Part Description

LP15383-0   Amylo-alpha-1,6-glucosidase
Amylo-alpha-1,6-glucosidase (AGL, EC 3.2.1.33) is one of the catalytic sites of the glycogen debrancher enzyme, which is encoded by the AGL gene [NCBI Gene ID: 178]. The other catalytic activity is and 4-alpha-glucanotransferase (EC 2.4.1.25). These enzymes are involved in glycogen degradation. Mutations in the AGL gene are associated with glycogen storage disease. Source: Regenstrief LOINC

LOINC Names Get Info

Fully-Specified Name
Amylo-alpha-1,6-glucosidase:CCnt:Pt:WBC:Qn:
Long Common Name
Amylo-alpha-1,6-glucosidase [Enzymatic activity/mass] in Leukocytes
Short Name
AGL WBC-cCnt
Display Name
Amylo-alpha-1,6-glucosidase (WBC) [Catalytic activity/Mass]
Consumer Name Alpha Get Info
Amylo-alpha-1,6-glucosidase, White blood cells

Part Model Get Info

  • Component
    Amylo-alpha-1,6-glucosidase
    LP15383-0
    • Analyte
      Amylo-alpha-1,6-glucosidase
      LP15383-0
      • Component Numerator
        Amylo-alpha-1,6-glucosidase
        LP15383-0
        • Component Numerator Core
          Amylo-alpha-1,6-glucosidase
          LP15383-0
        • Component Numerator Core Suffix
          NULL
           
      • Component Denominator
        NULL
         
        • Component Denominator Core
          NULL
           
        • Component Denominator Core Suffix
          NULL
           
    • Challenge
      NULL
       
    • Adjustment
      NULL
       
    • Count
      NULL
       
  • Property
    CCnt
    LP6790-2
  • Time
    Pt
    LP6960-1
  • System
    WBC
    LP7720-8
    • System Core
      WBC
      LP7720-8
    • Super System
      NULL
       
  • Scale
    Qn
    LP7753-9
  • Method
    NULL
     

Basic Attributes

Class
CHEM
Type
Laboratory
First Released
Version 2.58
Last Updated
Version 2.58 (ADD)
Order vs. Observation
Both

Language Variants Get Info

TagLanguageTranslation
cs-CZCzech (Czechia)Amylo-alfa-1,6-glukosidáza:Katalytický obsah:Časový bod:Leukocyty:Kvantitativní:
el-GRGreek (Greece)Αμυλο-α-1,6-γλυκοσιδάση:CCnt:Pt:Αριθμός λευκών αιμοσφαιρίων:Qn:
Synonyms: CCnt CHEM Pt Qn Αμυλο-α-1,6-γλυκοσιδάση Αριθμός λευκών αιμοσφαιρίων Γλυκοσιδάση
es-ESSpanish (Spain)Amilo-alfa-1,6 glucosidasa:Contenido catalítico:Punto temporal:Células sanguineas blancas:Qn:
Synonyms: Cuantitativo
es-MXSpanish (Mexico)Amilo-alfa-1,6-glucosidasa:Contenido catalítico:Punto temporal:células blancas de la sangre:Cuantitativo:
fr-CAFrench (Canada)Amylo-alpha-1,6-glucosidase:Contenu catalytique:Temps ponctuel:Leucocytes:Quantitatif:
fr-FRFrench (France)Amylo-alpha-1,6-glucosidase:Catalytique/Masse:Ponctuel:Leucocytes:Numérique:
fr-BEFrench (Belgium)Amylo-1,6-glucosidase:Contenu catalytique:Temps ponctuel:Leucocytes:Quantitatif:
it-ITItalian (Italy)Amilo-alfa-1,6-Glucosidasi:CCnt:Pt:WBC:Qn:
Synonyms: Chimica Contenuto Catalitico Globuli bianchi Punto nel tempo (episodio)
nl-NLDutch (Netherlands)amylo-1,6-glucosidase:enzymatische activiteit/massa:moment:leukocyten:kwantitatief:
Synonyms: witte bloedcellen
pl-PLPolish (Poland)Amylo-alfa-1,6-glukozydaza:zawartość katalityczna:punkt w czasie:leukocyty:ilościowy:
Synonyms: Amylo-alfa-1,6-glukozydaza Glukozydaza
ru-RURussian (Russian Federation)Амило-1,6-Глюкозидаза:КаталСод:ТчкВрм:Лейкоциты:Колич:
Synonyms: Каталитическое содержание Количественный Точка во времени;Момент
tr-TRTurkish (Turkey)Amilo-1,6-Glukozidaz:Ktlİçrk:Zmlı:Lökosit:Kant:
Synonyms: WBC
zh-CNChinese (China)淀粉-alpha-1,6-葡糖苷酶:催化含量:时间点:白细胞:定量型:
Synonyms: Ⅰ A1 型 I WBC;WBCs;白血球;白血细胞 α α1 催化含量(单位质量);单位质量的酶单位数 化学;化学检验项目;化学检验项目类;化学类;化学试验;非刺激耐受型化学检验项目;非刺激耐受型化学检验项目类;非刺激耐受型化学试验;非刺激耐受型化学试验类 可用数量表示的;定量性;数值型;数量型;连续数值型标尺 时刻;随机;随意;瞬间 淀粉-α-1,6-葡糖苷酶;AGL;Amylo-1,6-葡糖苷酶;Amylo-1,6-葡萄糖苷酶;Cori 氏病;Cori 病;淀粉-1,6-葡萄糖苷酶;淀粉-1,6-葡糖苷酶;糖原病 III 型;糖原贮积病 III;糖原贮积病 III 型 葡糖基蔗糖酶;葡萄糖苷酶;葡萄糖转化酶;麦牙糖酶;麦芽糖酶;麦芽糖酶-葡糖淀粉酶;麦芽糖酶-葡糖糖化酶 阿尔法

Example Units

UnitSource
nmol/min/mg{protein}Example UCUM Units

LOINC Terminology Service (API) using HL7® FHIR® Get Info

CodeSystem lookup
https://fhir.loinc.org/CodeSystem/$lookup?system=http://loinc.org&code=82222-1