Part Description

LP14031-6   N-Acetylgalactosamine-4-Sulfatase
An arylsulfatase that catalyzes the hydrolysis of the 4-sulfate groups of the N-acetyl-D-galactosamine 4-sulfate units of chondroitin sulfate and dermatan sulfate. A deficiency of this enzyme is responsible for the inherited lysosomal disease, Maroteaux-Lamy syndrome (MUCOPOLYSACCHARIDOSIS VI). EC 3.1.6.12. Source: National Library of Medicine, MeSH 2006

LOINC Names Get Info

Fully-Specified Name
N-Acetylgalactosamine-4-Sulfatase:CCnc:Pt:WBC:Qn:
Long Common Name
N-Acetylgalactosamine-4-Sulfatase [Enzymatic activity/volume] in Leukocytes
Short Name
Arylsulfatase B WBC-cCnc
Display Name
N-Acetylgalactosamine-4-Sulfatase (WBC) [Catalytic activity/Vol]
Consumer Name Alpha Get Info
N-Acetylgalactosamine-4-Sulfatase, White blood cells

Part Model Get Info

  • Component
    N-Acetylgalactosamine-4-Sulfatase
    LP14031-6
    • Analyte
      N-Acetylgalactosamine-4-Sulfatase
      LP14031-6
      • Component Numerator
        N-Acetylgalactosamine-4-Sulfatase
        LP14031-6
        • Component Numerator Core
          N-Acetylgalactosamine-4-Sulfatase
          LP14031-6
        • Component Numerator Core Suffix
          NULL
           
      • Component Denominator
        NULL
         
        • Component Denominator Core
          NULL
           
        • Component Denominator Core Suffix
          NULL
           
    • Challenge
      NULL
       
    • Adjustment
      NULL
       
    • Count
      NULL
       
  • Property
    CCnc
    LP6789-4
  • Time
    Pt
    LP6960-1
  • System
    WBC
    LP7720-8
    • System Core
      WBC
      LP7720-8
    • Super System
      NULL
       
  • Scale
    Qn
    LP7753-9
  • Method
    NULL
     

Basic Attributes

Class
CHEM
Type
Laboratory
First Released
Version 1.0
Last Updated
Version 2.73 (MIN)
Order vs. Observation
Both
Common Test Rank Get Info
15724

Language Variants Get Info

TagLanguageTranslation
cs-CZCzech (Czechia)N-acetylgalaktosamin-4-sulfatáza:Katalytická koncentrace:Časový bod:Leukocyty:Kvantitativní:
el-GRGreek (Greece)Ν-ακετυλογαλακτοζαμίνη-4-σουλφατάση:CCnc:Pt:Αριθμός λευκών αιμοσφαιρίων:Qn:
Synonyms: CCnc CHEM N Pt Qn Αριθμός λευκών αιμοσφαιρίων Ν-ακετυλογαλακτοζαμίνη-4-σουλφατάση
es-ARSpanish (Argentina)N-acetilgalactosamina-4-sulfatasa:concentración catalítica:punto en el tiempo:leucocito:cuantitativo:
es-ESSpanish (Spain)N-Acetilgalactosamina-4-sulfatasa:Concentración Catalítica:Punto temporal:Células sanguineas blancas:Qn:
Synonyms: Cuantitativo
es-MXSpanish (Mexico)N-acetilgalactosamina-4-sulfatasa:Concentración catalítica:Punto temporal:células blancas de la sangre:Cuantitativo:
et-EEEstonian (Estonia)N-atsetüülgalaktosamiin-4-sulfataas:CCnc:Pt:WBC:Qn:
Synonyms: Juhuslik Kvantitatiivne Leukotsüüdid
fr-CAFrench (Canada)N-acétylgalactosamine-4-sulfatase:Concentration catalytique:Temps ponctuel:Leucocytes:Quantitatif:
fr-FRFrench (France)Arylsulfatase B:Catalytique/Volume:Ponctuel:Leucocytes:Numérique:
fr-BEFrench (Belgium)N-acétylgalactosamine-4-sulfatase:Concentration catalytique:Temps ponctuel:Leucocytes:Quantitatif:
it-ITItalian (Italy)N-Acetilgalattosammina-4-Solfatasi:CCnC:Pt:WBC:Qn:
Synonyms: Chimica Concentrazione Catalitica Globuli bianchi Punto nel tempo (episodio)
ko-KRKorean (Korea, Republic Of)N-아세틸갈락토스아민-4-술파타아제:촉매농도:검사시점:백혈구:정량:
nl-NLDutch (Netherlands)N-acetylgalactosamine-4-sulfatase:enzymatische activiteit/volume:moment:leukocyten:kwantitatief:
Synonyms: witte bloedcellen
pt-BRPortuguese (Brazil)N-Acetilgalactosamina-4-Sulfatase:CCnc:Pt:Leucoc:Qn:
Synonyms: ; Arylsulfatase B; Maroteaux-Llamy disease; MPS VI; rhASB; rh4S; Aryl sulfatase B; Catalytic Concentration; Point in time; Random; Leukocytes; White blood cells; Leucocs; Quantitative; QNT; Quant; Quan; Chemistry
ru-RURussian (Russian Federation)N-Ацетилгалактозамин-4-Сульфатаза:КаталКонц:ТчкВрм:Лейкоциты:Колич:
Synonyms: Каталитическая концентрация Количественный Точка во времени;Момент
tr-TRTurkish (Turkey)N-asetilgalaktozamin-4-Sülfataz:KtlKons:Zmlı:Lökosit:Kant:
Synonyms: WBC
zh-CNChinese (China)N-乙酰半乳糖胺-4-硫酸酯酶:催化浓度:时间点:白细胞:定量型:
Synonyms: Maroteaux-Llamy 氏病;Maroteaux-Llamy 病;MPS VI;N-乙酰氨基半乳糖-4-硫酸酯酶;N-乙酰软骨糖胺-4-硫酸酯酶;rh4S;rhASB;芳基硫酸酯酶 B N 型 WBC;WBCs;白血球;白血细胞 催化浓度(单位体积);单位体积内酶的单位数 化学;化学检验项目;化学检验项目类;化学类;化学试验;非刺激耐受型化学检验项目;非刺激耐受型化学检验项目类;非刺激耐受型化学试验;非刺激耐受型化学试验类 可用数量表示的;定量性;数值型;数量型;连续数值型标尺 时刻;随机;随意;瞬间

LOINC Terminology Service (API) using HL7® FHIR® Get Info

CodeSystem lookup
https://fhir.loinc.org/CodeSystem/$lookup?system=http://loinc.org&code=2648-4