Term Description

C3DC (Malonylcarnitine)+C4OH (3-Hydroxybutyrylcarnitine)/C10 (Decanoylcarnitine) is a marker for malonic acidemia (also known as malonic aciduria), which is one of the secondary conditions on the HHS Secretary's Recommended Uniform Screening Panel for newborn screening.

Part Description

LP70167-9   Decanoylcarnitine (C10)
Decanoylcarnitine is a primary marker for Medium-chain acyl-CoA dehydrogenase deficiency and Glutaric acidemia type II. Secondary marker for Medium-chain ketoacyl-CoA thiolase deficiency. Source: Regenstrief LOINC

LOINC Names Get Info

Fully-Specified Name
Malonylcarnitine (C3-DC)+3-Hydroxybutyrylcarnitine (C4-OH)/Decanoylcarnitine (C10):SRto:Pt:Bld.dot:Qn:
Long Common Name
Malonylcarnitine (C3-DC)+3-Hydroxybutyrylcarnitine (C4-OH)/Decanoylcarnitine (C10) [Molar ratio] in DBS
Short Name
Malonyl+3OHbutyrylcarn/C10 DBS-sRto
Display Name
C3-DC+C4-OH/Decanoylcarnitine (C10) (DBS) [Molar ratio]
Consumer Name Alpha Get Info
C3-DC+C4-OH/Decanoylcarnitine (C10), Dried blood spot

Part Model Get Info

  • Component
    Malonylcarnitine (C3-DC)+3-Hydroxybutyrylcarnitine (C4-OH)/Decanoylcarnitine (C10)
    LP286470-2
    • Analyte
      Malonylcarnitine (C3-DC)+3-Hydroxybutyrylcarnitine (C4-OH)/Decanoylcarnitine (C10)
      LP286470-2
      • Component Numerator
        Malonylcarnitine (C3-DC)+3-Hydroxybutyrylcarnitine (C4-OH)
        LP133649-6
        • Component Numerator Core
          Malonylcarnitine (C3-DC)+3-Hydroxybutyrylcarnitine (C4-OH)
          LP133649-6
        • Component Numerator Core Suffix
          NULL
           
      • Component Denominator
        Decanoylcarnitine (C10)
        LP70167-9
        • Component Denominator Core
          Decanoylcarnitine (C10)
          LP70167-9
        • Component Denominator Core Suffix
          NULL
           
    • Challenge
      NULL
       
    • Adjustment
      NULL
       
    • Count
      NULL
       
  • Property
    SRto
    LP6868-6
  • Time
    Pt
    LP6960-1
  • System
    Bld.dot
    LP21304-8
    • System Core
      Bld.dot
      LP21304-8
    • Super System
      NULL
       
  • Scale
    Qn
    LP7753-9
  • Method
    NULL
     

Basic Attributes

Class
CHEM
Type
Laboratory
First Released
Version 2.48
Last Updated
Version 2.61 (MIN)
Order vs. Observation
Both

Member of these Panels

LOINCLong Common Name
58092-8Acylcarnitine newborn screen panel
54089-8Newborn screening panel American Health Information Community (AHIC)

Language Variants Get Info

TagLanguageTranslation
cs-CZCzech (Czechia)Malonylkarnitin (C3-DC)+3-hydroxybutyrylkarnitin (C4-OH)/dekanoylkarnitin (C10):Látkový poměr:Časový bod:Suchá krevní kapka (DBS):Kvantitativní:
el-GRGreek (Greece)Μηλονυλοκαρνιτίνη (C3-DC)+3-υδροξυβουτυρυλοκαρνιτίνη (C4-OH)/Δεκανοϋλοκαρνιτίνη (C10):SRto:Pt:Bld.dot:Qn:
Synonyms: 3-υδροξυβουτυρυλοκαρνιτίνη (C4-OH) Bld.dot CHEM Pt Qn SRto Αίμα Δεκανοϋλοκαρνιτίνη (C10) Μηλονυλοκαρνιτίνη (C3-DC) Μηλονυλοκαρνιτίνη (C3-DC)+3-υδροξυβουτυρυλοκαρνιτίνη (C4-OH)
es-ESSpanish (Spain)Malonilcarnitina (C3-DC)+3-hidroxibutirilcarnitina (C4-OH)/Decanoilcarnitina (C10):Relacion de Sustancia:Punto temporal:gota de sangre (papel de filtro):Qn:
Synonyms: Cuantitativo
es-MXSpanish (Mexico)Malonilcarnitina (C3-DC) + 3-Hidroxibutirilcarnitina (C4-OH) / Decanoilcarnitina (C10):Proporción de sustancia:Punto temporal:DBS:Cuantitativo:
fr-CAFrench (Canada)Malonylcarnitine (C3-DC)+3-hydroxybutyrylcarnitine (C4-OH)/Décanoylcarnitine (C10):Ratio de substance:Temps ponctuel:Sang sur papier filtre:Quantitatif:
fr-FRFrench (France)Malonylcarnitine (C3-DC)+3-hydroxybutyrylcarnitine (C4-OH)/décanoylcarnitine (C10):Moles ratio:Ponctuel:Sang buvard:Numérique:
it-ITItalian (Italy)Malonilcarnitina (C3-DC)+3-Idrossibutirilcarnitina (C4-OH)/Decanoilcarnitina (C10):Srto:Pt:Sangue.su carta da filtro:Qn:
Synonyms: Chimica Punto nel tempo (episodio) Rapporto di sostanza Sangue Spot sangue secco
nl-NLDutch (Netherlands)malonylcarnitine (C3-DC) + 3-hydroxybutyrylcarnitine (C4-OH)/decanoylcarnitine (C10):molaire verhouding:moment:gedroogde bloedspot:kwantitatief:
ru-RURussian (Russian Federation)Малонилкарнитин (C3-DC)+3-Гидроксибутирилкарнитин (C4-OH)/Деканоилкарнитин (C10):МольОтн:ТчкВрм:Кр.Сух.капл:Колич:
Synonyms: Количественный Кровь Кровь сухая капля Мольная доля;Молярная доля;Отношение концентраций Точка во времени;Момент
tr-TRTurkish (Turkey)Malonilkarnitin (C3-DC)+3-Hidroksibütirilkarnitin (C4-OH)/Dekanoilkarnitin (C10):SOrn:Zmlı:Kan.nokta:Kant:
Synonyms: SubsOranı
zh-CNChinese (China)丙二酰肉碱 (C3-DC)+3-羟基异丁酰肉碱 (C4-OH)/癸酰肉碱 (C10):物质的量比率:时间点:全血.斑点:定量型:
Synonyms: 3-羟基丁酰肉碱(肉毒碱、三甲基羟基丁酰甜菜碱、卡尼丁) (C4-OH);3OH-丁酰肉碱;3-羟丁酰肉碱;3-羟-丁酰肉碱;3-羟基丁酰基肉碱;3-羟基-丁酰肉碱;3-羟基丁酰肉碱, C4-OH;C4OH;C4-OH Ⅲ III 三 丙二酰肉碱(肉毒碱、三甲基羟基丁酰甜菜碱、卡尼丁) (C3-DC);C3DC;C3-DC;C3-DCC;丙二酸单酰肉碱;丙二酰基肉碱;丙二酰基酰基肉碱;丙二酸单酰基肉碱;丙二酸单酰肉碱, C3-DC;酰基肉碱丙二酸单酰基;丙二酸单酰肉碱;丙二酰肉碱 丙二酰肉碱(肉毒碱、三甲基羟基丁酰甜菜碱、卡尼丁)(肉毒碱、三甲基羟基丁酰甜菜碱、卡尼丁) (C3-DC)+3-羟基异丁酰肉碱 (C4-OH);丙二酰基肉碱 (C3-DC)+3-羟基异丁酰基肉碱 (C4-OH) 全血斑点(滤纸);滤纸;血液.斑点;血液斑点(滤纸) 化学;化学检验项目;化学检验项目类;化学类;化学试验;非刺激耐受型化学检验项目;非刺激耐受型化学检验项目类;非刺激耐受型化学试验;非刺激耐受型化学试验类 叁 可用数量表示的;定量性;数值型;数量型;连续数值型标尺 时刻;随机;随意;瞬间 物质的量比值;物质的量比;摩尔比;摩尔比率;摩尔比值 癸酰肉碱(肉毒碱、三甲基羟基丁酰甜菜碱、卡尼丁) (C10);C10 癸酰肉碱(肉毒碱、三甲基羟基丁酰甜菜碱、卡尼丁) (C10);C10;癸酰基肉碱;癸酰肉碱, C10 血;血液

Example Units

UnitSource
{ratio}Example UCUM Units

LOINC Terminology Service (API) using HL7® FHIR® Get Info

CodeSystem lookup
https://fhir.loinc.org/CodeSystem/$lookup?system=http://loinc.org&code=75213-9