Part Description

LP310462-9   Alpha-aminoadipic semialdehyde+Delta-1-piperideine-6-carboxylate
Alpha-aminoadipic semialdehyde (α-AASA) is a derivative of lysine used in the production of elastin and collagen. Accumulation of α-AASA (in CSF, plasma and urine) and pipecolic acid (CSF and plasma) due to a deficiency of α-AASA dehydrogenase (antiquin) occurs in patients with pyridoxine-dependent epilepsy (PDE), a rare, autosomal recessive disorder. PMID: 17560822 α-AASA exists in a reversible equilibrium with its Schiff base, delta-1-piperideine-6-carboxylate (P6C), which is also measured, sometimes in summation with α-AASA. PMID: 19631689 Source: Regenstrief LOINC

LOINC Names Get Info

Fully-Specified Name
Alpha-aminoadipic semialdehyde+Delta-1-Piperideine-6-carboxylate:SCnc:Pt:Ser/Plas:Qn:
Long Common Name
Alpha-aminoadipic semialdehyde+Delta-1-piperideine-6-carboxylate [Moles/volume] in Serum or Plasma
Short Name
AASA+P6C SerPl-sCnc
Display Name
Alpha-aminoadipic semialdehyde+Delta-1-Piperideine-6-carboxylate [Moles/Vol]
Consumer Name Alpha Get Info
Alpha-aminoadipic semialdehyde+Delta-1-piperideine-6-carboxylate, Blood

Part Model Get Info

  • Component
    Alpha-aminoadipic semialdehyde+Delta-1-piperideine-6-carboxylate
    LP310462-9
    • Analyte
      Alpha-aminoadipic semialdehyde+Delta-1-piperideine-6-carboxylate
      LP310462-9
      • Component Numerator
        Alpha-aminoadipic semialdehyde+Delta-1-piperideine-6-carboxylate
        LP310462-9
        • Component Numerator Core
          Alpha-aminoadipic semialdehyde+Delta-1-piperideine-6-carboxylate
          LP310462-9
        • Component Numerator Core Suffix
          NULL
           
      • Component Denominator
        NULL
         
        • Component Denominator Core
          NULL
           
        • Component Denominator Core Suffix
          NULL
           
    • Challenge
      NULL
       
    • Adjustment
      NULL
       
    • Count
      NULL
       
  • Property
    SCnc
    LP6860-3
  • Time
    Pt
    LP6960-1
  • System
    Ser/Plas
    LP7576-4
    • System Core
      Ser/Plas
      LP7576-4
    • Super System
      NULL
       
  • Scale
    Qn
    LP7753-9
  • Method
    NULL
     

Basic Attributes

Class
CHEM
Type
Laboratory
First Released
Version 2.66
Last Updated
Version 2.66 (ADD)
Order vs. Observation
Observation

Language Variants Get Info

TagLanguageTranslation
cs-CZCzech (Czechia)Alfa-aminoadipát-semialdehyd+delta-1-piperidein-6-karboxylát:Látková koncentrace:Časový bod:Sérum/plazma:Kvantitativní:
el-GRGreek (Greece)α-αμινο-διπική ημιαλδεΰδη+δ-1-πιπεριδινο-6-καρβοξυλικό:SCnc:Pt:Ορός/Πλάσμα:Qn:
Synonyms: CHEM Pt Qn SCnc Α-αμινοδιπική ημιαλδεΰδη α-αμινο-διπική ημιαλδεΰδη+δ-1-πιπεριδινο-6-καρβοξυλικό Ορός Ορός/Πλάσμα Πλάσμα
es-ESSpanish (Spain)Alfa-aminoadípico semialdehido+Delta-1-piperidina-6-carboxilato:Concentración de sustancia:Punto temporal:Suero o Plasma:Qn:
Synonyms: Cuantitativo
es-MXSpanish (Mexico)Semialdehído alfa-aminoadípico + Delta-1-piperideína-6-carboxilato:Concentración de sustancias:Punto temporal:Suero o Plasma:Cuantitativo:
fr-FRFrench (France)2-aminoadipique semialdéhyde+delta-1-pipéridéine-6-carboxylate:Moles/Volume:Ponctuel:Sérum/Plasma:Numérique:
it-ITItalian (Italy)Semialdeide alfa-aminoadipica+Delta-1-piperideine-6-carbossilato:SCnc:Pt:Siero/Plasma:Qn:
Synonyms: Chimica Concentrazione di Sostanza Plasma Punto nel tempo (episodio) Siero Siero o Plasma
pl-PLPolish (Poland)Semialdehyd alfa-aminoadypinowy+delta-1-piperydyno-6-karboksylan:stężenie molowe:punkt w czasie:surowica lub osocze:ilościowy:
Synonyms: Alfa-AASA Semialdehyd alfa-aminoadypinowy i delta-1-piperydyno-6-karboksylan
zh-CNChinese (China)Alpha-氨基己二酸半醛+Delta-1-哌啶-6-羧酸酯:物质的量浓度:时间点:血清/血浆:定量型:
Synonyms: Ⅰ Alpha-氨基己二酸半醛(α-氨基己二酸半醛)+Delta-1-哌啶-6-羧酸酯(δ-1-哌啶-6-羧酸酯);α-氨基己二酸半醛+δ-1-哌啶-6-羧酸酯;α-氨基己二酸半醛+δ1-哌啶-6-羧酸酯 I α α-氨基己二酸半醛 克分子浓度;克分子浓度(单位体积);摩尔浓度;摩尔浓度(单位体积);物质的量浓度(单位体积) 化学;化学检验项目;化学检验项目类;化学类;化学试验;非刺激耐受型化学检验项目;非刺激耐受型化学检验项目类;非刺激耐受型化学试验;非刺激耐受型化学试验类 可用数量表示的;定量性;数值型;数量型;连续数值型标尺 时刻;随机;随意;瞬间 血清或血浆 阿尔法

Example Units

UnitSource
umol/LExample UCUM Units

LOINC Terminology Service (API) using HL7® FHIR® Get Info

CodeSystem lookup
https://fhir.loinc.org/CodeSystem/$lookup?system=http://loinc.org&code=92766-5