Status Information

Status
DISCOURAGED
Comment
This analyte is usually reported as substance, not mass
Map-ToLong Common NameMapping Guidance
25348-4Beta aminoisobutyrate [Moles/time] in 24 hour Urine

Part Descriptions

LP15432-5   Beta aminoisobutyrate
3-Aminoisobutyric acid is a product formed by the catabolism of thymine. Copyright Text is available under the Creative Commons Attribution/Share-Alike License. See http://creativecommons.org/licenses/by-sa/3.0/ for details. Source: Wikipedia, Wikipedia

LP15432-5   Beta aminoisobutyrate
Beta aminoisobutyric acid (BAIB) is a nonprotein amino acid that is an end product of pyrimidine metabolism. The R and S enantiomers (previously named D-(minus)-BAIB and L-plus-BAIB) are produced from thymine and L-valine, respectively. Under normal circumstances, urine contains predominantly R-BAIB (from thymine) because it is eliminated by filtration and tubular secretion, while plasma contains about 80% S-BAIB (from valine), which is reabsorbed in the kidneys. In patients with dihydropyrimidine dehydrogenase deficiency, thymine catabolism is decreased, which results in moderately decreased CSF concentration and markedly decreased plasma concentration of BAIB. On the other hand, urine BAIB is elevated despite decreased breakdown of thymine, which indicates that there must be cross-over in the thymine and valine degradation pathways. PMID: 14705962 Deficiency of D-beta-aminoisobutyrate:pyruvate aminotransferase (EC 2.6.1.40) , an enzyme that is involved in the catabolism R-BAIB, also results in elevated urine BAIB and is associated with hyperuricemia. [OMIM: 210100] Source: Regenstrief LOINC, PMID: 14705962

LOINC Names Get Info

Fully-Specified Name
Beta aminoisobutyrate:MRat:24H:Urine:Qn:
Long Common Name
Beta aminoisobutyrate [Mass/time] in 24 hour Urine
Short Name
B-AIB 24h Ur-mRate
Display Name
Beta aminoisobutyrate (24H U) [Mass/Time]
Consumer Name Alpha Get Info
Beta aminoisobutyrate, Urine

Part Model Get Info

  • Component
    Beta aminoisobutyrate
    LP15432-5
    • Analyte
      Beta aminoisobutyrate
      LP15432-5
      • Component Numerator
        Beta aminoisobutyrate
        LP15432-5
        • Component Numerator Core
          Beta aminoisobutyrate
          LP15432-5
        • Component Numerator Core Suffix
          NULL
           
      • Component Denominator
        NULL
         
        • Component Denominator Core
          NULL
           
        • Component Denominator Core Suffix
          NULL
           
    • Challenge
      NULL
       
    • Adjustment
      NULL
       
    • Count
      NULL
       
  • Property
    MRat
    LP6833-0
  • Time
    24H
    LP6924-7
  • System
    Urine
    LP7681-2
    • System Core
      Urine
      LP7681-2
    • Super System
      NULL
       
  • Scale
    Qn
    LP7753-9
  • Method
    NULL
     

Basic Attributes

Class
CHEM
Type
Laboratory
First Released
Version 1.0i
Last Updated
Version 2.44 (MIN)
Order vs. Observation
Observation

Language Variants Get Info

TagLanguageTranslation
cs-CZCzech (Czechia)Beta-aminoizobutyrát:Hmotnostní tok:24 hodin:Moč:Kvantitativní:
el-GRGreek (Greece)β-αμινοϊσοβουτυρικό:MRat:24H:Ούρα:Qn:
Synonyms: 24H CHEM MRat Qn β-αμινοϊσοβουτυρικό Ούρα
es-ARSpanish (Argentina)beta aminoisobutirato:índice de masa:24 horas:orina:cuantitativo:
es-ESSpanish (Spain)Beta aminoisobutirato:Indice de masa:24 horas:Orina:Qn:
Synonyms: Cuantitativo
es-MXSpanish (Mexico)Beta aminoisobutirato:Tasa de masa:24H:Orina:Cuantitativo:
et-EEEstonian (Estonia)Beetaaminoisobutüraat:MRat:24 tunni:U:Qn:
Synonyms: Kvantitatiivne Uriin
fr-CAFrench (Canada)Bêta-aminoisobutyrate:Débit de masse:24 h:Urine:Quantitatif:
fr-FRFrench (France)Bêta aminoisobutyrate:Masse/Temps:24H:Urine:Numérique:
fr-BEFrench (Belgium)Béta-aminoisobutyrate:Débit de masse:24 h:Urine:Quantitatif:
it-ITItalian (Italy)Beta aminoisobutirrato:MRat:24h:Urine:Qn:
Synonyms: 24 Ore Chimica Indice di Massa
ko-KRKorean (Korea, Republic Of)베타 아미노이소뷰티레이트:질량율:24시간:뇨:정량:
nl-NLDutch (Netherlands)bèta-amino-isobutyraat:massa/tijd:24 uur:urine:kwantitatief:
Synonyms: 24U
pl-PLPolish (Poland)Beta aminoizomaślan:wskaźnik masowy w jednostce czasu:24h:mocz:ilościowy:
Synonyms: 24 godziny
pt-BRPortuguese (Brazil)Beta aminoisobutirato:MRat:24H:Urina:Qn:
Synonyms: ; B-AIB; 3-aminoisobutyrate; 3-aminoisobutyric acid; mRate; Mass rate; 1 day; 24 hours; 24HR; Ur; UR; Urn; UA; Quantitative; QNT; Quant; Quan; B; Chemistry
ru-RURussian (Russian Federation)Бета аминоизобутират:МассСк:24 часа:Моча:Колич:
Synonyms: Бета-аминоизобутират Количественный Массовая скорость
tr-TRTurkish (Turkey)Beta aminoizobütirat:KütlHz:24Sa:İdrar:Kant:
zh-CNChinese (China)Beta 氨基异丁酸:质量速率:24小时:尿液:定量型:
Synonyms: 1天;1日;24.0小时;一天;一日;二十四个小时;二十四小时 3-氨基异丁酸;B-AIB;Beta-氨基异丁酸;β氨基异丁酸;β-氨基异丁酸 B β 化学;化学检验项目;化学检验项目类;化学类;化学试验;非刺激耐受型化学检验项目;非刺激耐受型化学检验项目类;非刺激耐受型化学试验;非刺激耐受型化学试验类 单位时间内的质量数;质量速率(单位时间) 可用数量表示的;定量性;数值型;数量型;连续数值型标尺 尿;小便;下泉 贝塔

LOINC Terminology Service (API) using HL7® FHIR® Get Info

CodeSystem lookup
https://fhir.loinc.org/CodeSystem/$lookup?system=http://loinc.org&code=9320-3