90235-3
Heparan sulfate [Moles/volume] in DBS
Active
Part Description
LP15629-6 Heparan sulfate
Heparan sulfate is a derived disaccharide that accumulates in lysosomes, extracellular matrix, and body fluids of people with mucopolysaccharidoses (MPSs). MPSs are rare disorders caused by a deficiency of enzymes that break down glycosaminoglycans (GAGs). Symptoms of MPS vary due to which storage product accumulates and the level of enzymatic function or concentration that remains. Symptoms include musculoskeletal, airway, cardiac, and central nervous system disorders. Treatments include hematopoietic stem cell transplantation for the more critical forms of MPS and intravenous enzyme replacement therapy for the others. Treatment is most effective when it is initiated before irreversible tissue damage has occurred. Because MPS is so rare and the symptoms so variable, it is difficult to diagnose in its earliest stages. A solution to that problem is the development of newborn screening assays that can detect heparan sulfate, though the levels in the dried blood spot samples do not appear to predict the severity of disease. The pattern of dermatan and heparan sulfate can help distinguish between the different MPSs. PMID: 23084433
Source: Regenstrief LOINC
Fully-Specified Name
- Component
- Heparan sulfate
- Property
- SCnc
- Time
- Pt
- System
- Bld.dot
- Scale
- Qn
- Method
Additional Names
- Short Name
- Heparan sulfate DBS-sCnc
- Display Name
- Heparan sulfate (DBS) [Moles/Vol]
- Consumer Name Alpha Get Info
- Heparan sulfate, Dried blood spot
Basic Attributes
- Class
- CHEM
- Type
- Laboratory
- First Released
- Version 2.65
- Last Updated
- Version 2.65
- Order vs. Observation
- Both
Member of these Panels
LOINC | Long Common Name |
---|---|
94586-5 | Dermatan sulfate and heparan sulfate and keratan sulfate panel - DBS |
Language Variants Get Info
Tag | Language | Translation |
---|---|---|
es-ES | Spanish (Spain) | Heparán sulfato: Synonyms: Cuantitativo |
es-MX | Spanish (Mexico) | Sulfato de Heparán: |
et-EE | Estonian (Estonia) | Heparaansulfaat: Synonyms: Aine kontsentratsioon Juhuslik Kvantitatiivne Veri |
fr-FR | French (France) | Héparane sulfate: |
fr-CA | French (Canada) | Héparane-sulfate: |
fr-BE | French (Belgium) | Héparane-sulfate: Synonyms: SO4 |
it-IT | Italian (Italy) | Eparan solfato: Synonyms: Chimica Concentrazione di Sostanza Punto nel tempo (episodio) Sangue Spot sangue secco |
nl-NL | Dutch (Netherlands) | heparansulfaat: |
ru-RU | Russian (Russian Federation) | Гепаран сульфат: Synonyms: Гепарансульфат Количественный Кровь Кровь сухая капля Молярность; |
tr-TR | Turkish (Turkey) | Heparan sülfat: |
zh-CN | Chinese (China) | 硫酸类肝素: Synonyms: SO4; |
Example Units
Unit | Source |
---|---|
nmol/L | Example UCUM Units |
LOINC Terminology Service (API) using HL7® FHIR® Get Info
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- CodeSystem lookup
- https:
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