LP14512-5
3-Methylcrotonylglycine
Active
Description
3-Methylcrotonylglycine is an acyl glycine. Acyl glycines are normally minor metabolites of fatty acids. However, the excretion of certain acyl glycines is increased in several inborn errors of metabolism. In certain cases the measurement of these metabolites in body fluids can be used to diagnose disorders associated with mitochondrial fatty acid beta-oxidation. Acyl glycines are produced through the action of glycine N-acyltransferase (EC 2.3.1.13) which is an enzyme that catalyzes the chemical reaction: acyl-CoA + glycine < -- > CoA + N-acylglycine. 3-Methylcrotonylglycine is a normal amino acid metabolite found in urine. Increased levels of this metabolite are found in patients suffering from leucine catabolic disorders, such as 3-methylcrotonyl-CoA carboxylase deficiency. 3-Methylcrotonylglycine is often considered to be a diagnostic marker of organic acidemias. PMID: 11170888 Copyright Copyright ©2005-2009 Genome Alberta (Reference to original publication: Wishart DS, Knox C, Guo AC, et al. HMDB: a knowledgebase for the human metabolome. Nucleic Acids Res. 2009 37(Database issue):D603-610.) Source: Human Metabolome Database, Human Metabolome Database
Basic Part Properties
- Part Display Name
- 3-Methylcrotonylglycine
- Part Type
- Component (Describes the core component or analyte measured)
- Created On
- 2000-05-04
- Construct for LOINC Short Name
- 3Me-crotonylglycine
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Language Variants Get Info
| Tag | Language | Translation |
|---|---|---|
| zh-CN | Chinese (China) | 3-甲基丁烯酰甘氨酸 Synonyms: 3Me-丁烯酰甘氨酸; |
| fr-CA | French (Canada) | 3-méthylcrotonylglycine |
| es-ES | Spanish (Spain) | 3-metilcrotonilglicina |
| it-IT | Italian (Italy) | 3-Metilcrotonilglicina |
| tr-TR | Turkish (Turkey) | 3-Metilkrotonilglisin |
| ru-RU | Russian (Russian Federation) | 3-Метилкротонилглицин |
| nl-NL | Dutch (Netherlands) | 3-methylcrotonylglycine |
| fr-BE | French (Belgium) | 3-méthylcrotonylglycine |
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