Version 2.77

Description

The branched chain keto-acid dehydrogenase complex (BCKAD) is a multienzyme which catalyzes the oxidative decarboxylation of the alpha-keto acids derived from leucine, isoleucine, and valine. Source: Regenstrief Institute

Basic Part Properties

Part Display Name
Branched chain keto-acid dehydrogenase complex
Part Type
Component (Describes the core component or analyte measured)
Created On
2002-12-06
Construct for LOINC Short Name
BCKAD

LOINC Terminology Service (API) using HL7® FHIR® Get Info

CodeSystem lookup
https://fhir.loinc.org/CodeSystem/$lookup?system=http://loinc.org&code=LP30840-0

Language Variants Get Info

Tag Language Translation
zh-CN Chinese (China) 支链酮酸脱氢酶复合体
Synonyms: BCKAD;BCKADH;BCKDC;BCKDH;MSUD;分支链酮酸脱氢酶复合体;分支链酮酸脱氢酶复合物;支链酮酸尿病;支链酮酸尿症;支链酮酸脱氢酶复合体(Branched chain keto-acid dehydrogenase complex,BCKAD);支链酮酸脱氢酶复合物;枫糖尿病;枫糖浆尿病;槭糖尿病;槭糖浆尿病;歧链酮酸脱氢酶复合体;歧链酮酸脱氢酶复合物
fr-CA French (Canada) Complexe déshydrogénase acide cétonique branche ramifiée
es-ES Spanish (Spain) Complejo de la deshidrogenasa de los cetoácidos de cadena ramificada
it-IT Italian (Italy) Complesso chetoacido deidrogenasi a catena ramificata
tr-TR Turkish (Turkey) Dallı zincirli ketoasit dehidrogenaz kompleksi
ru-RU Russian (Russian Federation) Разветвленных цепей кето-кислот дегидрогеназы комплекс
nl-NL Dutch (Netherlands) vertakte-keten ketozuurdehydrogenasecomplex
fr-BE French (Belgium) Complexe déshydrogénase acide cétonique branche ramifiée