Version 2.77

Part Descriptions

LP15432-5   Beta aminoisobutyrate
3-Aminoisobutyric acid is a product formed by the catabolism of thymine. Copyright Text is available under the Creative Commons Attribution/Share-Alike License. See http://creativecommons.org/licenses/by-sa/3.0/ for details. Source: Wikipedia, Wikipedia

LP15432-5   Beta aminoisobutyrate
Beta aminoisobutyric acid (BAIB) is a nonprotein amino acid that is an end product of pyrimidine metabolism. The R and S enantiomers (previously named D-(minus)-BAIB and L-plus-BAIB) are produced from thymine and L-valine, respectively. Under normal circumstances, urine contains predominantly R-BAIB (from thymine) because it is eliminated by filtration and tubular secretion, while plasma contains about 80% S-BAIB (from valine), which is reabsorbed in the kidneys. In patients with dihydropyrimidine dehydrogenase deficiency, thymine catabolism is decreased, which results in moderately decreased CSF concentration and markedly decreased plasma concentration of BAIB. On the other hand, urine BAIB is elevated despite decreased breakdown of thymine, which indicates that there must be cross-over in the thymine and valine degradation pathways. PMID: 14705962 Deficiency of D-beta-aminoisobutyrate:pyruvate aminotransferase (EC 2.6.1.40) , an enzyme that is involved in the catabolism R-BAIB, also results in elevated urine BAIB and is associated with hyperuricemia. [OMIM: 210100] Source: Regenstrief LOINC, PMID: 14705962

Fully-Specified Name

Component
Beta aminoisobutyrate
Property
SCnc
Time
Pt
System
CSF
Scale
Qn
Method

Additional Names

Short Name
B-AIB CSF-sCnc
Display Name
Beta aminoisobutyrate (CSF) [Moles/Vol]
Consumer Name Alpha Get Info
Beta aminoisobutyrate, Spinal fluid

Basic Attributes

Class
CHEM
Type
Laboratory
First Released
Version 2.00
Last Updated
Version 2.73
Order vs. Observation
Observation
Common Test Rank Get Info
8792

Member of these Panels

LOINC Long Common Name
35507-3 Amino acids panel [Moles/volume] - Cerebral spinal fluid
79603-7 Beta alanine and Beta aminoisobutyrate and Gamma aminobutyrate panel - Cerebral spinal fluid

Member of these Groups Get Info

LOINC Group Group Name
LG48155-2 Beta aminoisobutyrate|Pt|CSF

Language Variants Get Info

Tag Language Translation
de-AT German (Austria) Synonyms: Beta-Aminoisobuttersäure /L
de-DE German (Germany) Beta-Aminoisobutyrat:Stoffmengenkonzentration:Zeitpunkt:Liquor:Quantitativ:
Synonyms: Zerebrospinalflüssigkeit
es-AR Spanish (Argentina) beta aminoisobutirato:concentración de sustancia:punto en el tiempo:líquido cefalorraquídeo:cuantitativo:
es-MX Spanish (Mexico) Beta aminoisobutirato:Concentración de sustancias:Punto temporal:Fluído espinal cerebral:Cuantitativo:
es-ES Spanish (Spain) Beta aminoisobutirato:Concentración de sustancia:Punto temporal:Líquido Cefalorraquideo:Qn:
Synonyms: Cuantitativo
et-EE Estonian (Estonia) Beetaaminoisobutüraat:SCnc:Pt:CSF:Qn:
Synonyms: Aine kontsentratsioon Juhuslik Kvantitatiivne Liikvor
fr-FR French (France) Bêta aminoisobutyrate:Moles/Volume:Ponctuel:Liquide céphalorachidien:Numérique:
fr-BE French (Belgium) Béta-aminoisobutyrate:Concentration de substance:Temps ponctuel:LCR:Quantitatif:
fr-CA French (Canada) Bêta-aminoisobutyrate:Concentration de substance:Temps ponctuel:LCR:Quantitatif:
it-IT Italian (Italy) Beta aminoisobutirrato:SCnc:Pt:LCS:Qn:
Synonyms: Chimica Concentrazione di Sostanza Liquido cerebrospinale Punto nel tempo (episodio)
ko-KR Korean (Korea, Republic Of) 베타 아미노이소뷰티레이트:물질농도:검사시점:뇌척수액:정량:
nl-NL Dutch (Netherlands) bèta-amino-isobutyraat:mol/volume:moment:liquor cerebrospinalis:kwantitatief:
pt-BR Portuguese (Brazil) Beta aminoisobutirato:SCnc:Pt:LCR:Qn:
Synonyms: ; B-AIB; 3-aminoisobutyrate; 3-aminoisobutyric acid; Substance concentration; Level; Point in time; Random; Cerebral spinal fluid; Spinal Fluid; Cerebrospinal Fl; Spinal Flu; Spinal Fld; Quantitative; QNT; Quant; Quan; B; Chemistry
ru-RU Russian (Russian Federation) Бета аминоизобутират:МолКонц:ТчкВрм:ЦСЖ:Колич:
Synonyms: Бета-аминоизобутират Количественный Молярность;Молярная объёмная концентрация Точка во времени;Момент Цереброспинальная жидкость
tr-TR Turkish (Turkey) Beta aminoizobütirat:SubKons:Zmlı:BOS:Kant:
uk-UA Ukrainian (Ukraine) Бета аміноізобутират:Молярна Концентрація:МоментЧасу:Спинномозкова рідина:Кількісно:
Synonyms: 3-aminoisobutyrate; 3-aminoisobutyric acid; B; B-AIB; Cerebral spinal fluid; Cerebrospinal Fl; Chemistry; Level; Point in time; QNT; Quan; Quant; Quantitative; Random; Spinal Fl; Spinal Fld; Spinal Flu; Spinal Fluid; Substance concentration
zh-CN Chinese (China) Beta 氨基异丁酸:物质的量浓度:时间点:脑脊液:定量型:
Synonyms: 3-氨基异丁酸;B-AIB;Beta-氨基异丁酸;β氨基异丁酸;β-氨基异丁酸 B CSF CSF;脊髓液;Cerebral spinal fluid;脑脊髓液 β 克分子浓度;克分子浓度(单位体积);摩尔浓度;摩尔浓度(单位体积);物质的量浓度(单位体积) 化学;化学检验项目;化学检验项目类;化学类;化学试验;非刺激耐受型化学检验项目;非刺激耐受型化学检验项目类;非刺激耐受型化学试验;非刺激耐受型化学试验类 可用数量表示的;定量性;数值型;数量型;连续数值型标尺 时刻;随机;随意;瞬间 脊液 脊髓液 脑脊液(Cerebral spinal fluid,CSF) 脑脊髓液 贝塔

Example Units

Unit Source
umol/L Example UCUM Units

LOINC Terminology Service (API) using HL7® FHIR® Get Info

CodeSystem lookup
https://fhir.loinc.org/CodeSystem/$lookup?system=http://loinc.org&code=26590-0