Version 2.77

Part Description

LP174021-8   Coagulation factor IX activity actual/Normal
Factor IX is one of the thirteen plasma proteins known as clotting factors that regulate hemostasis. When functionality or quantity of Factor IX is decreased, increased bleeding occurs. The bleeding can be internal into the joints and muscles, or external from minor cuts, dental procedures or trauma. The severity of bleeding is associated with how much functional FIX is present in the plasma. The three categories of severity are: 1) mild-6-49% of factor IX required for normal clotting is present or functional; 2) moderate-1-5% of factor IX required for normal clotting is present or functional; 3) severe-less than 1% of factor IX required for normal clotting is present or functional. Factor IX deficiency is known as hemophilia B or Christmas disease. It is usually an inherited genetic defect of the F9 gene located on the X chromosome, though the cause of hemophilia B in one third of patients is spontaneous mutation of the F9 gene. Treatment for hemophilia B is human or recombinant factor IX given intravenously.[https://www.hemophilia.org/Bleeding-Disorders/Types-of-Bleeding-Disorders/Hemophilia-B] Source: Regenstrief LOINC

Fully-Specified Name

Component
Coagulation factor IX activity actual/Normal
Property
RelCCnc
Time
Pt
System
PPP
Scale
Qn
Method
Chromo

Additional Names

Short Name
Fact IX Act/Nor PPP Chro
Display Name
Coagulation factor IX activity actual/normal Chromogenic method (PPP) [Rel catalytic activity/Vol]
Consumer Name Alpha Get Info
Coagulation Factor IX Activity actual/normal, Blood

Basic Attributes

Class
COAG
Type
Laboratory
First Released
Version 2.64
Last Updated
Version 2.73
Order vs. Observation
Both
Common Test Rank Get Info
7709

Language Variants Get Info

Tag Language Translation
de-AT German (Austria) Synonyms: Faktor IX Akt. chr
es-ES Spanish (Spain) Actividadd del factor IX de coagulación actual/normal:Concentración catalítica relativa:Punto temporal:Plasma pobre en plaquetas:Qn:Cromogénico ( Enzima)
Synonyms: Cuantitativo
es-MX Spanish (Mexico) Actividad del factor IX de coagulación real / normal:Concentración catalítica relativa:Punto temporal:Plasma pobre en plaquetas:Cuantitativo:Cromogénico (enzima)
fr-CA French (Canada) Facteur IX Activité , Mesuré/normal:Concentration catalytique relative:Temps ponctuel:Plasma pauvre en plaquettes:Quantitatif:Chromogénique
fr-FR French (France) Facteur IX activité Patient (%):Activité catalytique relative:Ponctuel:Plasma pauvre en plaquettes:Numérique:Technique chromogénique
fr-BE French (Belgium) Facteur IX Activité Mesuré/normal:Concentration catalytique relative:Temps ponctuel:Plasma pauvre en plaquettes:Quantitatif:Chromogénique
Synonyms: F IX F IX.Activité Mesuré/normal
it-IT Italian (Italy) Fattore di coagulazione IX, attività effettivo/normale:RelCCnc:Pt:PPP:Qn:Cromo
Synonyms: Attività del fattore di coagulazione IX Concentrazione Catalitica Relativa Cromogenico (Enzima) Plasma povero di piastrine Punto nel tempo (episodio) Studio di coagulazione
nl-NL Dutch (Netherlands) stollingsfactor IX activiteit gemeten/normaal:relatieve enzymatische activiteit/normaal:moment:plaatjesarm plasma:kwantitatief:chromogeen
Synonyms: coagulatiemethode gemeten/normaal
pl-PL Polish (Poland) Aktywność czynnika krzepnięcia IX badane/prawidłowe:względne stężenie katalityczne:punkt w czasie:osocze ubogopłytkowe:ilościowy:metoda z substratem chromogennym
Synonyms: Aktywność czynnika IX krzepnięcia oznaczona/prawidłowa IX PPP
ru-RU Russian (Russian Federation) Коагуляция фактор IX активность актуальный/нормальный:ОтнКаталКонц:ТчкВрм:ОПП:Колич:Хромо
Synonyms: Количественный Обеднённая пластинками плазма;Бедная тромбоцитами плазма Относительная каталитическая концентрация Точка во времени;Момент Хромогенный (Фермент)
tr-TR Turkish (Turkey) Koagülasyon faktörü IX aktivitesi gerçek/normal:GörKtlKons:Zmlı:TFkP:Kant:Kromo
uk-UA Ukrainian (Ukraine) Коагуляційний фактор IX активність фактична/Нормальна:Відносна Каталітична Концентрація:МоментЧасу:Бідна тромбоцитами плазма:Кількісно:Хромогенний метод
Synonyms: Act/Nor; Activ; Actvty; Antihemophilic factor B; Christmas factor; Chromogenic assay; Coag; Control; ENZY; Enzymatic assay; Fac; Fact; Fact IX; Factor 9; FIX; Hematology; Heme; Movements; Plas; Plasma thromboplastin component; Platelet poor plasma; Point in time; PTC; QNT; Quan; Quant; Quantitative; Random; RlCCnc; Thrombocyte cofactor II
zh-CN Chinese (China) 凝血因子IX活性 实际的/正常的:相对催化浓度:时间点:贫血小板血浆:定量型:凝血因子酶学测定法
Synonyms: Ⅸ FIX PTC;凝血因子Ⅸ;圣诞因子;圣诞因子(Christmas factor);圣诞节因子;抗血友病因子 B;血小板辅因子 II;血浆促凝血酶原激酶成分;血浆促凝血酶原激酶成分(Plasma thromboplastin component,PTC);血浆凝血活素成分;血浆凝血活酶成分;血浆凝血致活酶成分;血浆组织促凝血酶原激酶成分 乏血小板血浆;Platelet poor plasma;PPP 凝固;凝固现象;凝血;凝血作用;凝血功能;凝血功能类;凝血类成分;凝血过程 凝血功能;凝血功能试验;凝血过程;血液凝固;血液凝固功能;血液凝固过程 凝血因子Ⅸ;因子 IX;因子Ⅸ;血液制品 - 凝血因子 IX;血液制品 - 凝血因子Ⅸ;血液制品 - 因子 IX;血液制品 - 因子Ⅸ 凝血因子发色测定方法;凝血因子发色测定法;凝血因子酶学测定方法;发色法;发色测定方法;发色测定法;显色法;显色测定方法;显色测定法;酶学法;酶学测定方法;酶学测定法;酶法 可用数量表示的;定量性;数值型;数量型;连续数值型标尺 因子 IX 因素 实测值 实测值/正常值;实际/正常;实际值/正常值;实际测定值/正常值 实测的 实际值 对照 对照标准 对照物 对照的 时刻;随机;随意;瞬间 正常的 活动 系数

Example Units

Unit Source
% Example UCUM Units

LOINC Terminology Service (API) using HL7® FHIR® Get Info

CodeSystem lookup
https://fhir.loinc.org/CodeSystem/$lookup?system=http://loinc.org&code=88449-4