Version 2.80

Part Description

LP157346-0   Tripeptidyl peptidase I
Tripeptidyl peptidase 1 is an enzyme that sequentially removes tripeptides from the N termini of proteins. It is encoded by the TPP1 gene, located on chromosome 11p15.4. Mutations in TPP1 cause abnormal protein folding, which results in defective enzyme activity and a disorder known as neuronal ceroid lipofuscinosis-2 (CLN2), or Jansky-Bielschowsky disease. CLN2 is a progressive neurodegenerative disorder characterized by dementia, seizures, and visual failure. [OMIM: 204500] Source: Regenstrief LOINC , OMIM: 204500

Fully-Specified Name

Component
Tripeptidyl peptidase I
Property
CCnt
Time
Pt
System
Fibroblasts
Scale
Qn
Method

Additional Names

Long Common Name
Tripeptidyl peptidase I [Enzymatic activity/mass] in Fibroblast
Short Name
Tripeptidyl peptidase I Fib-cCnt
Display Name
Tripeptidyl peptidase I (Fibroblast) [Catalytic activity/Mass]
Consumer Name Alpha Get Info
Tripeptidyl Peptidase I, Fibroblast

Basic Attributes

Class
CHEM
Type
Laboratory
First Released
Version 2.48
Last Updated
Version 2.48 (MIN)
Order vs. Observation
Both

Member of these Panels

LOINC Long Common Name
93703-7 Palmitoyl protein thioesterase 1 and Tripeptidyl peptidase 1 panel - Fibroblast

Language Variants Get Info

Tag Language Translation
el-GR Greek (Greece) Τριπεπτιδυλική πεπτιδάση I:CCnt:Pt:Ινοβλάστες:Qn:
Synonyms: CCnt I Τριπεπτιδυλική πεπτιδάση I
es-MX Spanish (Mexico) Tripeptidil peptidasa I:Contenido catalítico:Punto temporal:Fibroblasto:Cuantitativo:
es-ES Spanish (Spain) Tripeptidil peptidasa I:Contenido catalítico:Punto temporal:Fibroblastos:Qn:
Synonyms: Cuantitativo
fr-FR French (France) Tripeptidyl peptidase I:Catalytique/Masse:Ponctuel:Fibroblastes:Numérique:
it-IT Italian (Italy) Tripeptidil-peptidasi I:CCnt:Pt:Fibroblasti:Qn:
Synonyms: Chimica Contenuto Catalitico Fibroblasto Punto nel tempo (episodio)
nl-NL Dutch (Netherlands) tripeptidylpeptidase I:enzymatische activiteit/massa:moment:fibroblast:kwantitatief:
pt-BR Portuguese (Brazil) Tripeptidil peptidase I::Pt:Fibroblastos:Qn:
ru-RU Russian (Russian Federation) Трипептидил пептидаза I:КаталСод:ТчкВрм:Фибробласты:Колич:
Synonyms: Каталитическое содержание Количественный Точка во времени;Момент
tr-TR Turkish (Turkey) Tripeptidil peptidaz I:Ktlİçrk:Zmlı:Fibroblastlar:Kant:
zh-CN Chinese (China) 三肽基肽酶 I:催化含量:时间点:成纤维细胞:定量型:
Synonyms: I 型 Tripeptidyl peptidase I;TPP I;TPPI;三肽酶 I 催化含量(单位质量);单位质量的酶单位数 化学;化学检验项目;化学检验项目类;化学类;化学试验;非刺激耐受型化学检验项目;非刺激耐受型化学检验项目类;非刺激耐受型化学试验;非刺激耐受型化学试验类 可用数量表示的;定量性;数值型;数量型;连续数值型标尺 时刻;随机;随意;瞬间 纤维原细胞;纤维母细胞

Example Units

Unit Source
nmol/h/mg{protein} Example UCUM Units

LOINC Terminology Service (API) using HL7® FHIR® Get Info

CodeSystem lookup
https://fhir.loinc.org/CodeSystem/$lookup?system=http://loinc.org&code=74576-0