Description

Succinate semialdehyde dehydrogenase (SSADH) [UniProt: P51649] is a mitochondrial protein involved in the degradation of gamma-aminobutyric acid (GABA), an inhibitory neurotransmitter. Decreased levels of SSADH causes succinate semialdehyde dehydrogenase deficiency (SSADHD), a condition characterized by developmental delay, hypotonia, mental retardation, ataxia, seizures, hyperkinetic behavior, aggression, and sleep disturbances.[OMIM: 271980] Prenatal diagnosis of SSADH deficiency may be performed by enzyme analysis in amniotic fluid and cells. PMID: 8464836 Source: Regenstrief LOINC

Basic Part Properties

Part Name
Succinate semialdehyde dehydrogenase
Part Display Name
Succinate semialdehyde dehydrogenase
Part Type
Component (Describes the core component or analyte measured)
Created On
2015-10-28
Construct for LOINC Short Name
SSADH

LOINC Terminology Service (API) using HL7® FHIR® Get Info

CodeSystem lookup
https://fhir.loinc.org/CodeSystem/$lookup?system=http://loinc.org&code=LP201790-5

Language Variants Get Info

TagLanguageTranslation
zh-CNChinese (China)琥珀酸半醛脱氢酶
Synonyms: SSADH
fr-CAFrench (Canada)Semialdéhyde succinate déshydrogénase
es-ESSpanish (Spain)Succinato-semialdehído deshidrogenasa
it-ITItalian (Italy)Deidrogenasi succinato semialdeide
tr-TRTurkish (Turkey)Süksinat semialdehid dehidrojenaz
nl-NLDutch (Netherlands)succinaat-semialdehyde-dehydrogenase
fr-FRFrench (France)Succinate semialdéhyde déshydrogénase
pl-PLPolish (Poland)Dehydrogenaza semialdehydu bursztynowego
Synonyms: SSADH
el-GRGreek (Greece)Ηλεκτρική ημιαλδεϋδική αφυδρογονάση
Synonyms: Ηλεκτρική ημιαλδεϋδική αφυδρογονάση