Part Descriptions

LP14022-5   Beta-N-acetylhexosaminidase
An enzyme hydrolyzing terminal non-reducing N-acetyl-D-hexosamine residues in N-acetyl-beta-D-hexosaminides. It acts on GLUCOSIDES; GALACTOSIDES; and several OLIGOSACCHARIDES. Hexosaminidase A cleaves GM2, GA2, globosides, and hexosamine oligosaccharides. Hexosaminidase B cleaves all the above substrates except GM2. Deficiency of Hexosaminidase A causes TAY-SACHS DISEASE, while deficiency of both A and B isozymes causes SANDHOFF DISEASE. The enzyme has also been used as a tumor marker to distinguish between malignant and benign disease. Source: National Library of Medicine, MeSH 2006

LP14022-5   Beta-N-acetylhexosaminidase
Beta-N-acetylhexosaminidase is also known as hexosaminidase and has two forms, A and B. Hexosaminidase B is used to screen for Tay-Sachs disease. Source: Regenstrief Institute

LOINC Names Get Info

Fully-Specified Name
Beta-N-acetylhexosaminidase:CCnt:Pt:Fibroblasts:Qn:
Long Common Name
Beta-N-acetylhexosaminidase [Enzymatic activity/mass] in Fibroblast
Short Name
B-NAH Fib-cCnt
Display Name
Beta-N-acetylhexosaminidase (Fibroblast) [Catalytic activity/Mass]
Consumer Name Alpha Get Info
Beta-N-acetylhexosaminidase, Fibroblast

Part Model Get Info

  • Component
    Beta-N-acetylhexosaminidase
    LP14022-5
    • Analyte
      Beta-N-acetylhexosaminidase
      LP14022-5
      • Component Numerator
        Beta-N-acetylhexosaminidase
        LP14022-5
        • Component Numerator Core
          Beta-N-acetylhexosaminidase
          LP14022-5
        • Component Numerator Core Suffix
          NULL
           
      • Component Denominator
        NULL
         
        • Component Denominator Core
          NULL
           
        • Component Denominator Core Suffix
          NULL
           
    • Challenge
      NULL
       
    • Adjustment
      NULL
       
    • Count
      NULL
       
  • Property
    CCnt
    LP6790-2
  • Time
    Pt
    LP6960-1
  • System
    Fibroblasts
    LP7234-0
    • System Core
      Fibroblasts
      LP7234-0
    • Super System
      NULL
       
  • Scale
    Qn
    LP7753-9
  • Method
    NULL
     

Basic Attributes

Class
CHEM
Type
Laboratory
First Released
Version 1.0o
Last Updated
Version 2.70 (MIN)
Order vs. Observation
Both

Language Variants Get Info

TagLanguageTranslation
cs-CZCzech (Czechia)Beta-N-acetylhexosaminidáza:Katalytický obsah:Časový bod:Fibroblast:Kvantitativní:
de-DEGerman (Germany)Beta-N-Acetylhexosaminidase:Katalytischer Gehalt:Zeitpunkt:Fibroblasten:Quantitativ:
el-GRGreek (Greece)β-N-ακετυλοεξοζαμινιδάση:CCnt:Pt:Ινοβλάστες:Qn:
Synonyms: CCnt CHEM N Pt Qn β-N-ακετυλοεξοζαμινιδάση Ινοβλάστες
es-ARSpanish (Argentina)beta-N-acetilhexosaminidasa:contenido catalítico:punto en el tiempo:fibroblastos:cuantitativo:
es-ESSpanish (Spain)Beta-N-acetilhexosaminidasa:Contenido catalítico:Punto temporal:Fibroblastos:Qn:
Synonyms: Cuantitativo
es-MXSpanish (Mexico)Beta-N-acetilhexosaminidasa:Contenido catalítico:Punto temporal:Fibroblasto:Cuantitativo:
fr-CAFrench (Canada)Bêta-N-acétylhexosaminidase:Contenu catalytique:Temps ponctuel:Fibroblastes:Quantitatif:
fr-FRFrench (France)Bêta N-hexosaminidase:Catalytique/Masse:Ponctuel:Fibroblastes:Numérique:
fr-BEFrench (Belgium)Béta-N-acétylhexosaminidase:Contenu catalytique:Temps ponctuel:Fibroblastes:Quantitatif:
it-ITItalian (Italy)Beta-N-acetilesosaminidasi:CCnt:Pt:Fibroblasti:Qn:
Synonyms: Chimica Contenuto Catalitico Fibroblasto Punto nel tempo (episodio)
ko-KRKorean (Korea, Republic Of)베타-N-아세틸헥소스아미니다아제:촉매구성:검사시점:섬유모세포:정량:
nl-NLDutch (Netherlands)bèta-N-acetylhexosaminidase:enzymatische activiteit/massa:moment:fibroblast:kwantitatief:
Synonyms: Beta-N-acetylhexosaminidase
pl-PLPolish (Poland)Beta-N-acetyloheksozaminidaza:zawartość katalityczna:punkt w czasie:fibroblasty:ilościowy:
pt-BRPortuguese (Brazil)Beta N-acetilhexosaminidase:CCnt:Pt:Fibroblastos:Qn:
Synonyms: ; B-NAH; GM2-gangliosidosis; Hexosaminidase; Catalytic Content; Point in time; Random; Fib; Fibr; Quantitative; QNT; Quant; Quan; B; Chemistry
ru-RURussian (Russian Federation)Бета-N-ацетилгексозаминидаза:КаталСод:ТчкВрм:Фибробласты:Колич:
Synonyms: Каталитическое содержание Количественный Точка во времени;Момент
tr-TRTurkish (Turkey)Beta-N-asetilhekzosaminidaz:Ktlİçrk:Zmlı:Fibroblastlar:Kant:
zh-CNChinese (China)Beta-N-乙酰己糖胺酶:催化含量:时间点:成纤维细胞:定量型:
Synonyms: B Beta-N-乙酰氨基己糖苷酶;B-NAH;GM2-神经节苷脂沉积症;GM2-神经节苷脂贮积病;β-N-乙酰己糖胺酶;β-N-乙酰氨基己糖苷酶;己糖胺酶;氨基己糖苷酶 N 型 β 催化含量(单位质量);单位质量的酶单位数 化学;化学检验项目;化学检验项目类;化学类;化学试验;非刺激耐受型化学检验项目;非刺激耐受型化学检验项目类;非刺激耐受型化学试验;非刺激耐受型化学试验类 可用数量表示的;定量性;数值型;数量型;连续数值型标尺 时刻;随机;随意;瞬间 纤维原细胞;纤维母细胞 贝塔

Example Units

UnitSource
nmol/h/mg{protein}Example UCUM Units
nmol/hr/mg of proteineCHN

LOINC Terminology Service (API) using HL7® FHIR® Get Info

CodeSystem lookup
https://fhir.loinc.org/CodeSystem/$lookup?system=http://loinc.org&code=24074-7