Version 2.80

Part Description

LP32459-7   von Willebrand factor cleaving protease inhibitor
von Willebrand factor (vWF) cleaving protease, or ADAMTS13, is a metalloprotease that cleaves vWF and thereby limits platelet aggregation and formation of microthrombi. vWF cleaving protease inhibitors can decrease the protease activity and/or more rapidly remove the enzyme from the circulation. Such inhibitors are one cause of thrombotic thrombocytopenic purpura (TTP), a disorder characterized by thrombocytopenia, anemia, fever, and neurologic and renal abnormalities. Idiopathic TTP is often due to anti-ADAMTS13 autoantibodies, while inherited TTP is an autosomal recessive disorder due to mutations in the ADAMTS13 gene that lead to impaired protease function. Work-up of patients with TTP can include vWF cleaving protease activity and, if that activity is low, inhibitor screen followed by quantification. PMID: 18756543 Source: Regenstrief LOINC

Fully-Specified Name

Component
von Willebrand factor cleaving protease inhibitor
Property
ACnc
Time
Pt
System
PPP
Scale
Qn
Method

Additional Names

Long Common Name
von Willebrand factor (vWf) cleaving protease inhibitor [Units/volume] in Platelet poor plasma
Short Name
vWF Cp Inhib PPP-aCnc
Display Name
vWf cleaving protease inhibitor Qn (PPP)
Consumer Name Alpha Get Info
vWf cleaving protease inhibitor, Blood

Basic Attributes

Class
COAG
Type
Laboratory
First Released
Version 2.15
Last Updated
Version 2.73 (MIN)
Order vs. Observation
Both
Common Test Rank Get Info
8839

Language Variants Get Info

Tag Language Translation
de-AT German (Austria) Synonyms: ADAMTS 13 Inhibitor
de-DE German (Germany) von Willebrand-Faktor spaltender Proteaseinhibitor:Arbiträre Konzentration:Zeitpunkt:Thrombozytenarmes Plasma:Quantitativ:
el-GR Greek (Greece) αναστολέας πρωτεάσης διάσπασης παράγοντα Von Willebrand:ACnc:Pt:PPP:Qn:
Synonyms: ACnc αναστολέας πρωτεάσης διάσπασης παράγοντα Von Willebrand παράγοντας Von Willebrand πρωτεάση διάσπασης παράγοντα Von Willebrand
es-ES Spanish (Spain) Inhibidor de la proteasa divisora del Factor de von Villebrand:Concentración arbitraria:Punto temporal:Plasma pobre en plaquetas:Qn:
Synonyms: Cuantitativo
es-MX Spanish (Mexico) Inhibidor de la proteasa que escinde el factor von Willebrand:Concentración arbitraria:Punto temporal:Plasma pobre en plaquetas:Cuantitativo:
fr-CA French (Canada) Inhibiteur de la protéase clivage du Facteur von Willebrand:Concentration arbitraire:Temps ponctuel:Plasma pauvre en plaquettes:Quantitatif:
fr-FR French (France) Facteur Willebrand inhibiteur de la protéase:Arbitraire/Volume:Ponctuel:Plasma pauvre en plaquettes:Numérique:
fr-BE French (Belgium) Inhibiteur de la protéase de coupage Facteur von Willebrand:Concentration arbitraire:Temps ponctuel:Plasma pauvre en plaquettes:Quantitatif:
Synonyms: Fvw
it-IT Italian (Italy) von Willebrand, inibitore proteasi di taglio fattore:ACnc:Pt:PPP:Qn:
Synonyms: Concentrazione Arbitraria Fattore di von Willebrand (vWf) Inibitore di proteasi di taglio del fattore di von Plasma povero di piastrine Proteasi di taglio del fattore di von Willebrand Punto nel tempo (episodio) Studio di coagulazione
ko-KR Korean (Korea, Republic Of) 폰 빌레브란트 인자 절단 단백분해효소 억제인자:임의농도:검사시점:혈소판제거혈장:정량:
nl-NL Dutch (Netherlands) von Willebrand-factor cleaving protease inhibitor:eenheid/volume:moment:plaatjesarm plasma:kwantitatief:
Synonyms: coagulatiemethode
pt-BR Portuguese (Brazil) Fator de von Willebrand clivagem do inibidor de protease:ACnc:Pt:PPPQ:Qn:
Synonyms: ; vWF Cp Inhib; ADAMTS13 inhibitor; vWCP; VWF-cp; VWFCP; vWf; Arbitrary concentration; Point in time; Random; Platelet poor plasma; Plas; Quantitative; QNT; Quant; Quan; Vonwillebrand; Von will; PR; Inhibit; Fac; Fact; COAGULATION
ru-RU Russian (Russian Federation) von Willebrand (vWf) расщепляющая протеаза ингибитор:ПроизвКонц:ТчкВрм:ОПП:Колич:
Synonyms: Количественный Обеднённая пластинками плазма;Бедная тромбоцитами плазма Произвольная концентрация Точка во времени;Момент
tr-TR Turkish (Turkey) von Willebrand faktörü parçalıyıcı proteaz inhibitörü:SçKons:Zmlı:TFkP:Kant:
uk-UA Ukrainian (Ukraine) інгібітор протеази, що розщеплює Фактор фон Віллебранда:Довільна Концентрація:МоментЧасу:Бідна тромбоцитами плазма:Кількісно:
Synonyms: ADAMTS13; ADAMTS-13; ADAMTS13 inhibitor; Arbitrary concentration; COAGULATION; Fac; Fact; Hematology; Heme; Inhib; Inhibit; Plas; Platelet poor plasma; Point in time; PR; QNT; Quan; Quant; Quantitative; Random; TTP; Von will; Vonwillebrand; vWCP; vWf; vWF Cp; vWF Cp Inhib; VWFCP; VWF-cp
zh-CN Chinese (China) von Willebrand 因子裂解蛋白酶抑制剂:任意型浓度:时间点:贫血小板血浆:定量型:
Synonyms: von Willebrand von Willebrand 因子（von Willebrand Factor，vWf）;vWf;vWf 因子;血管性假血友病因子;血管性血友病因子 von Willebrand 因子（vWf 因子、血管性假血友病因子、血管性血友病因子）裂解蛋白酶;ADAMTS13;von Willebrand 因子裂解蛋白酶（von Willebrand Factor Cleaving Protease，VWF-cp）;von Willebrand 因子裂解酶;vWCP;vWf 因子裂解蛋白酶;vWf 因子裂解酶;vWf 裂解酶;VWFCP;VWF-cp;血管性血友病因子裂解蛋白酶;血管性血友病因子裂解酶 von Willebrand 因子（vWf 因子、血管性假血友病因子、血管性血友病因子）裂解蛋白酶抑制剂;ADAMTS13 抑制剂;von Willebrand 因子裂解酶抑制剂;vWf 因子裂解蛋白酶抑制剂;vWf 因子裂解酶抑制剂;vWf 裂解蛋白酶抑制剂;vWf 裂解酶抑制剂;血管性血友病因子裂解蛋白酶抑制剂;血管性血友病因子裂解酶抑制剂 乏血小板血浆;Platelet poor plasma;PPP 任意型浓度(单位体积);任意浓度;单位体积的任意单位数;人工型浓度 冯·威勒布兰德 冯威勒布兰德 冯威勒布兰德氏 凝血功能;凝血功能试验;凝血过程;血液凝固;血液凝固功能;血液凝固过程 可用数量表示的;定量性;数值型;数量型;连续数值型标尺 因素 抑制因子 抑制物 抑制物质 时刻;随机;随意;瞬间 朊酶 系数 蛋白质酵素

Example Units

Unit Source
Inhibitor Units REGENSTRIEF
[arb'U]/mL Example UCUM Units

LOINC Terminology Service (API) using HL7® FHIR® Get Info

CodeSystem lookup
https://fhir.loinc.org/CodeSystem/$lookup?system=http://loinc.org&code=40824-5