Part Description

LP100176-9   2-Methylacetoacetate
2-Methylacetoacetic acid is a metabolite that has an increased excretion in patients with acetoacetyl-CoA thiolase deficiency. Thiolases are ubiquitous and important enzymes. Several isoenzymes are known, which can occur in the cytosol (ACAT2), the mitochondria (ACAT1), or the peroxisomes (ACAA2). Thiolases are CoA-dependent enzymes which catalyze the formation of a carbon-carbon bond in a Claisen condensation step and its reverse reaction via a thiolytic degradation mechanism. Mitochondrial acetoacetyl-coenzyme A (CoA) thiolase (T2) is important in the pathways for the synthesis and degradation of ketone bodies as well as for the degradation of 2-methylacetoacetyl-CoA. PMID: 17371050, PMID: 14518824, PMID: 9744475, PMID: 9001814 Copyright Copyright ©2005-2009 Genome Alberta (Reference to original publication: Wishart DS, Knox C, Guo AC, et al. HMDB: a knowledgebase for the human metabolome. Nucleic Acids Res. 2009 37(Database issue):D603-610.) Source: Human Metabolome Database, 2-Methylacetoacetate

LOINC Names Get Info

Fully-Specified Name
2-Methylacetoacetate:SCnc:Pt:CSF:Qn:
Long Common Name
2-Methylacetoacetate [Moles/volume] in Cerebrospinal Fluid
Short Name
2-Methylacetoacetate CSF-sCnc
Display Name
2-Methylacetoacetate (CSF) [Moles/Vol]
Consumer Name Alpha Get Info
2-Methylacetoacetate, Spinal fluid

Part Model Get Info

  • Component
    2-Methylacetoacetate
    LP100176-9
    • Analyte
      2-Methylacetoacetate
      LP100176-9
      • Component Numerator
        2-Methylacetoacetate
        LP100176-9
        • Component Numerator Core
          2-Methylacetoacetate
          LP100176-9
        • Component Numerator Core Suffix
          NULL
           
      • Component Denominator
        NULL
         
        • Component Denominator Core
          NULL
           
        • Component Denominator Core Suffix
          NULL
           
    • Challenge
      NULL
       
    • Adjustment
      NULL
       
    • Count
      NULL
       
  • Property
    SCnc
    LP6860-3
  • Time
    Pt
    LP6960-1
  • System
    CSF
    LP7156-5
    • System Core
      CSF
      LP7156-5
    • Super System
      NULL
       
  • Scale
    Qn
    LP7753-9
  • Method
    NULL
     

Basic Attributes

Class
CHEM
Type
Laboratory
First Released
Version 2.40
Last Updated
Version 2.83 (MIN)
Order vs. Observation
Both

Language Variants Get Info

TagLanguageTranslation
cs-CZCzech (Czechia)2-methylacetoacetát:Látková koncentrace:Časový bod:Mozkomíšní mok:Kvantitativní:
el-GRGreek (Greece)2-Ακετοξικό μεθύλιο:SCnc:Pt:ΕΝΥ:Qn:
Synonyms: 2-Ακετοξικό μεθύλιο CHEM Pt Qn SCnc ΕΝΥ
es-ESSpanish (Spain)2-Metilacetoacetato:Concentración de sustancia:Punto temporal:Líquido Cefalorraquideo:Qn:
Synonyms: Cuantitativo
es-MXSpanish (Mexico)2-metilacetoacetato:Concentración de sustancias:Punto temporal:Fluído espinal cerebral:Cuantitativo:
et-EEEstonian (Estonia)2-metüülatseetoatsetaat:SCnc:Pt:CSF:Qn:
Synonyms: Aine kontsentratsioon Juhuslik Kvantitatiivne Liikvor
fr-CAFrench (Canada)2-méthylacétoacetate:Concentration de substance:Temps ponctuel:LCR:Quantitatif:
fr-FRFrench (France)2-méthylacétoacétate:Moles/Volume:Ponctuel:Liquide céphalorachidien:Numérique:
fr-BEFrench (Belgium)2-Methylacetoacetate:Concentration de substance:Temps ponctuel:LCR:Quantitatif:
Synonyms: 2-Méthyl-acétoacétate
it-ITItalian (Italy)2-Metilacetoacetato:SCnc:Pt:LCS:Qn:
Synonyms: Chimica Concentrazione di Sostanza Liquido cerebrospinale Punto nel tempo (episodio)
nl-NLDutch (Netherlands)2-methylacetoacetaat:mol/volume:moment:liquor cerebrospinalis:kwantitatief:
pl-PLPolish (Poland)2-metyloacetooctan:stężenie molowe:punkt w czasie:płyn mózgowo-rdzeniowy:ilościowy:
ru-RURussian (Russian Federation)2-метилацетоацетат:МолКонц:ТчкВрм:ЦСЖ:Колич:
Synonyms: Количественный Молярность;Молярная объёмная концентрация Точка во времени;Момент Цереброспинальная жидкость
tr-TRTurkish (Turkey)2-Metilasetoasetat:SubKons:Zmlı:BOS:Kant:
zh-CNChinese (China)2-甲基乙酰乙酸乙酯:物质的量浓度:时间点:脑脊液:定量型:
Synonyms: Ⅱ CSF CSF;脊髓液;Cerebral spinal fluid;脑脊髓液 II α-丁酮酸乙酯;Α-丁酮酸乙酯;甲基乙醯乙酸乙酯;Α-甲基乙酰乙酸乙酯;Α-甲基乙酰乙酸乙酯 克分子浓度;克分子浓度(单位体积);摩尔浓度;摩尔浓度(单位体积);物质的量浓度(单位体积) 化学;化学检验项目;化学检验项目类;化学类;化学试验;非刺激耐受型化学检验项目;非刺激耐受型化学检验项目类;非刺激耐受型化学试验;非刺激耐受型化学试验类 可用数量表示的;定量性;数值型;数量型;连续数值型标尺 时刻;随机;随意;瞬间 脊液 脊髓液 脑脊液(Cerebral spinal fluid,CSF) 脑脊髓液

Example Units

UnitSource
umol/LExample UCUM Units

LOINC Terminology Service (API) using HL7® FHIR® Get Info

CodeSystem lookup
https://fhir.loinc.org/CodeSystem/$lookup?system=http://loinc.org&code=69786-2