Description

The BTD gene (biotinidase) [HGNC Gene ID:1122] is located on chromosome 3p25. The protein encoded by this gene functions to recycle protein-bound biotin by cleaving biocytin (biotin-epsilon-lysine), a normal product of carboxylase degradation, resulting in regeneration of free biotin. The encoded protein has also been shown to have biotinyl transferase activity. Mutations in this gene are associated with biotinidase deficiency. Multiple transcript variants encoding different isoforms have been described. [provided by RefSeq, Aug 2013] [NCBI Gene ID:686] Source: National Center for Biotechnology Information (NCBI) Gene

Reference Information

TypeSourceReference
WebcontentOnline Mendelian Inheritance in Man®Copyright OMIM® and Online Mendelian Inheritance in Man® are registered trademarks of the Johns Hopkins University. Link to OMIM

Basic Part Properties

Part Name
BTD gene
Part Display Name
BTD gene
Part Type
Component (Describes the core component or analyte measured)
Created On
2008-10-01
Construct for LOINC Short Name
BTD gene

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Language Variants Get Info

TagLanguageTranslation
zh-CNChinese (China)BTD 基因
Synonyms: biotinidase gene;生物素酶基因;生物素化物酶
et-EEEstonian (Estonia)BTD geen
es-ESSpanish (Spain)Gen BTD
it-ITItalian (Italy)BTD, gene
Synonyms: Gene BTD
tr-TRTurkish (Turkey)BTD geni
ru-RURussian (Russian Federation)BTD ген
nl-NLDutch (Netherlands)BTD-gen
Synonyms: BTD gen
fr-FRFrench (France)BTD gène
el-GRGreek (Greece)Γονίδιο BTD
Synonyms: Γονίδιο BTD
pl-PLPolish (Poland)BTD gen
Synonyms: Gen BTD;Gen biotynidazy