Part Description

LP18410-8   2-Oxoisovalerate
Elevated levels of 2-oxoisovalerate are associated with maple syrup disease, pyruvate dehydrogenase deficiciency, and lactic acidosis. Slight decreases may occur with deficiencies of lipoic acid or thiamine. (Information from: Kumps A, Duez P, Mardens Y. Metabolic, Nutritional, Iatrogenic, and Artifactual Sources of Urinary Organic Acids: A Comprehensive Table. Clinical Chemistry 2002, 48:708-717.) Source: Regenstrief Institute

LOINC Names Get Info

Fully-Specified Name
2-Oxoisovalerate:SCnc:Pt:Ser/Plas:Qn:
Long Common Name
2-Oxoisovalerate [Moles/volume] in Serum or Plasma
Short Name
2Oxoisovalerate SerPl-sCnc
Display Name
2-Oxoisovalerate [Moles/Vol]
Consumer Name Alpha Get Info
2-Oxoisovalerate, Blood

Part Model Get Info

  • Component
    2-Oxoisovalerate
    LP18410-8
    • Analyte
      2-Oxoisovalerate
      LP18410-8
      • Component Numerator
        2-Oxoisovalerate
        LP18410-8
        • Component Numerator Core
          2-Oxoisovalerate
          LP18410-8
        • Component Numerator Core Suffix
          NULL
           
      • Component Denominator
        NULL
         
        • Component Denominator Core
          NULL
           
        • Component Denominator Core Suffix
          NULL
           
    • Challenge
      NULL
       
    • Adjustment
      NULL
       
    • Count
      NULL
       
  • Property
    SCnc
    LP6860-3
  • Time
    Pt
    LP6960-1
  • System
    Ser/Plas
    LP7576-4
    • System Core
      Ser/Plas
      LP7576-4
    • Super System
      NULL
       
  • Scale
    Qn
    LP7753-9
  • Method
    NULL
     

Basic Attributes

Class
CHEM
Type
Laboratory
First Released
Version 2.13
Last Updated
Version 2.73 (MIN)
Order vs. Observation
Observation
Common Test Rank Get Info
9518

Member of these Panels

LOINCLong Common Name
101455-4Mitochondrial metabolites panel - Serum or Plasma
35866-3Organic acids panel - Serum or Plasma

Language Variants Get Info

TagLanguageTranslation
cs-CZCzech (Czechia)2-oxoizovalerát:Látková koncentrace:Časový bod:Sérum/plazma:Kvantitativní:
el-GRGreek (Greece)2-οξοϊσοβαλερικό:SCnc:Pt:Ορός/Πλάσμα:Qn:
Synonyms: 2-οξοϊσοβαλερικό CHEM Pt Qn SCnc Ορός Ορός/Πλάσμα Πλάσμα
es-ARSpanish (Argentina)2-oxoisovalerato:concentración de sustancia:punto en el tiempo:suero/plasma:cuantitativo:
es-ESSpanish (Spain)2-Oxoisovalerato:Concentración de sustancia:Punto temporal:Suero o Plasma:Qn:
Synonyms: Cuantitativo
es-MXSpanish (Mexico)2-oxoisovalerato:Concentración de sustancias:Punto temporal:Suero o Plasma:Cuantitativo:
et-EEEstonian (Estonia)2-oksoisovaleraat:SCnc:Pt:S/P:Qn:
Synonyms: Aine kontsentratsioon Juhuslik Kvantitatiivne Plasma Seerum Seerum või plasma
fr-CAFrench (Canada)2-oxoisovalérate:Concentration de substance:Temps ponctuel:Sérum/Plasma:Quantitatif:
fr-FRFrench (France)2-oxoisovalérate:Moles/Volume:Ponctuel:Sérum/Plasma:Numérique:
fr-BEFrench (Belgium)2-oxoisovalérate:Concentration de substance:Temps ponctuel:Sérum/Plasma:Quantitatif:
it-ITItalian (Italy)2-Ossoisovalerato:SCnc:Pt:Siero/Plasma:Qn:
Synonyms: Chimica Concentrazione di Sostanza Plasma Punto nel tempo (episodio) Siero Siero o Plasma
ko-KRKorean (Korea, Republic Of)2-옥소이소발레레이트:물질농도:검사시점:혈청/혈장:정량:
nl-NLDutch (Netherlands)2-oxoisovaleraat:mol/volume:moment:serum of plasma:kwantitatief:
pl-PLPolish (Poland)2-Oksoizowalerian:stężenie molowe:punkt w czasie:surowica lub osocze:ilościowy:
pt-BRPortuguese (Brazil)2-Oxoisovalerato:SCnc:Pt:Sor/Plas:Qn:
Synonyms: ; 2Oxoisovalerate; 2-ketoisovaleric acid; 2-ketoisovalerate; 2-oxoisovaleric acid; Substance concentration; Level; Point in time; Random; SerPl; SerPlas; SerP; Serum; SR; Plasma; Pl; Plsm; Quantitative; QNT; Quant; Quan; II; Chemistry
ru-RURussian (Russian Federation)2-Оксоизовалерат:МолКонц:ТчкВрм:Сыв/Плаз:Колич:
Synonyms: Количественный Молярность;Молярная объёмная концентрация Плазма Сыворотка Сыворотка или Плазма Точка во времени;Момент
tr-TRTurkish (Turkey)2-Okzoizovalerat:SubKons:Zmlı:Ser/Plaz:Kant:
zh-CNChinese (China)2-氧代异戊酸:物质的量浓度:时间点:血清/血浆:定量型:
Synonyms: 2-酮基异戊酸;2-酮异戊酸 Ⅱ II 克分子浓度;克分子浓度(单位体积);摩尔浓度;摩尔浓度(单位体积);物质的量浓度(单位体积) 化学;化学检验项目;化学检验项目类;化学类;化学试验;非刺激耐受型化学检验项目;非刺激耐受型化学检验项目类;非刺激耐受型化学试验;非刺激耐受型化学试验类 可用数量表示的;定量性;数值型;数量型;连续数值型标尺 时刻;随机;随意;瞬间 血清或血浆

Example Units

UnitSource
mcmol/LREGENSTRIEF
umol/LExample UCUM Units

LOINC Terminology Service (API) using HL7® FHIR® Get Info

CodeSystem lookup
https://fhir.loinc.org/CodeSystem/$lookup?system=http://loinc.org&code=35868-9