Description

The KCNQ1 gene (potassium channel, voltage gated KQT-like subfamily Q, member 1) [HGNC Gene ID:6294] is located on chromosome 11p15.5. This gene encodes a voltage-gated potassium channel required for repolarization phase of the cardiac action potential. This protein can form heteromultimers with two other potassium channel proteins, KCNE1 and KCNE3. Mutations in this gene are associated with hereditary long QT syndrome 1 (also known as Romano-Ward syndrome), Jervell and Lange-Nielsen syndrome, and familial atrial fibrillation. This gene exhibits tissue-specific imprinting, with preferential expression from the maternal allele in some tissues, and biallelic expression in others. This gene is located in a region of chromosome 11 amongst other imprinted genes that are associated with Beckwith-Wiedemann syndrome (BWS), and itself has been shown to be disrupted by chromosomal rearrangements in patients with BWS. Alternatively spliced transcript variants have been found for this gene. [provided by RefSeq, Aug 2011] [NCBI Gene ID:3784] Source: National Center for Biotechnology Information (NCBI) Gene

Reference Information

TypeSourceReference
WebcontentOnline Mendelian Inheritance in Man®Copyright OMIM® and Online Mendelian Inheritance in Man® are registered trademarks of the Johns Hopkins University. Link to OMIM

Basic Part Properties

Part Name
KCNQ1 gene
Part Display Name
KCNQ1 gene
Part Type
Component (Describes the core component or analyte measured)
Created On
2006-02-16
Construct for LOINC Short Name
KCNQ1 gene

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Language Variants Get Info

TagLanguageTranslation
zh-CNChinese (China)KCNQ1 基因
Synonyms: ATFB1;KCNA8;KCNA9;KCNQ10T1;Kv1.9;Kv7.1;KVLQT1;LQT;LQTS;Romano-Ward 长 QT 综合征;RWS;WRS;电压门控型钾离子通道, KQT 样亚家族, 成员 1;电压门控型钾通道, KQT 样亚家族, 成员 1;电压门控式钾离子通道, KQT 样亚家族, 成员 1;电压门控式钾通道, KQT 样亚家族, 成员 1;电压门控钾离子通道, KQT 样亚家族, 成员 1;电压门控钾通道, KQT 样亚家族, 成员 1;钾电压门控型通道, KQT 样亚家
et-EEEstonian (Estonia)KCNQ1 geen
es-ESSpanish (Spain)Gen KCNQ1
it-ITItalian (Italy)KCNQ1, gene
Synonyms: Gene KCNQ1
tr-TRTurkish (Turkey)KCNQ1 geni
ru-RURussian (Russian Federation)KCNQ1 ген
nl-NLDutch (Netherlands)KCNQ1-gen
Synonyms: KCNQ1 gen
fr-FRFrench (France)KCNQ1 gène
pl-PLPolish (Poland)KCNQ1 gen
Synonyms: Gen KCNQ1
el-GRGreek (Greece)Γονίδιο KCNQ1
Synonyms: Γονίδιο KCNQ1