Term Description

BCKAD is a multienzyme complex which catalyzes the oxidative decarboxylation of the a-keto acids derived from leucine, isoleucine and valine.

Part Description

LP30840-0   Branched chain keto-acid dehydrogenase complex
The branched chain keto-acid dehydrogenase complex (BCKAD) is a multienzyme which catalyzes the oxidative decarboxylation of the alpha-keto acids derived from leucine, isoleucine, and valine. Source: Regenstrief Institute

LOINC Names Get Info

Fully-Specified Name
Branched chain keto-acid dehydrogenase complex:Prid:Pt:Bld:Nom:
Long Common Name
Branched chain keto-acid dehydrogenase complex [Identifier] in Blood
Short Name
BCKAD Bld
Display Name
Branched chain keto-acid dehydrogenase complex Nom (Bld)
Consumer Name Alpha Get Info
Branched chain keto-acid dehydrogenase complex, Blood

Part Model Get Info

  • Component
    Branched chain keto-acid dehydrogenase complex
    LP30840-0
    • Analyte
      Branched chain keto-acid dehydrogenase complex
      LP30840-0
      • Component Numerator
        Branched chain keto-acid dehydrogenase complex
        LP30840-0
        • Component Numerator Core
          Branched chain keto-acid dehydrogenase complex
          LP30840-0
        • Component Numerator Core Suffix
          NULL
           
      • Component Denominator
        NULL
         
        • Component Denominator Core
          NULL
           
        • Component Denominator Core Suffix
          NULL
           
    • Challenge
      NULL
       
    • Adjustment
      NULL
       
    • Count
      NULL
       
  • Property
    Prid
    LP6850-4
  • Time
    Pt
    LP6960-1
  • System
    Bld
    LP7057-5
    • System Core
      Bld
      LP7057-5
    • Super System
      NULL
       
  • Scale
    Nom
    LP7750-5
  • Method
    NULL
     

Basic Attributes

Class
CHEM
Type
Laboratory
First Released
Version 2.09
Last Updated
Version 2.73 (MIN)
Order vs. Observation
Both
Common Test Rank Get Info
6455

Language Variants Get Info

TagLanguageTranslation
cs-CZCzech (Czechia)Dehydrogenáza ketokyselin s rozvětveným řetězcem komplex:Přítomnost nebo identita:Časový bod:Krev:Nominální:
el-GRGreek (Greece)Σύμπλεγμα αφυδρογονάσης κετοξέων διακλαδισμένης αλυσίδας:Prid:Pt:Αίμα:Nom:
Synonyms: CHEM Nom Prid Pt Αίμα Σύμπλεγμα αφυδρογονάσης κετοξέων διακλαδισμένης αλυσίδας
es-ARSpanish (Argentina)complejo de deshidrogenasa de cetoácidos de cadena ramificada:presencia o identidad:punto en el tiempo:sangre:Nominal:
es-ESSpanish (Spain)Complejo de la deshidrogenasa de los cetoácidos de cadena ramificada:Presencia o identidad:Punto temporal:Sangre:Nom:
es-MXSpanish (Mexico)Complejo cetoácido deshidrogenasa de cadena ramificada:Presencia o identidad:Punto temporal:Sangre:Nominal:
fr-CAFrench (Canada)Complexe déshydrogénase acide cétonique branche ramifiée:Présence ou identité:Temps ponctuel:Sang:Nominal:
fr-FRFrench (France)Complexe céto acide déshydrogénase branchée:Identification:Ponctuel:Sang:Résultat nominal:
fr-BEFrench (Belgium)Complexe déshydrogénase acide cétonique branche ramifiée:Présence ou identité:Temps ponctuel:Sang:Nominal:
it-ITItalian (Italy)Complesso chetoacido deidrogenasi a catena ramificata:Prid:Pt:Sangue:Nom:
Synonyms: Chimica Presenza o Identità Punto nel tempo (episodio) Sangue
ko-KRKorean (Korea, Republic Of)분지 사슬 케토산 탈수소효소 복합체:존재:검사시점:전혈:명칭결과:
nl-NLDutch (Netherlands)vertakte-keten ketozuurdehydrogenasecomplex:identificator:moment:bloed:nominaal:
pt-BRPortuguese (Brazil)Complexo cadeia ramificada ceto-ácida dehidrogenase:Ident:Pt:SgTotal:Nom:
Synonyms: ; BCKAD; BCKADH; BCKDH; BCKDC; Branch chain ketoaciduria; Maple syrup urine disease; MSUD; Identity or presence; Point in time; Random; Blood; WB; Whole blood; Nominal; Dehydrog; Dehyrdogenase; Compx; Chn; Chains; Acd; Acids; Chemistry
ru-RURussian (Russian Federation)Разветвленных цепей кето-кислот дегидрогеназы комплекс:ПрИд:ТчкВрм:Кр:Ном:
Synonyms: Кровь Номинальный;Именной Присутствие или Идентификация Точка во времени;Момент
tr-TRTurkish (Turkey)Dallı zincirli ketoasit dehidrogenaz kompleksi:MevcKimlik:Zmlı:Kan:Snf:
zh-CNChinese (China)支链酮酸脱氢酶复合体:存在与否或特征标识:时间点:全血:名义型:
Synonyms: BCKAD;BCKADH;BCKDC;BCKDH;MSUD;分支链酮酸脱氢酶复合体;分支链酮酸脱氢酶复合物;支链酮酸尿病;支链酮酸尿症;支链酮酸脱氢酶复合体(Branched chain keto-acid dehydrogenase complex,BCKAD);支链酮酸脱氢酶复合物;枫糖尿病;枫糖浆尿病;槭糖尿病;槭糖浆尿病;歧链酮酸脱氢酶复合体;歧链酮酸脱氢酶复合物 分类型应答;分类型结果;名义性;名称型;名词型;名词性;标称性;没有自然次序的名义型或分类型应答 化学;化学检验项目;化学检验项目类;化学类;化学试验;非刺激耐受型化学检验项目;非刺激耐受型化学检验项目类;非刺激耐受型化学试验;非刺激耐受型化学试验类 去氢酶 复合体 存在;存在与否;特征标识;身份;身份标识 时刻;随机;随意;瞬间 血;血液 酸

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CodeSystem lookup
https://fhir.loinc.org/CodeSystem/$lookup?system=http://loinc.org&code=33359-1