Part Description

LP18400-9   2-Hydroxy-3-Methylvalerate
2-hydroxy-3-methylvaleric acid (HMVA) is an acid generated by L-isoleucine oxidation pathway and involves four stereoisomers (2S,3S-HMVA, 2R,3R-HMVA, 2S,3R-HMVA and 2R,3S-HMVA). Increased levels of HMVA are found in patients with maple syrup urine disease (MSUD), an inherited metabolic disease characterized by sweet-smelling urine, ketoacidosis, seizures, and neurological dysfunction. Source: Regenstrief LOINC

LOINC Names Get Info

Fully-Specified Name
2-Hydroxy-3-Methylvalerate:PrThr:Pt:Urine:Ord:
Long Common Name
2-Hydroxy-3-Methylvalerate [Presence] in Urine
Short Name
2OH3Me-valerate Ur Ql
Display Name
2-Hydroxy-3-Methylvalerate Ql (U)
Consumer Name Alpha Get Info
2-Hydroxy-3-Methylvalerate, Urine

Part Model Get Info

  • Component
    2-Hydroxy-3-Methylvalerate
    LP18400-9
    • Analyte
      2-Hydroxy-3-Methylvalerate
      LP18400-9
      • Component Numerator
        2-Hydroxy-3-Methylvalerate
        LP18400-9
        • Component Numerator Core
          2-Hydroxy-3-Methylvalerate
          LP18400-9
        • Component Numerator Core Suffix
          NULL
           
      • Component Denominator
        NULL
         
        • Component Denominator Core
          NULL
           
        • Component Denominator Core Suffix
          NULL
           
    • Challenge
      NULL
       
    • Adjustment
      NULL
       
    • Count
      NULL
       
  • Property
    PrThr
    LP217195-9
  • Time
    Pt
    LP6960-1
  • System
    Urine
    LP7681-2
    • System Core
      Urine
      LP7681-2
    • Super System
      NULL
       
  • Scale
    Ord
    LP7751-3
  • Method
    NULL
     

Basic Attributes

Class
CHEM
Type
Laboratory
First Released
Version 2.04
Last Updated
Version 2.73 (MIN)
Change Reason
The PrThr property is used for LOINC terms whose results are reported using an ordered categorical scale, regardless of whether or not an internal threshold was used to make that determination. This change was approved by the Laboratory LOINC Committee in June 2016.
Order vs. Observation
Observation
Common Test Rank Get Info
14085

Language Variants Get Info

TagLanguageTranslation
cs-CZCzech (Czechia)2-hydroxy-3-methylvalerát:Přítomnost nebo práh:Časový bod:Moč:Ordinální:
de-DEGerman (Germany)2-Hydroxy-3-Methylvalerat:Nachweis oder Schwellenwert:Zeitpunkt:Urin:Ordinal:
el-GRGreek (Greece)2-υδροξυ-3-μεθυλοβαλεριανικό:PrThr:Pt:Ούρα:Ord:
Synonyms: 2-υδροξυ-3-μεθυλοβαλεριανικό CHEM Ord PrThr Pt Ούρα
es-ARSpanish (Argentina)2-hidroxi-3-metilvalerato:concentración arbitraria:punto en el tiempo:orina:ordinal:
es-ESSpanish (Spain)2-Hidroxi-3-Metilvalerato:PrThr:Punto temporal:Orina:Ord:
es-MXSpanish (Mexico)2-hidroxi-3-metilvalerato:Presencia o umbral:Punto temporal:Orina:Ordinal:
et-EEEstonian (Estonia)2-hüdroksü-3-metüülvaleraat:PrThr:Pt:U:Ord:
Synonyms: Järgarvuline Juhuslik Uriin
fr-CAFrench (Canada)2-hydroxy-3-méthylvalérate:Présence-Seuil:Temps ponctuel:Urine:Ordinal:
fr-FRFrench (France)2-hydroxy-3-méthylvalérate:Présence/Seuil:Ponctuel:Urine:Qualitatif:
fr-BEFrench (Belgium)2-hydroxy-3-méthylvalérate:PrThr:Temps ponctuel:Urine:Ordinal:
it-ITItalian (Italy)2-Idrossi-3-Metilvalerato:PrThr:Pt:Urine:Ord:
Synonyms: Chimica Presenza o Soglia Punto nel tempo (episodio)
ko-KRKorean (Korea, Republic Of)2-하이드록시-3-메틸발레레이트:임의농도:검사시점:뇨:순위척도:
nl-NLDutch (Netherlands)2-hydroxy-3-methylvaleraat:aanwezigheid:moment:urine:ordinaal:
pl-PLPolish (Poland)2-Hydroksy-3-Metylowalerian:granica wykrywalności:punkt w czasie:mocz:uporządkowany:
Synonyms: Kwas 2-hydroksy-3-metylobutanowy
pt-BRPortuguese (Brazil)2-Hidroxi-3-Metilvalerato:ACnc:Pt:Urina:Ord:
Synonyms: ; 2OH3Me-valerate; 2-hydroxy-3-methylvaleric acid; Arbitrary concentration; Point in time; Random; Ur; UR; Urn; UA; Ql; Ordinal; QL; Qualitative; Qual; Screen; Hydrox; OH; III; II; Chemistry
ru-RURussian (Russian Federation)2-Гидрокси-3-Метилвалерат:PrThr:ТчкВрм:Моча:Пор:
Synonyms: Порядковый Точка во времени;Момент
tr-TRTurkish (Turkey)2-Hidroksi-3-Metilvalerat:MevcEşik:Zmlı:İdrar:Srl:
Synonyms: Mevcut
zh-CNChinese (China)2-羟基-3-甲基戊酸:存在情况或阈值:时间点:尿液:序数型:
Synonyms: 2OH3Me-戊酸 Ⅱ Ⅲ Hydroxy II III OH 三 依次型;分类顺序型;定性的;序数型(或称等级型);性质上的;有序型;有序性分类应答;有序性分类结果;秩次型;等级型;筛查;顺序型 化学;化学检验项目;化学检验项目类;化学类;化学试验;非刺激耐受型化学检验项目;非刺激耐受型化学检验项目类;非刺激耐受型化学试验;非刺激耐受型化学试验类 叁 存在情况;存在;存在与否;是否存在;阈值;界值;界限;阀值;临界值;存在情况(存在、存在与否、是否存在)或阈值(界值、界限、阀值、临界值) 尿;小便;下泉 时刻;随机;随意;瞬间 羟

LOINC Terminology Service (API) using HL7® FHIR® Get Info

CodeSystem lookup
https://fhir.loinc.org/CodeSystem/$lookup?system=http://loinc.org&code=29880-2