Version 2.77

Part Descriptions

LP15432-5   Beta aminoisobutyrate
3-Aminoisobutyric acid is a product formed by the catabolism of thymine. Copyright Text is available under the Creative Commons Attribution/Share-Alike License. See http://creativecommons.org/licenses/by-sa/3.0/ for details. Source: Wikipedia, Wikipedia

LP15432-5   Beta aminoisobutyrate
Beta aminoisobutyric acid (BAIB) is a nonprotein amino acid that is an end product of pyrimidine metabolism. The R and S enantiomers (previously named D-(minus)-BAIB and L-plus-BAIB) are produced from thymine and L-valine, respectively. Under normal circumstances, urine contains predominantly R-BAIB (from thymine) because it is eliminated by filtration and tubular secretion, while plasma contains about 80% S-BAIB (from valine), which is reabsorbed in the kidneys. In patients with dihydropyrimidine dehydrogenase deficiency, thymine catabolism is decreased, which results in moderately decreased CSF concentration and markedly decreased plasma concentration of BAIB. On the other hand, urine BAIB is elevated despite decreased breakdown of thymine, which indicates that there must be cross-over in the thymine and valine degradation pathways. PMID: 14705962 Deficiency of D-beta-aminoisobutyrate:pyruvate aminotransferase (EC 2.6.1.40) , an enzyme that is involved in the catabolism R-BAIB, also results in elevated urine BAIB and is associated with hyperuricemia. [OMIM: 210100] Source: Regenstrief LOINC, PMID: 14705962

Fully-Specified Name

Component
Beta aminoisobutyrate
Property
SCnc
Time
Pt
System
Amnio fld
Scale
Qn
Method

Additional Names

Short Name
B-AIB Amn-sCnc
Display Name
Beta aminoisobutyrate (Amn fld) [Moles/Vol]
Consumer Name Alpha Get Info
Beta aminoisobutyrate, Amniotic fluid

Basic Attributes

Class
CHEM
Type
Laboratory
First Released
Version 2.00
Last Updated
Version 2.70
Order vs. Observation
Observation

Member of these Panels

LOINC Long Common Name
35508-1 Amino acids panel [Moles/volume] - Amniotic fluid

Member of these Groups Get Info

LOINC Group Group Name
LG48156-0 Beta aminoisobutyrate|Pt|Amnio fld

Language Variants Get Info

Tag Language Translation
de-DE German (Germany) Beta-Aminoisobutyrat:Stoffmengenkonzentration:Zeitpunkt:Amnionflüssigkeit:Quantitativ:
es-AR Spanish (Argentina) beta aminoisobutirato:concentración de sustancia:punto en el tiempo:líquido amniótico:cuantitativo:
es-ES Spanish (Spain) Beta aminoisobutirato:Concentración de sustancia:Punto temporal:Fluido Ammiótico:Qn:
Synonyms: Cuantitativo
es-MX Spanish (Mexico) Beta aminoisobutirato:Concentración de sustancias:Punto temporal:Líquido amniótico:Cuantitativo:
et-EE Estonian (Estonia) Beetaaminoisobutüraat:SCnc:Pt:AmnF:Qn:
Synonyms: Aine kontsentratsioon Amnionivedelik Juhuslik Kvantitatiivne
fr-CA French (Canada) Bêta-aminoisobutyrate:Concentration de substance:Temps ponctuel:Liquide amniotique:Quantitatif:
fr-FR French (France) Bêta aminoisobutyrate:Moles/Volume:Ponctuel:Liquide amniotique:Numérique:
fr-BE French (Belgium) Béta-aminoisobutyrate:Concentration de substance:Temps ponctuel:Liquide amniotique:Quantitatif:
it-IT Italian (Italy) Beta aminoisobutirrato:SCnc:Pt:Liquido amniotico:Qn:
Synonyms: Chimica Concentrazione di Sostanza Liquido amniotico Punto nel tempo (episodio)
ko-KR Korean (Korea, Republic Of) 베타 아미노이소뷰티레이트:물질농도:검사시점:양수:정량:
nl-NL Dutch (Netherlands) bèta-amino-isobutyraat:mol/volume:moment:vruchtwater:kwantitatief:
pt-BR Portuguese (Brazil) Beta aminoisobutirato:SCnc:Pt:LiqAmni:Qn:
Synonyms: ; B-AIB; 3-aminoisobutyrate; 3-aminoisobutyric acid; Substance concentration; Level; Point in time; Random; Amn; Amniotic fluid; Amn fl; Amniotic flu; AF; Quantitative; QNT; Quant; Quan; B; Chemistry
ru-RU Russian (Russian Federation) Бета аминоизобутират:МолКонц:ТчкВрм:Амниотич ждк:Колич:
Synonyms: Амниотическая жидкость Бета-аминоизобутират Количественный Молярность;Молярная объёмная концентрация Точка во времени;Момент
tr-TR Turkish (Turkey) Beta aminoizobütirat:SubKons:Zmlı:Amniyon sv:Kant:
Synonyms: Amniyon mayii
zh-CN Chinese (China) Beta 氨基异丁酸:物质的量浓度:时间点:羊水:定量型:
Synonyms: 3-氨基异丁酸;B-AIB;Beta-氨基异丁酸;β氨基异丁酸;β-氨基异丁酸 B β 克分子浓度;克分子浓度(单位体积);摩尔浓度;摩尔浓度(单位体积);物质的量浓度(单位体积) 化学;化学检验项目;化学检验项目类;化学类;化学试验;非刺激耐受型化学检验项目;非刺激耐受型化学检验项目类;非刺激耐受型化学试验;非刺激耐受型化学试验类 可用数量表示的;定量性;数值型;数量型;连续数值型标尺 时刻;随机;随意;瞬间 羊膜水;胎水 贝塔

Example Units

Unit Source
umol/dL Example UCUM Units

LOINC Terminology Service (API) using HL7® FHIR® Get Info

CodeSystem lookup
https://fhir.loinc.org/CodeSystem/$lookup?system=http://loinc.org&code=27217-9