood

Basic Attributes

Class
CHEM
Type
Laboratory
First Released
Version 1.0j-a
Last Updated
Version 2.66
Order vs. Observation
Both

Language Variants Get Info

Tag Language Translation
de-DE German (Germany) Porphobilinogendeaminase:Katalytische Konzentration:Zeitpunkt:Blut:Quantitativ:
es-AR Spanish (Argentina) porfobilinógeno deaminasa:concentración catalítica:punto en el tiempo:sangre:cuantitativo:
es-ES Spanish (Spain) Porfobilinogeno desaminasa:Concentración Catalítica:Punto temporal:Sangre:Qn:
Synonyms: Cuantitativo
es-MX Spanish (Mexico) Desaminasa de porfobilinógeno:Concentración catalítica:Punto temporal:Sangre:Cuantitativo:
et-EE Estonian (Estonia) Porfobilinogeeni deaminaas:CCnc:Pt:B:Qn:
Synonyms: Juhuslik Kvantitatiivne Veri
fr-CA French (Canada) Porphobilinogène-désaminase:Concentration catalytique:Temps ponctuel:Sang:Quantitatif:
fr-FR French (France) Porphobilinogène déaminase:Catalytique/Volume:Ponctuel:Sang:Numérique:
fr-BE French (Belgium) Porphobilinogène-désaminase:Concentration catalytique:Temps ponctuel:Sang:Quantitatif:
it-IT Italian (Italy) Porfobilinogeno deaminasi:CCnC:Pt:Sangue:Qn:
Synonyms: Chimica Concentrazione Catalitica Punto nel tempo (episodio) Sangue
ko-KR Korean (Korea, Republic Of) 포르포빌리노겐 탈아미노효소:촉매농도:검사시점:전혈:정량:
nl-NL Dutch (Netherlands) porfobilinogeendeaminase:enzymatische activiteit/volume:moment:bloed:kwantitatief:
pt-BR Portuguese (Brazil) Porfobilinogênio deaminase:CCnc:Pt:SgTotal:Qn:
Synonyms: ; PBG Deaminase; Hydroxymethylbilane Synthase; Uroporphyrinogen I Synthase; PBG-D; Porphoblngn; Porpoblngn; Porph; Porphobili; Catalytic Concentration; Point in time; Random; Blood; WB; Whole blood; Quantitative; QNT; Quant; Quan; Chemistry
ru-RU Russian (Russian Federation) Порфобилиноген деаминаза:КаталКонц:ТчкВрм:Кр:Колич:
Synonyms: Каталитическая концентрация Количественный Кровь Порфобилиноген дезаминаза Точка во времени;Момент
tr-TR Turkish (Turkey) Porfobilinojen deaminaz:KtlKons:Zmlı:Kan:Kant:
zh-CN Chinese (China) 胆色素原脱氨酶:催化浓度:时间点:全血:定量型:
Synonyms: PBG Deaminase;PBG 脱氨酶;PBG-D;尿卟啉原 I 合酶;羟甲基胆色烷合酶;胆色素脱色氨酶 PBG;Porph;卟吩胆色素原;胆素原 催化浓度(单位体积);单位体积内酶的单位数 化学;化学检验项目;化学检验项目类;化学类;化学试验;非刺激耐受型化学检验项目;非刺激耐受型化学检验项目类;非刺激耐受型化学试验;非刺激耐受型化学试验类 可用数量表示的;定量性;数值型;数量型;连续数值型标尺 时刻;随机;随意;瞬间 血;血液

Example Units

Unit Source
nmol/s/L{RBCs} Example UCUM Units

LOINC Terminology Service (API) using HL7® FHIR® Get Info

CodeSystem lookup
https://fhir.loinc.org/CodeSystem/$lookup?system=http://loinc.org&code=12810-8