Term Description

One method for diagnosing acyl CoA dehydrogenase deficiencies is fatty acid oxidation analysis in cultured fibroblasts. Using multiple fatty acid substrates with varying carbon chain lengths, such as palmitate (16 carbons) LOINC 78358-9 and and myristate (14 carbons) (this term), can help differentiate between disorders such as long-chain acyl CoA dehydrogenase deficiency and medium-chain acyl CoA dehydrogenase deficiency. PMID: 2109149 Enzyme activity is measured as nanomoles of fatty acid oxidized per hour per milligram of cell protein (nmol FA/h/mg protein). PMID: 12840153

LOINC Names Get Info

Fully-Specified Name
Acyl CoA dehydrogenases:CCnt:Pt:Fibroblasts:Qn:[9,10-3H] myristate substrate
Long Common Name
Acyl CoA dehydrogenases [Enzymatic activity/mass] in Fibroblast by [9,10-3H] myristate substrate
Short Name
ACADs Fib Myristate-cCnt
Display Name
Acyl CoA dehydrogenases [9,10-3H] myristate substrate (Fibroblast) [Catalytic activity/Mass]
Consumer Name Alpha Get Info
Acyl coA dehydrogenases, Fibroblast

Part Model Get Info

  • Component
    Acyl CoA dehydrogenases
    LP200316-0
    • Analyte
      Acyl CoA dehydrogenases
      LP200316-0
      • Component Numerator
        Acyl CoA dehydrogenases
        LP200316-0
        • Component Numerator Core
          Acyl CoA dehydrogenases
          LP200316-0
        • Component Numerator Core Suffix
          NULL
           
      • Component Denominator
        NULL
         
        • Component Denominator Core
          NULL
           
        • Component Denominator Core Suffix
          NULL
           
    • Challenge
      NULL
       
    • Adjustment
      NULL
       
    • Count
      NULL
       
  • Property
    CCnt
    LP6790-2
  • Time
    Pt
    LP6960-1
  • System
    Fibroblasts
    LP7234-0
    • System Core
      Fibroblasts
      LP7234-0
    • Super System
      NULL
       
  • Scale
    Qn
    LP7753-9
  • Method
    [9,10-3H] myristate substrate
    LP199479-9

Basic Attributes

Class
CHEM
Type
Laboratory
First Released
Version 2.54
Last Updated
Version 2.54 (ADD)
Order vs. Observation
Both

Member of these Panels

LOINCLong Common Name
74533-1Fatty acid oxidation panel - Fibroblast

Member of these Groups Get Info

LOINC GroupGroup Name
LG30219-6Acyl CoA dehydrogenases|CCnt|Pt|Fibroblasts

Language Variants Get Info

TagLanguageTranslation
cs-CZCzech (Czechia)Acyl-CoA-dehydrogenázy:Katalytický obsah:Časový bod:Fibroblast:Kvantitativní:Substrát [9,10-3H] myristát
el-GRGreek (Greece)Ακυλο-CoA αφυδρογονάσες:CCnt:Pt:Ινοβλάστες:Qn:[9,10-3H] μυριστικό υπόστρωμα
Synonyms: [9,10-3H] μυριστικό υπόστρωμα CCnt CHEM Pt Qn Ακυλο-CoA αφυδρογονάσες Ινοβλάστες
es-ESSpanish (Spain)Acil Coenzima A deshidrogenasas:Contenido catalítico:Punto temporal:Fibroblastos:Qn:Sustrato [9,10-3H] miristato
Synonyms: Cuantitativo
es-MXSpanish (Mexico)Acil CoA deshidrogenasas:Contenido catalítico:Punto temporal:Fibroblasto:Cuantitativo:[9,10-3H] sustrato de miristato
fr-FRFrench (France)Acyl CoA déshydrogénases:Catalytique/Masse:Ponctuel:Fibroblastes:Numérique:Substrat [9,10-3H] myristate
it-ITItalian (Italy)Acil CoA deidrogenasi:CCnt:Pt:Fibroblasti:Qn:[9,10-3H] substrato miristato
Synonyms: Chimica Contenuto Catalitico Fibroblasto Punto nel tempo (episodio)
nl-NLDutch (Netherlands)acyl-CoA-dehydrogenase:enzymatische activiteit/massa:moment:fibroblast:kwantitatief:[9,10-3h] myristaatsubstraat
pl-PLPolish (Poland)Dehydrogenazy acylo-CoA:zawartość katalityczna:punkt w czasie:fibroblasty:ilościowy:substrat [9,10-3H] mirystycyny
zh-CNChinese (China)酰基 CoA 脱氢酶:催化含量:时间点:成纤维细胞:定量型:[9,10-3H] 肉豆蔻酸底物法
Synonyms: AcdA;酰基辅酶 A 脱氢酶 催化含量(单位质量);单位质量的酶单位数 化学;化学检验项目;化学检验项目类;化学类;化学试验;非刺激耐受型化学检验项目;非刺激耐受型化学检验项目类;非刺激耐受型化学试验;非刺激耐受型化学试验类 可用数量表示的;定量性;数值型;数量型;连续数值型标尺 时刻;随机;随意;瞬间 纤维原细胞;纤维母细胞

Example Units

UnitSource
nmol/h/mg{protein}Example UCUM Units

LOINC Terminology Service (API) using HL7® FHIR® Get Info

CodeSystem lookup
https://fhir.loinc.org/CodeSystem/$lookup?system=http://loinc.org&code=78360-5