Part Descriptions

LP15432-5   Beta aminoisobutyrate
3-Aminoisobutyric acid is a product formed by the catabolism of thymine. Copyright Text is available under the Creative Commons Attribution/Share-Alike License. See http://creativecommons.org/licenses/by-sa/3.0/ for details. Source: Wikipedia, Wikipedia

LP15432-5   Beta aminoisobutyrate
Beta aminoisobutyric acid (BAIB) is a nonprotein amino acid that is an end product of pyrimidine metabolism. The R and S enantiomers (previously named D-(minus)-BAIB and L-plus-BAIB) are produced from thymine and L-valine, respectively. Under normal circumstances, urine contains predominantly R-BAIB (from thymine) because it is eliminated by filtration and tubular secretion, while plasma contains about 80% S-BAIB (from valine), which is reabsorbed in the kidneys. In patients with dihydropyrimidine dehydrogenase deficiency, thymine catabolism is decreased, which results in moderately decreased CSF concentration and markedly decreased plasma concentration of BAIB. On the other hand, urine BAIB is elevated despite decreased breakdown of thymine, which indicates that there must be cross-over in the thymine and valine degradation pathways. PMID: 14705962 Deficiency of D-beta-aminoisobutyrate:pyruvate aminotransferase (EC 2.6.1.40) , an enzyme that is involved in the catabolism R-BAIB, also results in elevated urine BAIB and is associated with hyperuricemia. [OMIM: 210100] Source: Regenstrief LOINC, PMID: 14705962

LOINC Names Get Info

Fully-Specified Name
Beta aminoisobutyrate:SCnc:Pt:Ser/Plas:Qn:
Long Common Name
Beta aminoisobutyrate [Moles/volume] in Serum or Plasma
Short Name
B-AIB SerPl-sCnc
Display Name
Beta aminoisobutyrate [Moles/Vol]
Consumer Name Alpha Get Info
Beta aminoisobutyrate, Blood

Part Model Get Info

  • Component
    Beta aminoisobutyrate
    LP15432-5
    • Analyte
      Beta aminoisobutyrate
      LP15432-5
      • Component Numerator
        Beta aminoisobutyrate
        LP15432-5
        • Component Numerator Core
          Beta aminoisobutyrate
          LP15432-5
        • Component Numerator Core Suffix
          NULL
           
      • Component Denominator
        NULL
         
        • Component Denominator Core
          NULL
           
        • Component Denominator Core Suffix
          NULL
           
    • Challenge
      NULL
       
    • Adjustment
      NULL
       
    • Count
      NULL
       
  • Property
    SCnc
    LP6860-3
  • Time
    Pt
    LP6960-1
  • System
    Ser/Plas
    LP7576-4
    • System Core
      Ser/Plas
      LP7576-4
    • Super System
      NULL
       
  • Scale
    Qn
    LP7753-9
  • Method
    NULL
     

Basic Attributes

Class
CHEM
Type
Laboratory
First Released
Version 2.00
Last Updated
Version 2.73 (MIN)
Order vs. Observation
Observation
Common Test Rank Get Info
2852

Member of these Panels

LOINCLong Common Name
35083-5Amino acids panel [Moles/volume] - Serum or Plasma
79650-8Beta alanine and Beta aminoisobutyrate and Gamma aminobutyrate panel - Serum or Plasma

Member of these Groups Get Info

LOINC GroupGroup Name
LG52629-9Beta aminoisobutyrate|SCnc|Pt|ANYBldSerPl

Language Variants Get Info

TagLanguageTranslation
cs-CZCzech (Czechia)Beta-aminoizobutyrát:Látková koncentrace:Časový bod:Sérum/plazma:Kvantitativní:
de-ATGerman (Austria)Synonyms: Beta-Aminoisobutyrat
de-DEGerman (Germany)Beta-Aminoisobutyrat:Stoffmengenkonzentration:Zeitpunkt:Serum oder Plasma:Quantitativ:
el-GRGreek (Greece)β-αμινοϊσοβουτυρικό:SCnc:Pt:Ορός/Πλάσμα:Qn:
Synonyms: CHEM Pt Qn SCnc β-αμινοϊσοβουτυρικό Ορός Ορός/Πλάσμα Πλάσμα
es-ARSpanish (Argentina)beta aminoisobutirato:concentración de sustancia:punto en el tiempo:plasma:cuantitativo:
es-ESSpanish (Spain)Beta aminoisobutirato:Concentración de sustancia:Punto temporal:Suero o Plasma:Qn:
Synonyms: Cuantitativo
es-MXSpanish (Mexico)Beta aminoisobutirato:Concentración de sustancias:Punto temporal:Suero o Plasma:Cuantitativo:
et-EEEstonian (Estonia)Beetaaminoisobutüraat:SCnc:Pt:S/P:Qn:
Synonyms: Aine kontsentratsioon Juhuslik Kvantitatiivne Plasma Seerum Seerum või plasma
fr-CAFrench (Canada)Bêta-aminoisobutyrate:Concentration de substance:Temps ponctuel:Sérum/Plasma:Quantitatif:
fr-FRFrench (France)Bêta aminoisobutyrate:Moles/Volume:Ponctuel:Sérum/Plasma:Numérique:
fr-BEFrench (Belgium)Béta-aminoisobutyrate:Concentration de substance:Temps ponctuel:Sérum/Plasma:Quantitatif:
it-ITItalian (Italy)Beta aminoisobutirrato:SCnc:Pt:Siero/Plasma:Qn:
Synonyms: Chimica Concentrazione di Sostanza Plasma Punto nel tempo (episodio) Siero Siero o Plasma
ko-KRKorean (Korea, Republic Of)베타 아미노이소뷰티레이트:물질농도:검사시점:혈청/혈장:정량:
nl-NLDutch (Netherlands)bèta-amino-isobutyraat:mol/volume:moment:serum of plasma:kwantitatief:
pl-PLPolish (Poland)Beta aminoizomaślan:stężenie molowe:punkt w czasie:surowica lub osocze:ilościowy:
pt-BRPortuguese (Brazil)Beta aminoisobutirato:SCnc:Pt:Sor/Plas:Qn:
Synonyms: ; B-AIB; 3-aminoisobutyrate; 3-aminoisobutyric acid; Substance concentration; Level; Point in time; Random; SerPl; SerPlas; SerP; Serum; SR; Plasma; Pl; Plsm; Quantitative; QNT; Quant; Quan; B; Chemistry
ru-RURussian (Russian Federation)Бета аминоизобутират:МолКонц:ТчкВрм:Сыв/Плаз:Колич:
Synonyms: Бета-аминоизобутират Количественный Молярность;Молярная объёмная концентрация Плазма Сыворотка Сыворотка или Плазма Точка во времени;Момент
tr-TRTurkish (Turkey)Beta aminoizobütirat:SubKons:Zmlı:Ser/Plaz:Kant:
uk-UAUkrainian (Ukraine)Бета аміноізобутират:Молярна Концентрація:МоментЧасу:Сироватка/Плазма:Кількісно:
Synonyms: 3-aminoisobutyrate; 3-aminoisobutyric acid; B; B-AIB; Chemistry; Level; Pl; Plasma; Plsm; Point in time; QNT; Quan; Quant; Quantitative; Random; SerP; SerPl; SerPlas; Serum; Serum or plasma; SR; Substance concentration
zh-CNChinese (China)Beta 氨基异丁酸:物质的量浓度:时间点:血清/血浆:定量型:
Synonyms: 3-氨基异丁酸;B-AIB;Beta-氨基异丁酸;β氨基异丁酸;β-氨基异丁酸 B β 克分子浓度;克分子浓度(单位体积);摩尔浓度;摩尔浓度(单位体积);物质的量浓度(单位体积) 化学;化学检验项目;化学检验项目类;化学类;化学试验;非刺激耐受型化学检验项目;非刺激耐受型化学检验项目类;非刺激耐受型化学试验;非刺激耐受型化学试验类 可用数量表示的;定量性;数值型;数量型;连续数值型标尺 时刻;随机;随意;瞬间 血清或血浆 贝塔

Example Units

UnitSource
mcmol/dLREGENSTRIEF
mcmol/LREGENSTRIEF
umol/LExample UCUM Units

LOINC Terminology Service (API) using HL7® FHIR® Get Info

CodeSystem lookup
https://fhir.loinc.org/CodeSystem/$lookup?system=http://loinc.org&code=26605-6