LP14338-5
Hexacarboxylporphyrin III
Active
Descriptions
Part of porphyrin fractionation testing useful in diagnosing porphyrin cutanea tarda, hereditary coproporphyria, and variegate porphyria. Such patients typically will present with profound elevations of porphyrin analytes (e.g. > 5-fold) during acute episodes. Moderate elevations (e.g. < 3-fold) are more often due to medications or environmental factors. Source: Regenstrief LOINC
Hexacarboxylporphyrin III is a bile product that arises from the conversion of Hexacarboxylporphyrinogen III to Hexacarboxylporphyrin III by porphyrinogen carboxy-lyase (EC 4.1.1.37). Copyright Copyright ©2005-2009 Genome Alberta (Reference to original publication: Wishart DS, Knox C, Guo AC, et al. HMDB: a knowledgebase for the human metabolome. Nucleic Acids Res. 2009 37(Database issue):D603-610.) Source: Human Metabolome Database, Hexacarboxylporphyrin III
Porphyrins are created as byproducts of porphyrinogens. Hereditary enzyme disorders leading to the buildup of porphyrins or porphyrinogens cause porphyrias and affect the heme biosynthetic pathway. Most of these disorders are inherited as autosomal dominant disorders. Increased urine porphyrins are seen with congenital erythropoietic porphyria, acute intermittent porphyria, hereditary coproporphyria, variegate porphyria, and porphyria cutanea tarda. Information from LOINC partner 1 and Jacobs and DeMott Laboratory Test Handbook, 5th edition, DS Jacobs, WR DeMott and DK Oxley, 2001. Source: Regenstrief Institute
Basic Part Properties
- Part Display Name
- Hexacarboxylporphyrin III
- Part Type
- Component (Describes the core component or analyte measured)
- Created On
- 2000-05-04
- Construct for LOINC Short Name
- Hexa-CPr3
LOINC Terminology Service (API) using HL7® FHIR® Get Info
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- CodeSystem lookup
- https:
//fhir.loinc.org/CodeSystem/$lookup?system=http: //loinc.org&code=LP14338-5
Language Variants Get Info
| Tag | Language | Translation |
|---|---|---|
| zh-CN | Chinese (China) | 六羧基卟啉 III Synonyms: Hexa-CPr3; |
| et-EE | Estonian (Estonia) | Heksakarboksüülporfüriin III |
| es-ES | Spanish (Spain) | Hexacarboxilporfirina III |
| it-IT | Italian (Italy) | Esacarbossilporfirina III |
| tr-TR | Turkish (Turkey) | Hekzakarboksilporfirin III |
| ru-RU | Russian (Russian Federation) | Гексакарбоксилпорфирин III |
| nl-NL | Dutch (Netherlands) | hexacarboxylporfyrine III |
LOINC Copyright
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