Part Description

LP230267-9   Dipeptidyl aminopeptidase-like protein 6
Dipeptidyl aminopeptidase-like protein 6 (DPPX) is a regulatory subunit of neuronal Kv4.2 potassium channel and is encoded by the DPPX gene. PMID: 25320100 DPPX is a type II membrane protein that binds to specific voltage-gated potassium channels and changes their biophysical characteristics. Alterations in the DPPX gene are associated with amyotrophic lateral sclerosis with idiopathic ventricular fibrillation. [NCBI Gene ID: 1804] IgG to DPPX is a biomarker for a frequently multifocal neurological disorder that develops insidiously, can be severe, responds to immunotherapy and is likely to relapse. Clinical symptoms associated with postive DPPX IgG include encephalopathy (with cortical, cerebellar or brainstem manifestations), myelopathy and autonomic dysfunction. PMID: 25320100 Source: Regenstrief LOINC

LOINC Names Get Info

Fully-Specified Name
Dipeptidyl aminopeptidase-like protein 6 Ab.IgG:Titr:Pt:CSF:SemiQn:IF
Long Common Name
Dipeptidyl aminopeptidase-like protein 6 IgG Ab [Titer] in Cerebrospinal Fluid by Immunofluorescence
Short Name
DPPX IgG Titr CSF IF
Display Name
Dipeptidyl aminopeptidase-like protein 6 IgG IF (CSF) [Titer]
Consumer Name Alpha Get Info
Dipeptidyl aminopeptidase-like protein 6 IgG antibody, Spinal fluid

Part Model Get Info

  • Component
    Dipeptidyl aminopeptidase-like protein 6 Ab.IgG
    LP232461-6
    • Analyte
      Dipeptidyl aminopeptidase-like protein 6 Ab.IgG
      LP232461-6
      • Component Numerator
        Dipeptidyl aminopeptidase-like protein 6 Ab.IgG
        LP232461-6
        • Component Numerator Core
          Dipeptidyl aminopeptidase-like protein 6
          LP230267-9
        • Component Numerator Core Suffix
          Ab.IgG
          LP32401-9
      • Component Denominator
        NULL
         
        • Component Denominator Core
          NULL
           
        • Component Denominator Core Suffix
          NULL
           
    • Challenge
      NULL
       
    • Adjustment
      NULL
       
    • Count
      NULL
       
  • Property
    Titr
    LP6881-9
  • Time
    Pt
    LP6960-1
  • System
    CSF
    LP7156-5
    • System Core
      CSF
      LP7156-5
    • Super System
      NULL
       
  • Scale
    SemiQn
    LP436123-6
  • Method
    IF
    LP6323-2

Basic Attributes

Class
SERO
Type
Laboratory
First Released
Version 2.68
Last Updated
Version 2.83 (MIN)
Order vs. Observation
Both

Language Variants Get Info

TagLanguageTranslation
cs-CZCzech (Czechia)Dipeptidyl aminopeptidase-like protein 6 (DPP6) IgG:Arbitrární koncentrace (titr):Časový bod:Mozkomíšní mok:Semikvantitativní:Imunofluoresecence (IF)
el-GRGreek (Greece)Πρωτεΐνη τύπου διπεπτιδυλικής αμινοπεπτιδάσης 6 Αντισώματα IgG:Titr:Pt:ΕΝΥ:Ημιποσοτική:Ανοσοφθορισμός
Synonyms: Pt SERO Titr Ανοσοσφαιρίνη G Ανοσοφθορισμός Αντίσωμα Αντισώματα IgG ΕΝΥ Ημιποσοτική Πρωτεΐνη Πρωτεΐνη τύπου διπεπτιδυλικής αμινοπεπτιδάσης 6
es-ESSpanish (Spain)Proteina 6 tipo Dipeptidil aminopeptidasa IgG:Titulo / Factor de dilución:Punto temporal:Líquido Cefalorraquideo:Semicuantitativo:Inmunofluorescencia (IF)
Synonyms: Semicuantitativo
es-MXSpanish (Mexico)Proteína similar a la dipeptidil aminopeptidasa 6 Ab.IgG:Título:Punto temporal:Fluído espinal cerebral:Cuantitativo:Inmunofluorescencia (IF)
fr-FRFrench (France)DPPX6 Ac IgG:Titre:Ponctuel:Liquide céphalorachidien:Semi-Quantitatif:Immunofluorescence
it-ITItalian (Italy)Dipeptidil aminopeptidasi-like proteina 6 Ab.IgG:Titr:Pt:LCS:SemiQn:IF
Synonyms: anticorpi IgG anticorpo Immunofluorescenza (IF) Liquido cerebrospinale Punto nel tempo (episodio) Sierologia (anticorpi e la maggior parte degli ant Titolo
nl-NLDutch (Netherlands)dipeptidyl-aminopeptidase-achtig proteïne 6 As.IgG:titer:moment:liquor cerebrospinalis:semikwantitatief:immunofluorescentie
Synonyms: antistof; antilichaam dipeptidyl-aminopeptidase-like IF
pl-PLPolish (Poland)Białko podobne do dipeptydylowej aminopeptydazy 6 Ab.IgG:miano:punkt w czasie:płyn mózgowo-rdzeniowy:półilościowy:immunofluorescencja
Synonyms: DPP6 IgG przeciwciała IgG Przeciwciała IgG do białka podobnego do aminopeptydazy dipeptydylowej 6
zh-CNChinese (China)二肽氨基肽酶样蛋白 6 抗体.IgG:滴定度:时间点:脑脊液:半定量型:免疫荧光法
Synonyms: Ab.IgG;IgG;抗体 IgG Ab;自身抗体 CSF CSF;脊髓液;Cerebral spinal fluid;脑脊髓液 IFA法;IF法;抗补体免疫荧光法;时间分辨荧光法;荧光原位杂交技术;荧光原位杂交法;荧光抗体 PR;Prot;成分 - 化学 - 蛋白质类;蛋白;朊;蛋白质类;蛋白质类物质 二肽氨肽酶样蛋白 6;DPP6;DPPX;DPP VI;VF2;MRD33;DPL1;二肽氨基肽酶相关蛋白;二肽氨基肽酶 6;二肽氨基肽酶 IV-样蛋白;二肽氨基肽酶 VI;Dipeptidyl aminopeptidase-related protein;Dipeptidyl peptidase 6;Dipeptidyl peptidase IV-like protein;Dipeptidyl peptidase VI 免疫球蛋白 G 效价;滴定浓度;滴定率;滴定量;滴度;稀释倍数;稀释因子;稀释系数 时刻;随机;随意;瞬间 氨肽酶 脊液 脊髓液 脑脊液(Cerebral spinal fluid,CSF) 脑脊髓液 血清;血清学;血清学检验项目;血清学检验项目 (非微生物学);血清学检验项目(非微生物学);血清学检验项目类;血清学检验项目类 (非微生物学);血清学类;血清学类检验项目;血清学类检验项目 (非微生物学);血清学类试验;血清学类试验 (非微生物学);血清学试验;血清学试验 (非微生物学);血清学试验(非微生物学);血清学试验类 (非微生物学);血清类

Example Units

UnitSource
{titer}Example UCUM Units

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CodeSystem lookup
https://fhir.loinc.org/CodeSystem/$lookup?system=http://loinc.org&code=94284-7