26904-3 2-Methylcitrate [Moles/volume] in Serum or Plasma

Term Description

same as methylcitrate

Part Descriptions

LP18136-9   2-Methylcitrate
Elevated methylcitric acid levels are indicative of an underlying metabolic disorder such as methylmalonic acidemia (MMA) and propionic acidemia (PA). Source: Regenstrief LOINC

LP18136-9   2-Methylcitrate
2-Methylcitrate (methylcitric acid (MCA)) is measured as a second-tier assay when abnormal propionyl carnitine or methionine concentrations are identified in a primary newborn screen. Methylmalonic acidemia (MMA) and propionic acidemia (PA) are defects of propionate metabolism caused by deficiencies in methylmalonyl-CoA mutase and propionyl-CoA carboxylase, respectively. The clinical phenotype of both conditions includes vomiting, hypotonia, lethargy, apnea, hypothermia, and coma in the newborn period, and both MMA and PA are associated with elevated MCA and propionyl carnitine concentrations. MMA and PA can be distinguished based on methylmalonic acid concentration, which is elevated in MMA and normal in PA. Source: Regenstrief LOINC

Fully-Specified Name

Component
2-Methylcitrate
Property
SCnc
Time
Pt
System
Ser/Plas
Scale
Qn
Method

Basic Attributes

Class
CHEM
Type
Laboratory
First Released
Version 2.00
Last Updated
Version 2.73 (MIN)
Order vs. Observation
Observation
Common Test Rank Get Info
8253

Member of these Panels

LOINCLong Common Name
104535-0Cobalamin, Methionine and Methylmalonic Acid Pathways Panel - Serum or Plasma
101455-4Mitochondrial metabolites panel - Serum or Plasma

Member of these Groups Get Info

LOINC GroupGroup Name
LG41972-72-Methylcitrate|Pt|Ser/Plas

Language Variants Get Info

TagLanguageTranslation
cs-CZCzech (Czechia)2-methylcitrát:Látková koncentrace:Časový bod:Sérum/plazma:Kvantitativní:
de-DEGerman (Germany)2-Methylcitrat:Stoffmengenkonzentration:Zeitpunkt:Serum oder Plasma:Quantitativ:
el-GRGreek (Greece)Κιτρικό 2-μεθύλιο:SCnc:Pt:Ορός/Πλάσμα:Qn:
Synonyms: CHEM Pt Qn SCnc Κιτρικό 2-μεθύλιο Ορός Ορός/Πλάσμα Πλάσμα
es-ARSpanish (Argentina)2-metilcitrato:concentración de sustancia:punto en el tiempo:suero/plasma:cuantitativo:
es-ESSpanish (Spain)2-Metilcitrato:Concentración de sustancia:Punto temporal:Suero o Plasma:Qn:
Synonyms: Cuantitativo
es-MXSpanish (Mexico)2-metilcitrato:Concentración de sustancias:Punto temporal:Suero o Plasma:Cuantitativo:
et-EEEstonian (Estonia)2-metüültsitraat:SCnc:Pt:S/P:Qn:
Synonyms: Aine kontsentratsioon Juhuslik Kvantitatiivne Plasma Seerum Seerum või plasma
fr-CAFrench (Canada)2-méthylcitrate:Concentration de substance:Temps ponctuel:Sérum/Plasma:Quantitatif:
fr-FRFrench (France)2-méthylcitrate:Moles/Volume:Ponctuel:Sérum/Plasma:Numérique:
fr-BEFrench (Belgium)2-méthylcitrate:Concentration de substance:Temps ponctuel:Sérum/Plasma:Quantitatif:
it-ITItalian (Italy)2-Metilcitrato:SCnc:Pt:Siero/Plasma:Qn:
Synonyms: Chimica Concentrazione di Sostanza Plasma Punto nel tempo (episodio) Siero Siero o Plasma
ko-KRKorean (Korea, Republic Of)2-메틸시트레이트:물질농도:검사시점:혈청/혈장:정량:
nl-NLDutch (Netherlands)2-methylcitraat:mol/volume:moment:serum of plasma:kwantitatief:
pl-PLPolish (Poland)2-Metylocytrynian:stężenie molowe:punkt w czasie:surowica lub osocze:ilościowy:
pt-BRPortuguese (Brazil)2-Metilcitrato:SCnc:Pt:Sor/Plas:Qn:
Synonyms: ; 2Me-citrate; Methylcitric acid; Substance concentration; Level; Point in time; Random; SerPl; SerPlas; SerP; Serum; SR; Plasma; Pl; Plsm; Quantitative; QNT; Quant; Quan; II; Chemistry
ru-RURussian (Russian Federation)2-Метилцитрат:МолКонц:ТчкВрм:Сыв/Плаз:Колич:
Synonyms: Количественный Молярность;Молярная объёмная концентрация Плазма Сыворотка Сыворотка или Плазма Точка во времени;Момент
tr-TRTurkish (Turkey)2-Metilsitrat:SubKons:Zmlı:Ser/Plaz:Kant:
zh-CNChinese (China)2-甲基柠檬酸:物质的量浓度:时间点:血清/血浆:定量型:
Synonyms: 2Me-柠檬酸;Me-柠檬酸;甲基柠檬酸 Ⅱ II 克分子浓度;克分子浓度(单位体积);摩尔浓度;摩尔浓度(单位体积);物质的量浓度(单位体积) 化学;化学检验项目;化学检验项目类;化学类;化学试验;非刺激耐受型化学检验项目;非刺激耐受型化学检验项目类;非刺激耐受型化学试验;非刺激耐受型化学试验类 可用数量表示的;定量性;数值型;数量型;连续数值型标尺 时刻;随机;随意;瞬间 血清或血浆

Example Units

UnitSource
nmol/LExample UCUM Units

33273-4 3-Methylglutaconate [Moles/volume] in Serum or Plasma

Part Descriptions

LP18420-7   3-Methylglutaconate
3-Methylglutaconic acid is a glutarate which builds up in the urine in 3-Methylglutaconic aciduria or 3-Hydroxy-3-methylglutaric aciduria. Copyright Text is available under the Creative Commons Attribution/Share-Alike License. See http://creativecommons.org/licenses/by-sa/3.0/ for details. Source: Wikipedia, Wikipedia

Fully-Specified Name

Component
3-Methylglutaconate
Property
SCnc
Time
Pt
System
Ser/Plas
Scale
Qn
Method

Basic Attributes

Class
CHEM
Type
Laboratory
First Released
Version 2.09
Last Updated
Version 2.70 (MIN)
Order vs. Observation
Observation

Member of these Panels

LOINCLong Common Name
101455-4Mitochondrial metabolites panel - Serum or Plasma

Language Variants Get Info

TagLanguageTranslation
cs-CZCzech (Czechia)3-methylglutakonát:Látková koncentrace:Časový bod:Sérum/plazma:Kvantitativní:
el-GRGreek (Greece)3-μεθυλογλουτακονικό οξύ:SCnc:Pt:Ορός/Πλάσμα:Qn:
Synonyms: 3-μεθυλογλουτακονικό οξύ CHEM Pt Qn SCnc Ορός Ορός/Πλάσμα Πλάσμα
es-ARSpanish (Argentina)3-metilglutaconato:concentración de sustancia:punto en el tiempo:suero/plasma:cuantitativo:
es-ESSpanish (Spain)3-Metilglutaconato:Concentración de sustancia:Punto temporal:Suero o Plasma:Qn:
Synonyms: Cuantitativo
es-MXSpanish (Mexico)3-metilglutaconato:Concentración de sustancias:Punto temporal:Suero o Plasma:Cuantitativo:
et-EEEstonian (Estonia)3-metüülglutakonaat:SCnc:Pt:S/P:Qn:
Synonyms: Aine kontsentratsioon Juhuslik Kvantitatiivne Plasma Seerum Seerum või plasma
fr-CAFrench (Canada)3-méthylglutaconate:Concentration de substance:Temps ponctuel:Sérum/Plasma:Quantitatif:
fr-FRFrench (France)3-méthylglutaconate:Moles/Volume:Ponctuel:Sérum/Plasma:Numérique:
fr-BEFrench (Belgium)3-méthylglutaconate:Concentration de substance:Temps ponctuel:Sérum/Plasma:Quantitatif:
it-ITItalian (Italy)3-Metilglutaconato:SCnc:Pt:Siero/Plasma:Qn:
Synonyms: Chimica Concentrazione di Sostanza Plasma Punto nel tempo (episodio) Siero Siero o Plasma
ko-KRKorean (Korea, Republic Of)3-메틸글루타코네이트:물질농도:검사시점:혈청/혈장:정량:
nl-NLDutch (Netherlands)3-methylglutaconaat:mol/volume:moment:serum of plasma:kwantitatief:
pl-PLPolish (Poland)3-metyloglutakonian:stężenie molowe:punkt w czasie:surowica lub osocze:ilościowy:
pt-BRPortuguese (Brazil)3-Metilglutaconato:SCnc:Pt:Sor/Plas:Qn:
Synonyms: ; 3Me-glutaconate; 3-methylglutaconic acid; Substance concentration; Level; Point in time; Random; SerPl; SerPlas; SerP; Serum; SR; Plasma; Pl; Plsm; Quantitative; QNT; Quant; Quan; III; Chemistry
ru-RURussian (Russian Federation)3-Метилглутаконат:МолКонц:ТчкВрм:Сыв/Плаз:Колич:
Synonyms: Количественный Молярность;Молярная объёмная концентрация Плазма Сыворотка Сыворотка или Плазма Точка во времени;Момент
tr-TRTurkish (Turkey)3-Metilglutakonat:SubKons:Zmlı:Ser/Plaz:Kant:
zh-CNChinese (China)3-甲基戊烯二酸:物质的量浓度:时间点:血清/血浆:定量型:
Synonyms: 3-Me-戊烯二酸 Ⅲ III 三 克分子浓度;克分子浓度(单位体积);摩尔浓度;摩尔浓度(单位体积);物质的量浓度(单位体积) 化学;化学检验项目;化学检验项目类;化学类;化学试验;非刺激耐受型化学检验项目;非刺激耐受型化学检验项目类;非刺激耐受型化学试验;非刺激耐受型化学试验类 叁 可用数量表示的;定量性;数值型;数量型;连续数值型标尺 时刻;随机;随意;瞬间 血清或血浆

Example Units

UnitSource
nmol/LExample UCUM Units
nmol/LREGENSTRIEF

35870-5 2-Oxoisocaproate [Moles/volume] in Serum or Plasma

Part Descriptions

LP16012-4   2-Oxoisocaproate
2-oxoisocaproate is a branched-chain 2-oxo acid (BCOA) that accumulates in maple syrup urine disease (MSUD). Increased levels of BCOAs is associated with chronic dysmyelinating changes in the central nervous system (CNS). PMID: 1583867 Source: Regenstrief LOINC, PMID: 1583867

Fully-Specified Name

Component
2-Oxoisocaproate
Property
SCnc
Time
Pt
System
Ser/Plas
Scale
Qn
Method

Basic Attributes

Class
CHEM
Type
Laboratory
First Released
Version 2.13
Last Updated
Version 2.73 (MIN)
Order vs. Observation
Observation
Common Test Rank Get Info
9520

Member of these Panels

LOINCLong Common Name
101455-4Mitochondrial metabolites panel - Serum or Plasma
35866-3Organic acids panel - Serum or Plasma

Language Variants Get Info

TagLanguageTranslation
cs-CZCzech (Czechia)2-Oxoisokapronát:Látková koncentrace:Časový bod:Sérum/plazma:Kvantitativní:
el-GRGreek (Greece)2-Οξοϊσοκαπροϊκό οξύ:SCnc:Pt:Ορός/Πλάσμα:Qn:
Synonyms: 2-Οξοϊσοκαπροϊκό οξύ CHEM Pt Qn SCnc Ορός Ορός/Πλάσμα Πλάσμα
es-ARSpanish (Argentina)2-oxoisocaproato:concentración de sustancia:punto en el tiempo:suero/plasma:cuantitativo:
es-ESSpanish (Spain)2-Oxoisocaproato:Concentración de sustancia:Punto temporal:Suero o Plasma:Qn:
Synonyms: Cuantitativo
es-MXSpanish (Mexico)2-oxoisocaproato:Concentración de sustancias:Punto temporal:Suero o Plasma:Cuantitativo:
et-EEEstonian (Estonia)2-oksoisokaproaat:SCnc:Pt:S/P:Qn:
Synonyms: Aine kontsentratsioon Juhuslik Kvantitatiivne Plasma Seerum Seerum või plasma
fr-CAFrench (Canada)2-oxoisocaproate:Concentration de substance:Temps ponctuel:Sérum/Plasma:Quantitatif:
fr-FRFrench (France)2-oxoisocaproate:Moles/Volume:Ponctuel:Sérum/Plasma:Numérique:
fr-BEFrench (Belgium)2-oxoisocaproate:Concentration de substance:Temps ponctuel:Sérum/Plasma:Quantitatif:
it-ITItalian (Italy)2-Ossoisocaproato:SCnc:Pt:Siero/Plasma:Qn:
Synonyms: Chimica Concentrazione di Sostanza Plasma Punto nel tempo (episodio) Siero Siero o Plasma
ko-KRKorean (Korea, Republic Of)2-옥소이소카프로에이트:물질농도:검사시점:혈청/혈장:정량:
nl-NLDutch (Netherlands)2-oxoisocaproaat:mol/volume:moment:serum of plasma:kwantitatief:
pl-PLPolish (Poland)2-Oksoizokapronian:stężenie molowe:punkt w czasie:surowica lub osocze:ilościowy:
pt-BRPortuguese (Brazil)2-Oxoisocaproato:SCnc:Pt:Sor/Plas:Qn:
Synonyms: ; 2Oxoisocaproate; 2-ketoisocaproic acid; 2-ketoisocaproate; alpha-ketoisocaproic acid; alpha-ketoisocaproate; 2-keto-4-methylvalerate; 2-oxoisocaproic acid; Substance concentration; Level; Point in time; Random; SerPl; SerPlas; SerP; Serum; SR; Plasma; Pl; Plsm; Quantitative; QNT; Quant; Quan; II; Chemistry
ru-RURussian (Russian Federation)2-Оксоизокапроат:МолКонц:ТчкВрм:Сыв/Плаз:Колич:
Synonyms: Количественный Молярность;Молярная объёмная концентрация Плазма Сыворотка Сыворотка или Плазма Точка во времени;Момент
tr-TRTurkish (Turkey)2-Okzoizokaproat:SubKons:Zmlı:Ser/Plaz:Kant:
zh-CNChinese (China)2-氧代异己酸:物质的量浓度:时间点:血清/血浆:定量型:
Synonyms: 2-酮基-4-甲基戊酸;2-酮基异己酸;2-酮异己酸;Alpha-酮基异己酸;α-酮基异己酸 Ⅱ II 克分子浓度;克分子浓度(单位体积);摩尔浓度;摩尔浓度(单位体积);物质的量浓度(单位体积) 化学;化学检验项目;化学检验项目类;化学类;化学试验;非刺激耐受型化学检验项目;非刺激耐受型化学检验项目类;非刺激耐受型化学试验;非刺激耐受型化学试验类 可用数量表示的;定量性;数值型;数量型;连续数值型标尺 时刻;随机;随意;瞬间 血清或血浆

Example Units

UnitSource
umol/LExample UCUM Units
mcmol/LREGENSTRIEF

35868-9 2-Oxoisovalerate [Moles/volume] in Serum or Plasma

Part Descriptions

LP18410-8   2-Oxoisovalerate
Elevated levels of 2-oxoisovalerate are associated with maple syrup disease, pyruvate dehydrogenase deficiciency, and lactic acidosis. Slight decreases may occur with deficiencies of lipoic acid or thiamine. (Information from: Kumps A, Duez P, Mardens Y. Metabolic, Nutritional, Iatrogenic, and Artifactual Sources of Urinary Organic Acids: A Comprehensive Table. Clinical Chemistry 2002, 48:708-717.) Source: Regenstrief Institute

Fully-Specified Name

Component
2-Oxoisovalerate
Property
SCnc
Time
Pt
System
Ser/Plas
Scale
Qn
Method

Basic Attributes

Class
CHEM
Type
Laboratory
First Released
Version 2.13
Last Updated
Version 2.73 (MIN)
Order vs. Observation
Observation
Common Test Rank Get Info
9518

Member of these Panels

LOINCLong Common Name
101455-4Mitochondrial metabolites panel - Serum or Plasma
35866-3Organic acids panel - Serum or Plasma

Language Variants Get Info

TagLanguageTranslation
cs-CZCzech (Czechia)2-oxoizovalerát:Látková koncentrace:Časový bod:Sérum/plazma:Kvantitativní:
el-GRGreek (Greece)2-οξοϊσοβαλερικό:SCnc:Pt:Ορός/Πλάσμα:Qn:
Synonyms: 2-οξοϊσοβαλερικό CHEM Pt Qn SCnc Ορός Ορός/Πλάσμα Πλάσμα
es-ARSpanish (Argentina)2-oxoisovalerato:concentración de sustancia:punto en el tiempo:suero/plasma:cuantitativo:
es-ESSpanish (Spain)2-Oxoisovalerato:Concentración de sustancia:Punto temporal:Suero o Plasma:Qn:
Synonyms: Cuantitativo
es-MXSpanish (Mexico)2-oxoisovalerato:Concentración de sustancias:Punto temporal:Suero o Plasma:Cuantitativo:
et-EEEstonian (Estonia)2-oksoisovaleraat:SCnc:Pt:S/P:Qn:
Synonyms: Aine kontsentratsioon Juhuslik Kvantitatiivne Plasma Seerum Seerum või plasma
fr-CAFrench (Canada)2-oxoisovalérate:Concentration de substance:Temps ponctuel:Sérum/Plasma:Quantitatif:
fr-FRFrench (France)2-oxoisovalérate:Moles/Volume:Ponctuel:Sérum/Plasma:Numérique:
fr-BEFrench (Belgium)2-oxoisovalérate:Concentration de substance:Temps ponctuel:Sérum/Plasma:Quantitatif:
it-ITItalian (Italy)2-Ossoisovalerato:SCnc:Pt:Siero/Plasma:Qn:
Synonyms: Chimica Concentrazione di Sostanza Plasma Punto nel tempo (episodio) Siero Siero o Plasma
ko-KRKorean (Korea, Republic Of)2-옥소이소발레레이트:물질농도:검사시점:혈청/혈장:정량:
nl-NLDutch (Netherlands)2-oxoisovaleraat:mol/volume:moment:serum of plasma:kwantitatief:
pl-PLPolish (Poland)2-Oksoizowalerian:stężenie molowe:punkt w czasie:surowica lub osocze:ilościowy:
pt-BRPortuguese (Brazil)2-Oxoisovalerato:SCnc:Pt:Sor/Plas:Qn:
Synonyms: ; 2Oxoisovalerate; 2-ketoisovaleric acid; 2-ketoisovalerate; 2-oxoisovaleric acid; Substance concentration; Level; Point in time; Random; SerPl; SerPlas; SerP; Serum; SR; Plasma; Pl; Plsm; Quantitative; QNT; Quant; Quan; II; Chemistry
ru-RURussian (Russian Federation)2-Оксоизовалерат:МолКонц:ТчкВрм:Сыв/Плаз:Колич:
Synonyms: Количественный Молярность;Молярная объёмная концентрация Плазма Сыворотка Сыворотка или Плазма Точка во времени;Момент
tr-TRTurkish (Turkey)2-Okzoizovalerat:SubKons:Zmlı:Ser/Plaz:Kant:
zh-CNChinese (China)2-氧代异戊酸:物质的量浓度:时间点:血清/血浆:定量型:
Synonyms: 2-酮基异戊酸;2-酮异戊酸 Ⅱ II 克分子浓度;克分子浓度(单位体积);摩尔浓度;摩尔浓度(单位体积);物质的量浓度(单位体积) 化学;化学检验项目;化学检验项目类;化学类;化学试验;非刺激耐受型化学检验项目;非刺激耐受型化学检验项目类;非刺激耐受型化学试验;非刺激耐受型化学试验类 可用数量表示的;定量性;数值型;数量型;连续数值型标尺 时刻;随机;随意;瞬间 血清或血浆

Example Units

UnitSource
umol/LExample UCUM Units
mcmol/LREGENSTRIEF

35869-7 2-Oxo,3-Methylvalerate [Moles/volume] in Serum or Plasma

Part Descriptions

LP18407-4   2-Oxo,3-Methylvalerate
3-Methyl-2-oxovaleric acid is a metabolite of isoleucine in man, animals and bacteria. It is the alpha-keto acid analogue of isoleucine. 3-Methyl-2-oxovaleric acid is produced from isoleucine by cytosolic branched chain aminotransferase 1 (EC:2.6.1.42), whereupon it is further degraded by branched chain keto acid dehydrogenase E1 to 2-Methyl-1-hydroxybutyl-ThPP. It is used as a clinical marker for maple syrup urine disease (MSUD). MSUD is caused by a deficiency of the branched-chain -keto acid dehydrogenase compex resulting in an accumulation of branched-chain amino acids and the corresponding -keto-and -hydroxy acids in blood, urine and cerebrospinal fluid causing neurological damage and mental retardation. Copyright Copyright ©2005-2009 Genome Alberta (Reference to original publication: Wishart DS, Knox C, Guo AC, et al. HMDB: a knowledgebase for the human metabolome. Nucleic Acids Res. 2009 37(Database issue):D603-610.) Source: Human Metabolome Database, 2-Oxo,3-Methylvalerate

Fully-Specified Name

Component
2-Oxo,3-Methylvalerate
Property
SCnc
Time
Pt
System
Ser/Plas
Scale
Qn
Method

Basic Attributes

Class
CHEM
Type
Laboratory
First Released
Version 2.13
Last Updated
Version 2.73 (MIN)
Order vs. Observation
Both
Common Test Rank Get Info
9519

Member of these Panels

LOINCLong Common Name
101455-4Mitochondrial metabolites panel - Serum or Plasma
35866-3Organic acids panel - Serum or Plasma

Language Variants Get Info

TagLanguageTranslation
cs-CZCzech (Czechia)2-oxo-3-methylvalerát:Látková koncentrace:Časový bod:Sérum/plazma:Kvantitativní:
el-GRGreek (Greece)3-μεθυλο-2-οξο-βαλερικό οξύ:SCnc:Pt:Ορός/Πλάσμα:Qn:
Synonyms: 3-μεθυλο-2-οξο-βαλερικό οξύ CHEM Pt Qn SCnc Ορός Ορός/Πλάσμα Πλάσμα
es-ARSpanish (Argentina)2-oxo,3-metilvalerato:concentración de sustancia:punto en el tiempo:suero/plasma:cuantitativo:
es-ESSpanish (Spain)2-Oxo,3-Metilvalerato:Concentración de sustancia:Punto temporal:Suero o Plasma:Qn:
Synonyms: Cuantitativo
es-MXSpanish (Mexico)2-oxo, 3-metilvalerato:Concentración de sustancias:Punto temporal:Suero o Plasma:Cuantitativo:
fr-CAFrench (Canada)2-oxo,3-méthylvalérate:Concentration de substance:Temps ponctuel:Sérum/Plasma:Quantitatif:
fr-FRFrench (France)2-oxo-3-méthylvalérate:Moles/Volume:Ponctuel:Sérum/Plasma:Numérique:
fr-BEFrench (Belgium)2-oxo,3-méthylvalérate:Concentration de substance:Temps ponctuel:Sérum/Plasma:Quantitatif:
it-ITItalian (Italy)2-Osso,3-Metilvalerato:SCnc:Pt:Siero/Plasma:Qn:
Synonyms: Chimica Concentrazione di Sostanza Plasma Punto nel tempo (episodio) Siero Siero o Plasma
ko-KRKorean (Korea, Republic Of)2-옥소,3-메틸발레레이트:물질농도:검사시점:혈청/혈장:정량:
nl-NLDutch (Netherlands)2-oxo,3-methylvaleraat:mol/volume:moment:serum of plasma:kwantitatief:
pl-PLPolish (Poland)2-Okso-3-metylwalerian:stężenie molowe:punkt w czasie:surowica lub osocze:ilościowy:
pt-BRPortuguese (Brazil)2-Oxo,3-Metilvalerato:SCnc:Pt:Sor/Plas:Qn:
Synonyms: ; 2Oxo3Me-valerate; 2-keto-3-methylvaleric acid; 2-keto-3-methylvalerate; 2-oxo,3-methylvaleric acid; Substance concentration; Level; Point in time; Random; SerPl; SerPlas; SerP; Serum; SR; Plasma; Pl; Plsm; Quantitative; QNT; Quant; Quan; III; II; Chemistry
ru-RURussian (Russian Federation)2-Оксо,3-Метилвалерат:МолКонц:ТчкВрм:Сыв/Плаз:Колич:
Synonyms: Количественный Молярность;Молярная объёмная концентрация Плазма Сыворотка Сыворотка или Плазма Точка во времени;Момент
tr-TRTurkish (Turkey)2-Okzo,3-Metilvalerat:SubKons:Zmlı:Ser/Plaz:Kant:
zh-CNChinese (China)2-氧代,3-甲基戊酸:物质的量浓度:时间点:血清/血浆:定量型:
Synonyms: 2Oxo3Me-戊酸;2-酮-3-甲基戊酸;2-酮基-3-甲基戊酸 Ⅱ Ⅲ II III 三 克分子浓度;克分子浓度(单位体积);摩尔浓度;摩尔浓度(单位体积);物质的量浓度(单位体积) 化学;化学检验项目;化学检验项目类;化学类;化学试验;非刺激耐受型化学检验项目;非刺激耐受型化学检验项目类;非刺激耐受型化学试验;非刺激耐受型化学试验类 叁 可用数量表示的;定量性;数值型;数量型;连续数值型标尺 时刻;随机;随意;瞬间 血清或血浆

Example Units

UnitSource
umol/LExample UCUM Units
mcmol/LREGENSTRIEF

72450-0 3-Hydroxyisovalerate [Moles/volume] in Serum or Plasma

Part Descriptions

LP15301-2   3-Hydroxyisovalerate
3-Hydroxyisovaleric acid is a normal human metabolite excreted in the urine. Elevated levels of this compound are found in several inherited disorders such as Dihydrolipoamide dehydrogenase Deficiency, 3-Methylcrotonyl-CoA carboxylase 1 deficiency, 3-Hydroxy-3-methylglutaryl-CoA lyase deficiency (3-hydroxy-3-methylglutaryl -CoA lyase Deficiency, Biotinidase deficiency multiple carboxylase deficiency late-onset , Late onset multiple carboxylase deficiency, HolMcarboxylase synthetase deficiency, 3-Methylcrotonyl-CoA carboxylase 2 deficiency. 3-Hydroxyisovaleric acid is also elevated in smokers, in subjects undergoing long-term anticonvulsant therapy with carbamazepine and/or phenytoin. These levels are elevated due to impairment of renal reclamation of biotin. Levels may also be increased from prolonged consumption of raw egg-whites PMID: 16895887, PMID: 9523856, PMID: 15447901, PMID: 9176832, [OMIM: 210210], [OMIM: 253270], [OMIM: 600529], [OMIM: 253260], [OMIM: 246450], [OMIM: 210200], [OMIM: 238331] Copyright Copyright ©2005-2009 Genome Alberta (Reference to original publication: Wishart DS, Knox C, Guo AC, et al. HMDB: a knowledgebase for the human metabolome. Nucleic Acids Res. 2009 37(Database issue):D603-610.) Source: Human Metabolome Database, Human Metabolome Database

Fully-Specified Name

Component
3-Hydroxyisovalerate
Property
SCnc
Time
Pt
System
Ser/Plas
Scale
Qn
Method

Basic Attributes

Class
CHEM
Type
Laboratory
First Released
Version 2.42
Last Updated
Version 2.42 (MIN)
Order vs. Observation
Both

Member of these Panels

LOINCLong Common Name
101455-4Mitochondrial metabolites panel - Serum or Plasma

Language Variants Get Info

TagLanguageTranslation
cs-CZCzech (Czechia)3-hydroxyizovalerát:Látková koncentrace:Časový bod:Sérum/plazma:Kvantitativní:
el-GRGreek (Greece)3-υδροξυϊσοβαλεριανικό:SCnc:Pt:Ορός/Πλάσμα:Qn:
Synonyms: 3-υδροξυϊσοβαλεριανικό CHEM Pt Qn SCnc Ορός Ορός/Πλάσμα Πλάσμα
es-ESSpanish (Spain)3-Hidroxiisovalerato:Concentración de sustancia:Punto temporal:Suero o Plasma:Qn:
Synonyms: Cuantitativo
es-MXSpanish (Mexico)3-hidroxiisovalerato:Concentración de sustancias:Punto temporal:Suero o Plasma:Cuantitativo:
et-EEEstonian (Estonia)3-hüdroksüisovaleraat:SCnc:Pt:S/P:Qn:
Synonyms: Aine kontsentratsioon Juhuslik Kvantitatiivne Plasma Seerum Seerum või plasma
fr-CAFrench (Canada)3-hydroxyisovalérate:Concentration de substance:Temps ponctuel:Sérum/Plasma:Quantitatif:
fr-FRFrench (France)3-hydroxyisovalérate:Moles/Volume:Ponctuel:Sérum/Plasma:Numérique:
fr-BEFrench (Belgium)3-hydroxyisovalérate:Concentration de substance:Temps ponctuel:Sérum/Plasma:Quantitatif:
it-ITItalian (Italy)3-Idrossiisovalerato:SCnc:Pt:Siero/Plasma:Qn:
Synonyms: Chimica Concentrazione di Sostanza Plasma Punto nel tempo (episodio) Siero Siero o Plasma
nl-NLDutch (Netherlands)3-hydroxyisovaleraat:mol/volume:moment:serum of plasma:kwantitatief:
pl-PLPolish (Poland)3-Hydroksyizowalerian:stężenie molowe:punkt w czasie:surowica lub osocze:ilościowy:
ru-RURussian (Russian Federation)3-Гидроксиизовалерат:МолКонц:ТчкВрм:Сыв/Плаз:Колич:
Synonyms: Количественный Молярность;Молярная объёмная концентрация Плазма Сыворотка Сыворотка или Плазма Точка во времени;Момент
tr-TRTurkish (Turkey)3-Hidroksiizovalerat:SubKons:Zmlı:Ser/Plaz:Kant:
zh-CNChinese (China)3-羟基异戊酸:物质的量浓度:时间点:血清/血浆:定量型:
Synonyms: 3-HIA;3OH-异戊酸;3-羟基-异戊酸 Ⅲ III 三 克分子浓度;克分子浓度(单位体积);摩尔浓度;摩尔浓度(单位体积);物质的量浓度(单位体积) 化学;化学检验项目;化学检验项目类;化学类;化学试验;非刺激耐受型化学检验项目;非刺激耐受型化学检验项目类;非刺激耐受型化学试验;非刺激耐受型化学试验类 叁 可用数量表示的;定量性;数值型;数量型;连续数值型标尺 时刻;随机;随意;瞬间 血清或血浆

Example Units

UnitSource
umol/LExample UCUM Units

47536-8 3-Hydroxypropionate (3-OH-C3) [Moles/volume] in Plasma

Part Descriptions

LP18417-3   3-Hydroxypropionate
3-Hydroxypropionic acid is a carboxylic acid, specifically a beta hydroxy acid. It is an acidic viscous liquid with a pKa of 4.5. It is very soluble in water, soluble in ethanol, and miscible with diethyl ether. Upon distillation, it dehydrates to form acrylic acid. Copyright Text is available under the Creative Commons Attribution/Share-Alike License. See http://creativecommons.org/licenses/by-sa/3.0/ for details. Source: Wikipedia, Wikipedia

Fully-Specified Name

Component
3-Hydroxypropionate
Property
SCnc
Time
Pt
System
Plas
Scale
Qn
Method

Basic Attributes

Class
CHEM
Type
Laboratory
First Released
Version 2.21
Last Updated
Version 2.70 (MIN)
Order vs. Observation
Both

Member of these Panels

LOINCLong Common Name
101455-4Mitochondrial metabolites panel - Serum or Plasma

Language Variants Get Info

TagLanguageTranslation
cs-CZCzech (Czechia)3-hydroxypropionát (3-OH-C3):Látková koncentrace:Časový bod:Plazma:Kvantitativní:
el-GRGreek (Greece)3-υδροξυπροπιονικό:SCnc:Pt:Πλάσμα:Qn:
Synonyms: 3-υδροξυπροπιονικό CHEM Pt Qn SCnc Πλάσμα
es-ESSpanish (Spain)3-Hidroxipropionato:Concentración de sustancia:Punto temporal:Plasma:Qn:
Synonyms: Cuantitativo
es-MXSpanish (Mexico)3-hidroxipropionato:Concentración de sustancias:Punto temporal:Plasma:Cuantitativo:
et-EEEstonian (Estonia)3-hüdroksüpropionaat:SCnc:Pt:P:Qn:
Synonyms: Aine kontsentratsioon Juhuslik Kvantitatiivne Plasma
fr-CAFrench (Canada)3-hydroxypropionate, 3-OH-C3:Concentration de substance:Temps ponctuel:Plasma:Quantitatif:
fr-FRFrench (France)3-hydroxypropionate:Moles/Volume:Ponctuel:Plasma:Numérique:
fr-BEFrench (Belgium)3-hydroxypropionate, 3-OH-C3:Concentration de substance:Temps ponctuel:Plasma:Quantitatif:
it-ITItalian (Italy)3-Idrossipropionato:SCnc:Pt:Plasma:Qn:
Synonyms: 3-Idrossipropionato (3-OH-C3) Chimica Concentrazione di Sostanza Plasma Punto nel tempo (episodio)
nl-NLDutch (Netherlands)3-hydroxypropionaat:mol/volume:moment:plasma:kwantitatief:
pl-PLPolish (Poland)3-hydroksypropionian:stężenie molowe:punkt w czasie:osocze:ilościowy:
pt-BRPortuguese (Brazil)3-Hidroxipropionato:SCnc:Pt:Plasma:Qn:
Synonyms: ; 3OH-Propionate; 3-hydroxy-propionate; 3-hydroxypropionic acid; Substance concentration; Level; Point in time; Random; Plasma; Pl; Plsm; Quantitative; QNT; Quant; Quan; III; Chemistry
ru-RURussian (Russian Federation)3-Гидроксипропионат:МолКонц:ТчкВрм:Плаз:Колич:
Synonyms: Количественный Молярность;Молярная объёмная концентрация Плазма Точка во времени;Момент
tr-TRTurkish (Turkey)3-Hidroksipropiyonat:SubKons:Zmlı:Plaz:Kant:
zh-CNChinese (China)3-羟基丙酸:物质的量浓度:时间点:血浆:定量型:
Synonyms: 3OH-Propionate;3OH-羟基丙酸;3-羟-丙酸;3-羟基-丙酸;3-羟基丙酸, 3-OH-C3 Ⅲ III 三 克分子浓度;克分子浓度(单位体积);摩尔浓度;摩尔浓度(单位体积);物质的量浓度(单位体积) 化学;化学检验项目;化学检验项目类;化学类;化学试验;非刺激耐受型化学检验项目;非刺激耐受型化学检验项目类;非刺激耐受型化学试验;非刺激耐受型化学试验类 叁 可用数量表示的;定量性;数值型;数量型;连续数值型标尺 时刻;随机;随意;瞬间

Example Units

UnitSource
umol/LExample UCUM Units

69789-6 2-methyl-3-hydroxybutyrate (C5-OH) [Moles/volume] in Serum or Plasma

Part Descriptions

LP18406-6   2-Methyl-3-Hydroxybutyrate
2-Methyl,3-Hydroxybutyric acid (HMBA) is involved in isoleucine catabolism and beta-oxidation of fatty acids and ketogenesis. HMBA is excreted in abnormally high amounts in beta-ketothiolase deficiency. PMID: 10755375 Source: Regenstrief LOINC, PMID: 10755375

Fully-Specified Name

Component
2-Methyl-3-Hydroxybutyrate
Property
SCnc
Time
Pt
System
Ser/Plas
Scale
Qn
Method

Basic Attributes

Class
CHEM
Type
Laboratory
First Released
Version 2.40
Last Updated
Version 2.70 (MIN)
Change Reason
Corrected typo by replacing comma between 'methyl' and '3' with a dash.
Order vs. Observation
Both

Member of these Panels

LOINCLong Common Name
101455-4Mitochondrial metabolites panel - Serum or Plasma

Language Variants Get Info

TagLanguageTranslation
cs-CZCzech (Czechia)2-methyl-3-hydroxybutyrát (C5-OH):Látková koncentrace:Časový bod:Sérum/plazma:Kvantitativní:
el-GRGreek (Greece)2-μεθυλ-3-υδροξυβουτυρικό:SCnc:Pt:Ορός/Πλάσμα:Qn:
Synonyms: 2-μεθυλ-3-υδροξυβουτυρικό CHEM Pt Qn SCnc Ορός Ορός/Πλάσμα Πλάσμα
es-ESSpanish (Spain)2-Metil-3-Hidroxibutirato:Concentración de sustancia:Punto temporal:Suero o Plasma:Qn:
Synonyms: Cuantitativo
es-MXSpanish (Mexico)2-metil-3-hidroxibutirato:Concentración de sustancias:Punto temporal:Suero o Plasma:Cuantitativo:
fr-CAFrench (Canada)2-méthyl-3-hydroxybutyrate:Concentration de substance:Temps ponctuel:Sérum/Plasma:Quantitatif:
fr-FRFrench (France)2-méthyl-3-hydroxybutyrate:Moles/Volume:Ponctuel:Sérum/Plasma:Numérique:
fr-BEFrench (Belgium)2-méthyl,3-hydroxybutyrate:Concentration de substance:Temps ponctuel:Sérum/Plasma:Quantitatif:
it-ITItalian (Italy)2-Metil-3-Idrossibutirrato,2-metil,3-idrossibutirrato (C5-OH):SCnc:Pt:Siero/Plasma:Qn:
Synonyms: Chimica Concentrazione di Sostanza Plasma Punto nel tempo (episodio) Siero Siero o Plasma
nl-NLDutch (Netherlands)2-methyl,3-hydroxybutyraat:mol/volume:moment:serum of plasma:kwantitatief:
pl-PLPolish (Poland)2-Metylo-3-Hydroksymaślan:stężenie molowe:punkt w czasie:surowica lub osocze:ilościowy:
ru-RURussian (Russian Federation)2-Метил,3-Гидроксибутират:МолКонц:ТчкВрм:Сыв/Плаз:Колич:
Synonyms: Количественный Молярность;Молярная объёмная концентрация Плазма Сыворотка Сыворотка или Плазма Точка во времени;Момент
tr-TRTurkish (Turkey)2-Metil,3-Hidroksibütirat:SubKons:Zmlı:Ser/Plaz:Kant:
zh-CNChinese (China)2-甲基-3-羟基丁酸:物质的量浓度:时间点:血清/血浆:定量型:
Synonyms: 2Me3OH-丁酸;2-甲基,3-羟基丁酸;2-甲基-3-羟丁酸 Ⅱ Ⅲ II III 三 克分子浓度;克分子浓度(单位体积);摩尔浓度;摩尔浓度(单位体积);物质的量浓度(单位体积) 化学;化学检验项目;化学检验项目类;化学类;化学试验;非刺激耐受型化学检验项目;非刺激耐受型化学检验项目类;非刺激耐受型化学试验;非刺激耐受型化学试验类 叁 可用数量表示的;定量性;数值型;数量型;连续数值型标尺 时刻;随机;随意;瞬间 羟丁酸 血清或血浆

Example Units

UnitSource
umol/LExample UCUM Units

75083-6 Aconitate [Moles/volume] in Serum or Plasma

Part Descriptions

LP18428-0   Aconitate
Aconitic acid is an organic acid. The two isomers are cis-aconitic acid and trans-aconitic acid. The conjugate base of cis-aconitic acid, cis-aconitate is an intermediate in the isomerization of citrate to isocitrate in the citric acid cycle. It is acted upon by the enzyme aconitase. Copyright Text is available under the Creative Commons Attribution/Share-Alike License. See http://creativecommons.org/licenses/by-sa/3.0/ for details. Source: Wikipedia, Wikipedia

Fully-Specified Name

Component
Aconitate
Property
SCnc
Time
Pt
System
Ser/Plas
Scale
Qn
Method

Basic Attributes

Class
CHEM
Type
Laboratory
First Released
Version 2.48
Last Updated
Version 2.52 (MIN)
Order vs. Observation
Both

Member of these Panels

LOINCLong Common Name
101455-4Mitochondrial metabolites panel - Serum or Plasma

Language Variants Get Info

TagLanguageTranslation
cs-CZCzech (Czechia)Akonitát:Látková koncentrace:Časový bod:Sérum/plazma:Kvantitativní:
el-GRGreek (Greece)Ακονιτικό οξύ:SCnc:Pt:Ορός/Πλάσμα:Qn:
Synonyms: CHEM Pt Qn SCnc Ακονιτικό οξύ Ορός Ορός/Πλάσμα Πλάσμα
es-MXSpanish (Mexico)Aconitate:Concentración de sustancias:Punto temporal:Suero o Plasma:Cuantitativo:
es-ESSpanish (Spain)Aconitato:Concentración de sustancia:Punto temporal:Suero o Plasma:Qn:
Synonyms: Cuantitativo
et-EEEstonian (Estonia)Akonitaat:SCnc:Pt:S/P:Qn:
Synonyms: Aine kontsentratsioon Juhuslik Kvantitatiivne Plasma Seerum Seerum või plasma
fr-CAFrench (Canada)Aconitate:Concentration de substance:Temps ponctuel:Sérum/Plasma:Quantitatif:
fr-FRFrench (France)Aconitate:Moles/Volume:Ponctuel:Sérum/Plasma:Numérique:
fr-BEFrench (Belgium)Aconitate:Concentration de substance:Temps ponctuel:Sérum/Plasma:Quantitatif:
it-ITItalian (Italy)Aconitato:SCnc:Pt:Siero/Plasma:Qn:
Synonyms: Chimica Concentrazione di Sostanza Plasma Punto nel tempo (episodio) Siero Siero o Plasma
nl-NLDutch (Netherlands)aconitaat:mol/volume:moment:serum of plasma:kwantitatief:
pl-PLPolish (Poland)Akonitan:stężenie molowe:punkt w czasie:surowica lub osocze:ilościowy:
Synonyms: Kwas akonitowy
ru-RURussian (Russian Federation)Аконитат:МолКонц:ТчкВрм:Сыв/Плаз:Колич:
Synonyms: Количественный Молярность;Молярная объёмная концентрация Плазма Сыворотка Сыворотка или Плазма Точка во времени;Момент
tr-TRTurkish (Turkey)Akonitat:SubKons:Zmlı:Ser/Plaz:Kant:
zh-CNChinese (China)乌头酸:物质的量浓度:时间点:血清/血浆:定量型:
Synonyms: 1-丙烯-1,2,3-三羧酸;乌头酸根;乌头酸盐;乌头酸酯 克分子浓度;克分子浓度(单位体积);摩尔浓度;摩尔浓度(单位体积);物质的量浓度(单位体积) 化学;化学检验项目;化学检验项目类;化学类;化学试验;非刺激耐受型化学检验项目;非刺激耐受型化学检验项目类;非刺激耐受型化学试验;非刺激耐受型化学试验类 可用数量表示的;定量性;数值型;数量型;连续数值型标尺 时刻;随机;随意;瞬间 血清或血浆

Example Units

UnitSource
nmol/LExample UCUM Units

35867-1 Acetoacetate [Moles/volume] in Serum or Plasma

Part Descriptions

LP15312-9   Acetoacetate
Acetoacetic acid (also known as 3-oxobutanoic acid or diacetic acid) is a beta-keto acid of the keto acid group. It is a weak organic acid produced in the liver under conditions of poor metabolism leading to excessive fatty acid breakdown. Increased levels are seen with gluconeogenesis, PHD complex deficiency, respiratory chain defects, IVA,PA, MMA, multiple carboxylase deficiency,3-methylcrotonyl-CoA carboxylase deficiency, glyceroluria, MSUD, GA I, MAD deficiency,Beta-ketothiolase deficiencies,2-amino/2-ketoadipic acidemia, mitochondrial SCHAD, and fatty acids oxidation deficiency. Source: Regenstrief Institute, PMID:11978597

Fully-Specified Name

Component
Acetoacetate
Property
SCnc
Time
Pt
System
Ser/Plas
Scale
Qn
Method

Basic Attributes

Class
CHEM
Type
Laboratory
First Released
Version 2.13
Last Updated
Version 2.73 (MIN)
Order vs. Observation
Both
Common Test Rank Get Info
9517

Member of these Panels

LOINCLong Common Name
101455-4Mitochondrial metabolites panel - Serum or Plasma
35866-3Organic acids panel - Serum or Plasma

Member of these Groups Get Info

LOINC GroupGroup Name
LG42455-2Acetoacetate|Pt|Ser/Plas|101.081 g/mole
LG14820-1Acetoacetate|SCnc|Pt|ANYBldSerPl

Language Variants Get Info

TagLanguageTranslation
cs-CZCzech (Czechia)Acetoacetát:Látková koncentrace:Časový bod:Sérum/plazma:Kvantitativní:
de-ATGerman (Austria)Synonyms: Acetoacetat
de-DEGerman (Germany)Acetoacetat:Stoffmengenkonzentration:Zeitpunkt:Serum oder Plasma:Quantitativ:
el-GRGreek (Greece)Ακετοξικό:SCnc:Pt:Ορός/Πλάσμα:Qn:
Synonyms: CHEM Pt Qn SCnc Ακετοξικό Ορός Ορός/Πλάσμα Πλάσμα
es-ARSpanish (Argentina)acetoacetato:concentración de sustancia:punto en el tiempo:suero/plasma:cuantitativo:
es-ESSpanish (Spain)Acetoacetato:Concentración de sustancia:Punto temporal:Suero o Plasma:Qn:
Synonyms: Cuantitativo
es-MXSpanish (Mexico)Acetoacetato:Concentración de sustancias:Punto temporal:Suero o Plasma:Cuantitativo:
et-EEEstonian (Estonia)Atseetoatsetaat:SCnc:Pt:S/P:Qn:
Synonyms: Aine kontsentratsioon Juhuslik Kvantitatiivne Plasma Seerum Seerum või plasma
fr-CAFrench (Canada)Acétoacétate:Concentration de substance:Temps ponctuel:Sérum/Plasma:Quantitatif:
fr-FRFrench (France)Acétoacétate:Moles/Volume:Ponctuel:Sérum/Plasma:Numérique:
fr-BEFrench (Belgium)Acétoacétate:Concentration de substance:Temps ponctuel:Sérum/Plasma:Quantitatif:
it-ITItalian (Italy)Acetoacetato:SCnc:Pt:Siero/Plasma:Qn:
Synonyms: Chimica Concentrazione di Sostanza Plasma Punto nel tempo (episodio) Siero Siero o Plasma
ko-KRKorean (Korea, Republic Of)아세토아세트산:물질농도:검사시점:혈청/혈장:정량:
nl-NLDutch (Netherlands)acetoacetaat:mol/volume:moment:serum of plasma:kwantitatief:
pl-PLPolish (Poland)Acetooctan:stężenie molowe:punkt w czasie:surowica lub osocze:ilościowy:
pt-BRPortuguese (Brazil)Acetoacetato:SCnc:Pt:Sor/Plas:Qn:
Synonyms: ; Acetoacet; AcAc; 3-ketobutyrate; 3-oxobutyric acid; oxobutyrate; Acetoacetic acid; Beta-ketobutyrate; Acetoacetates; Substance concentration; Level; Point in time; Random; SerPl; SerPlas; SerP; Serum; SR; Plasma; Pl; Plsm; Quantitative; QNT; Quant; Quan; Chemistry
ru-RURussian (Russian Federation)Ацетоацетат:МолКонц:ТчкВрм:Сыв/Плаз:Колич:
Synonyms: Количественный Молярность;Молярная объёмная концентрация Плазма Сыворотка Сыворотка или Плазма Точка во времени;Момент
tr-TRTurkish (Turkey)Asetoasetat:SubKons:Zmlı:Ser/Plaz:Kant:
zh-CNChinese (China)乙酰乙酸:物质的量浓度:时间点:血清/血浆:定量型:
Synonyms: 3-氧代丁酸;3-酮丁酸;AcAc;Beta-酮丁酸;β-酮丁酸;乙酰乙酸盐;氧代丁酸 克分子浓度;克分子浓度(单位体积);摩尔浓度;摩尔浓度(单位体积);物质的量浓度(单位体积) 化学;化学检验项目;化学检验项目类;化学类;化学试验;非刺激耐受型化学检验项目;非刺激耐受型化学检验项目类;非刺激耐受型化学试验;非刺激耐受型化学试验类 可用数量表示的;定量性;数值型;数量型;连续数值型标尺 时刻;随机;随意;瞬间 血清或血浆

Example Units

UnitSource
umol/LExample UCUM Units
mcmol/LREGENSTRIEF

69803-5 Alpha ketoglutarate [Moles/volume] in Serum or Plasma

Part Descriptions

LP15365-7   Alpha ketoglutarate
2-Ketoglutaric acid (alpha ketoglutarate) is an important nitrogen transporter and a key intermediate in the Krebs cycle.Amino groups of amino acids are attached to it by transamination and carried to the liver where the urea cycle takes place. Increased levels found with 2-ketoglutaric DH deficiency, GA I, 2-amino/2-ketoadipate acidemia, dihdrolipoyl DH(E3) deficiency, glycogen storage disorders I, 2-hydroxyglutaric aciduria(D-form), and fumarase deficiency. Very low values are sometimes encountered in chronic fatigue syndrome.(Information from: Kumps A, Duez P, Mardens Y. Metabolic, Nutritional, Iatrogenic, and Artifactual Sources of Urinary Organic Acids: A Comprehensive Table. Clinical Chemistry 2002, 48:708-717.) Source: Regenstrief Institute

Fully-Specified Name

Component
Alpha ketoglutarate
Property
SCnc
Time
Pt
System
Ser/Plas
Scale
Qn
Method

Basic Attributes

Class
CHEM
Type
Laboratory
First Released
Version 2.40
Last Updated
Version 2.70 (MIN)
Order vs. Observation
Both

Member of these Panels

LOINCLong Common Name
101455-4Mitochondrial metabolites panel - Serum or Plasma

Member of these Groups Get Info

LOINC GroupGroup Name
LG42401-6Alpha ketoglutarate|Pt|Ser/Plas

Language Variants Get Info

TagLanguageTranslation
cs-CZCzech (Czechia)Alfa-ketoglutarát:Látková koncentrace:Časový bod:Sérum/plazma:Kvantitativní:
el-GRGreek (Greece)Άλφα κετογλουταρικό:SCnc:Pt:Ορός/Πλάσμα:Qn:
Synonyms: CHEM Pt Qn SCnc Άλφα κετογλουταρικό Ορός Ορός/Πλάσμα Πλάσμα
es-ESSpanish (Spain)Alfa Cetoglutarato:Concentración de sustancia:Punto temporal:Suero o Plasma:Qn:
Synonyms: Cuantitativo
es-MXSpanish (Mexico)Cetoglutarato alfa:Concentración de sustancias:Punto temporal:Suero o Plasma:Cuantitativo:
et-EEEstonian (Estonia)Alfaketoglutaraat:SCnc:Pt:S/P:Qn:
Synonyms: Aine kontsentratsioon Juhuslik Kvantitatiivne Plasma Seerum Seerum või plasma
fr-CAFrench (Canada)Alpha-ketoglutarate:Concentration de substance:Temps ponctuel:Sérum/Plasma:Quantitatif:
fr-FRFrench (France)2-cétoglutarate:Moles/Volume:Ponctuel:Sérum/Plasma:Numérique:
fr-BEFrench (Belgium)Alpha-kétoglutarate:Concentration de substance:Temps ponctuel:Sérum/Plasma:Quantitatif:
Synonyms: Alpha-cétoglutarate
it-ITItalian (Italy)Alfa chetoglutarato:SCnc:Pt:Siero/Plasma:Qn:
Synonyms: Chimica Concentrazione di Sostanza Plasma Punto nel tempo (episodio) Siero Siero o Plasma
nl-NLDutch (Netherlands)alfa-ketoglutaraat:mol/volume:moment:serum of plasma:kwantitatief:
pl-PLPolish (Poland)Alfa ketoglutaran:stężenie molowe:punkt w czasie:surowica lub osocze:ilościowy:
Synonyms: Alfa-ketoglutaran
ru-RURussian (Russian Federation)Альфа кетоглутарат:МолКонц:ТчкВрм:Сыв/Плаз:Колич:
Synonyms: Альфа-кетоглутарат Количественный Молярность;Молярная объёмная концентрация Плазма Сыворотка Сыворотка или Плазма Точка во времени;Момент
tr-TRTurkish (Turkey)Alfa ketoglutarat:SubKons:Zmlı:Ser/Plaz:Kant:
zh-CNChinese (China)Alpha 酮戊二酸:物质的量浓度:时间点:血清/血浆:定量型:
Synonyms: 2-酮戊二酸;2-酮戊二酸根;2-酮戊二酸盐;2-酮戊二酸酯;A-Ketoglut;AKG;Alpha 酮戊二酸根;Alpha 酮戊二酸盐;Alpha 酮戊二酸酯;Alpha-酮戊二酸;Alpha-酮戊二酸根;Alpha-酮戊二酸盐;Alpha-酮戊二酸酯;A-酮戊二酸;A-酮戊二酸根;A-酮戊二酸盐;A-酮戊二酸酯;α酮戊二酸;α-酮戊二酸;α酮戊二酸根;α-酮戊二酸根;α酮戊二酸盐;α-酮戊二酸盐;α酮戊二酸酯;α-酮戊二酸酯 α 克分子浓度;克分子浓度(单位体积);摩尔浓度;摩尔浓度(单位体积);物质的量浓度(单位体积) 化学;化学检验项目;化学检验项目类;化学类;化学试验;非刺激耐受型化学检验项目;非刺激耐受型化学检验项目类;非刺激耐受型化学试验;非刺激耐受型化学试验类 可用数量表示的;定量性;数值型;数量型;连续数值型标尺 时刻;随机;随意;瞬间 血清或血浆 阿尔法

Example Units

UnitSource
umol/LExample UCUM Units

69843-1 Alpha hydroxybutyrate [Moles/volume] in Serum or Plasma

Fully-Specified Name

Component
Alpha hydroxybutyrate
Property
SCnc
Time
Pt
System
Ser/Plas
Scale
Qn
Method

Basic Attributes

Class
CHEM
Type
Laboratory
First Released
Version 2.40
Last Updated
Version 2.70 (MIN)
Order vs. Observation
Both

Member of these Panels

LOINCLong Common Name
101455-4Mitochondrial metabolites panel - Serum or Plasma

Language Variants Get Info

TagLanguageTranslation
cs-CZCzech (Czechia)Alfa-hydroxybutyrát:Látková koncentrace:Časový bod:Sérum/plazma:Kvantitativní:
el-GRGreek (Greece)α-υδροξυβουτυρικό:SCnc:Pt:Ορός/Πλάσμα:Qn:
Synonyms: CHEM Pt Qn SCnc α-υδροξυβουτυρικό Ορός Ορός/Πλάσμα Πλάσμα
es-ESSpanish (Spain)Alfa Hidroxibutirato:Concentración de sustancia:Punto temporal:Suero o Plasma:Qn:
Synonyms: Cuantitativo
es-MXSpanish (Mexico)Alfa hidroxibutirato:Concentración de sustancias:Punto temporal:Suero o Plasma:Cuantitativo:
et-EEEstonian (Estonia)Alfahüdroksübutüraat:SCnc:Pt:S/P:Qn:
Synonyms: Aine kontsentratsioon Juhuslik Kvantitatiivne Plasma Seerum Seerum või plasma
fr-CAFrench (Canada)Hydroxybutyrate alpha:Concentration de substance:Temps ponctuel:Sérum/Plasma:Quantitatif:
fr-FRFrench (France)2-hydroxybutyrate:Moles/Volume:Ponctuel:Sérum/Plasma:Numérique:
fr-BEFrench (Belgium)Hydroxybutyrate alpha:Concentration de substance:Temps ponctuel:Sérum/Plasma:Quantitatif:
it-ITItalian (Italy)Alfa idrossibutirrato:SCnc:Pt:Siero/Plasma:Qn:
Synonyms: Chimica Concentrazione di Sostanza Plasma Punto nel tempo (episodio) Siero Siero o Plasma
nl-NLDutch (Netherlands)alfa-hydroxybutyraat:mol/volume:moment:serum of plasma:kwantitatief:
pl-PLPolish (Poland)Alfa hydroksymaślan:stężenie molowe:punkt w czasie:surowica lub osocze:ilościowy:
ru-RURussian (Russian Federation)Альфа гидроксибутират:МолКонц:ТчкВрм:Сыв/Плаз:Колич:
Synonyms: Альфа-гидроксибутират Количественный Молярность;Молярная объёмная концентрация Плазма Сыворотка Сыворотка или Плазма Точка во времени;Момент
tr-TRTurkish (Turkey)Alfa hidroksibütirat:SubKons:Zmlı:Ser/Plaz:Kant:
zh-CNChinese (China)Alpha 羟基丁酸:物质的量浓度:时间点:血清/血浆:定量型:
Synonyms: 2OH-丁酸;2-羟基丁酸;Alpha-OH-丁酸;Alpha-羟基丁酸;A-OH-丁酸;α 羟基丁酸;α-OH-丁酸;α-羟基丁酸 α 克分子浓度;克分子浓度(单位体积);摩尔浓度;摩尔浓度(单位体积);物质的量浓度(单位体积) 化学;化学检验项目;化学检验项目类;化学类;化学试验;非刺激耐受型化学检验项目;非刺激耐受型化学检验项目类;非刺激耐受型化学试验;非刺激耐受型化学试验类 可用数量表示的;定量性;数值型;数量型;连续数值型标尺 时刻;随机;随意;瞬间 羟丁酸 血清或血浆 阿尔法

Example Units

UnitSource
umol/LExample UCUM Units

6873-4 Beta hydroxybutyrate [Moles/volume] in Serum or Plasma

Part Descriptions

LP15436-6   Beta hydroxybutyrate
Increases in beta-hydroxybutyrate are due to excessive fatty acid oxidation. Elevated levels are seen in gluconeogenesis, PHD complex deficiency, respiratory chain defects, IVA, PA, MMA, multiple carboxylase deficiency, 3-methylcrotonyl-CoA carboxylase deficiency, glyceroluria, MSUD, GA I, MAD deficiency, Beta-ketothiolase deficiencies, 2-amino/2-ketoadipic acidemia,mitochondrial SCHAD,and fatty acids oxidation deficiency. (Kumps A, Duez P, Mardens Y. Metabolic, Nutritional, Iatrogenic, and Artifactual Sources of Urinary Organic Acids: A Comprehensive Table. Clinical Chemistry 2002, 48:708-717.) Source: Regenstrief Institute

Fully-Specified Name

Component
Beta hydroxybutyrate
Property
SCnc
Time
Pt
System
Ser/Plas
Scale
Qn
Method

Basic Attributes

Class
CHEM
Type
Laboratory
First Released
Version 1.0h(2)
Last Updated
Version 2.73 (MIN)
Order vs. Observation
Both
Common Test Rank Get Info
1063

Member of these Panels

LOINCLong Common Name
101629-4Hypoglycemia evaluation panel - Serum or Plasma
101455-4Mitochondrial metabolites panel - Serum or Plasma
35866-3Organic acids panel - Serum or Plasma

Member of these Groups Get Info

LOINC GroupGroup Name
LG43202-7Beta hydroxybutyrate|Pt|Ser/Plas
LG26613-6Beta hydroxybutyrate|SCnc|Pt|ANYBldSerPl

Language Variants Get Info

TagLanguageTranslation
cs-CZCzech (Czechia)Beta-hydroxybutyrát:Látková koncentrace:Časový bod:Sérum/plazma:Kvantitativní:
de-ATGerman (Austria)Synonyms: Beta-Hydroxybutyrat
de-DEGerman (Germany)Beta-Hydroxybutyrat:Stoffmengenkonzentration:Zeitpunkt:Serum oder Plasma:Quantitativ:
el-GRGreek (Greece)β-υδροξυβουτυρικό:SCnc:Pt:Ορός/Πλάσμα:Qn:
Synonyms: CHEM Pt Qn SCnc β-υδροξυβουτυρικό Ορός Ορός/Πλάσμα Πλάσμα
es-ARSpanish (Argentina)beta hidroxibutirato:concentración de sustancia:punto en el tiempo:suero/plasma:cuantitativo:
es-ESSpanish (Spain)Beta Hidroxibutirato:Concentración de sustancia:Punto temporal:Suero o Plasma:Qn:
Synonyms: Cuantitativo
es-MXSpanish (Mexico)Beta hidroxibutirato:Concentración de sustancias:Punto temporal:Suero o Plasma:Cuantitativo:
et-EEEstonian (Estonia)Beetahüdroksübutüraat:SCnc:Pt:S/P:Qn:
Synonyms: Aine kontsentratsioon Juhuslik Kvantitatiivne Plasma Seerum Seerum või plasma
fr-CAFrench (Canada)Bêta-hydroxybutyrate:Concentration de substance:Temps ponctuel:Sérum/Plasma:Quantitatif:
fr-FRFrench (France)Bêta hydroxybutyrate:Moles/Volume:Ponctuel:Sérum/Plasma:Numérique:
fr-BEFrench (Belgium)Béta-hydroxybutyrate:Concentration de substance:Temps ponctuel:Sérum/Plasma:Quantitatif:
it-ITItalian (Italy)Beta idrossibutirrato:SCnc:Pt:Siero/Plasma:Qn:
Synonyms: Chimica Concentrazione di Sostanza Plasma Punto nel tempo (episodio) Siero Siero o Plasma
ko-KRKorean (Korea, Republic Of)베타 수산화부티레이트:물질농도:검사시점:혈청/혈장:정량:
nl-NLDutch (Netherlands)bèta-hydroxybutyraat:mol/volume:moment:serum of plasma:kwantitatief:
pl-PLPolish (Poland)Beta hydroksymaślan:stężenie molowe:punkt w czasie:surowica lub osocze:ilościowy:
pt-BRPortuguese (Brazil)Beta Hidroxibutirato:SCnc:Pt:Sor/Plas:Qn:
Synonyms: ; B-OH-Butyr; 3-hydroxybutyrate; BOHB; Betahydroxybutyrate; Betahydroxybutyric acid; Beta hydroxybutyric acid; 3-hydroxybutyric acid; Substance concentration; Level; Point in time; Random; SerPl; SerPlas; SerP; Serum; SR; Plasma; Pl; Plsm; Quantitative; QNT; Quant; Quan; Hydroxybutyric acid; B; Chemistry
ru-RURussian (Russian Federation)Бета гидроксибутират:МолКонц:ТчкВрм:Сыв/Плаз:Колич:
Synonyms: Количественный Молярность;Молярная объёмная концентрация Плазма Сыворотка Сыворотка или Плазма Точка во времени;Момент
tr-TRTurkish (Turkey)Beta Hidroksibütirat:SubKons:Zmlı:Ser/Plaz:Kant:
uk-UAUkrainian (Ukraine)Бета гідроксибутират:Молярна Концентрація:МоментЧасу:Сироватка/Плазма:Кількісно:
Synonyms: 3-hydroxybutyrate; 3-hydroxybutyric acid; B; Beta hydroxy butyrate; Beta hydroxybutyric acid; Betahydroxybutyrate; Betahydroxybutyric acid; BHB; BOHB; B-OH-Butyr; Chemistry; Hydroxybutyric acid; Level; Pl; Plasma; Plsm; Point in time; QNT; Quan; Quant; Quantitative; Random; SerP; SerPl; SerPlas; Serum; Serum or plasma; SR; Substance concentration; UniversalLabOrders
zh-CNChinese (China)Beta 羟基丁酸:物质的量浓度:时间点:血清/血浆:定量型:
Synonyms: 3-羟基丁酸;Beta-羟基丁酸;BOHB;B-OH-丁酸;β羟基丁酸;β-羟基丁酸 B β 克分子浓度;克分子浓度(单位体积);摩尔浓度;摩尔浓度(单位体积);物质的量浓度(单位体积) 化学;化学检验项目;化学检验项目类;化学类;化学试验;非刺激耐受型化学检验项目;非刺激耐受型化学检验项目类;非刺激耐受型化学试验;非刺激耐受型化学试验类 可用数量表示的;定量性;数值型;数量型;连续数值型标尺 时刻;随机;随意;瞬间 羟丁酸 血清或血浆 贝塔

Example Units

UnitSource
mmol/LExample UCUM Units
mmol/LREGENSTRIEF

75081-0 Fumarate [Moles/volume] in Serum or Plasma

Part Descriptions

LP15583-5   Fumarate
Fumaric acid is produced by the dehydrogenation of succinic acid by the enzyme succinic acid dehydrogenase in the Krebs cycle. Elevations noted in patients with fumarase deficiency. Source: Regenstrief Institute

Fully-Specified Name

Component
Fumarate
Property
SCnc
Time
Pt
System
Ser/Plas
Scale
Qn
Method

Basic Attributes

Class
CHEM
Type
Laboratory
First Released
Version 2.48
Last Updated
Version 2.67 (MIN)
Order vs. Observation
Both

Member of these Panels

LOINCLong Common Name
101455-4Mitochondrial metabolites panel - Serum or Plasma

Language Variants Get Info

TagLanguageTranslation
cs-CZCzech (Czechia)Fumarát:Látková koncentrace:Časový bod:Sérum/plazma:Kvantitativní:
el-GRGreek (Greece)Φουμαρικό:SCnc:Pt:Ορός/Πλάσμα:Qn:
Synonyms: CHEM Pt Qn SCnc Ορός Ορός/Πλάσμα Πλάσμα Φουμαρικό
es-MXSpanish (Mexico)Fumarato:Concentración de sustancias:Punto temporal:Suero o Plasma:Cuantitativo:
es-ESSpanish (Spain)Fumarato:Concentración de sustancia:Punto temporal:Suero o Plasma:Qn:
Synonyms: Cuantitativo
et-EEEstonian (Estonia)Fumaraat:SCnc:Pt:S/P:Qn:
Synonyms: Aine kontsentratsioon Juhuslik Kvantitatiivne Plasma Seerum Seerum või plasma
fr-CAFrench (Canada)Fumarate:Concentration de substance:Temps ponctuel:Sérum/Plasma:Quantitatif:
fr-FRFrench (France)Fumarate:Moles/Volume:Ponctuel:Sérum/Plasma:Numérique:
fr-BEFrench (Belgium)Fumarate:Concentration de substance:Temps ponctuel:Sérum/Plasma:Quantitatif:
it-ITItalian (Italy)Fumarato:SCnc:Pt:Siero/Plasma:Qn:
Synonyms: Chimica Concentrazione di Sostanza Plasma Punto nel tempo (episodio) Siero Siero o Plasma
nl-NLDutch (Netherlands)fumaraat:mol/volume:moment:serum of plasma:kwantitatief:
pl-PLPolish (Poland)Kwas fumarowy:stężenie molowe:punkt w czasie:surowica lub osocze:ilościowy:
ru-RURussian (Russian Federation)Фумарат:МолКонц:ТчкВрм:Сыв/Плаз:Колич:
Synonyms: Количественный Молярность;Молярная объёмная концентрация Плазма Сыворотка Сыворотка или Плазма Точка во времени;Момент
tr-TRTurkish (Turkey)Fumarat:SubKons:Zmlı:Ser/Plaz:Kant:
zh-CNChinese (China)延胡索酸:物质的量浓度:时间点:血清/血浆:定量型:
Synonyms: 克分子浓度;克分子浓度(单位体积);摩尔浓度;摩尔浓度(单位体积);物质的量浓度(单位体积) 化学;化学检验项目;化学检验项目类;化学类;化学试验;非刺激耐受型化学检验项目;非刺激耐受型化学检验项目类;非刺激耐受型化学试验;非刺激耐受型化学试验类 反丁烯二酸根;反丁烯二酸酯;反式丁烯二酸;富马酸 可用数量表示的;定量性;数值型;数量型;连续数值型标尺 时刻;随机;随意;瞬间 血清或血浆

Example Units

UnitSource
umol/LExample UCUM Units

15038-3 Citrate [Moles/volume] in Serum or Plasma

Part Descriptions

LP14741-0   Citrate
A citrate is an ionic form of citric acid, such as C3 H5 O(COO)3 3ˆ', that is, citric acid minus three hydrogen ions. Citrates are compounds containing this group, either ionic compounds, the salts, or analogous covalent compounds, esters. An example of a salt is sodium citrate and an ester is trimethyl citrate. Because citric acid is a multifunctional acid, several intermediate ions exist: hydrogen citrate ion, HC6 H5 O7 2ˆ' and dihydrogen citrate ion, H2 C6 H5 O7 ˆ'. These may form salts as well, called acid salts. Salts of the hydrogen citrate ions are weakly acidic, whereas salts of the citrate ion itself (with an inert cation such as sodium ion) are weakly basic. Copyright Text is available under the Creative Commons Attribution/Share-Alike License. See http://creativecommons.org/licenses/by-sa/3.0/ for details. Source: Wikipedia, Citrate (Wikipedia)

LP14741-0   Citrate
Citrate testing is used to diagnose renal tubular acidosis and evaluate kidney stone disease. Acid-base balance plays a critical role in citrate excretion. In acidosis, increased citrate utilization occurs and causes reduced citrate excretion. In alkalosis, citrate excretion increases. Hypocitruria promotes the formation of calcium kidney stones because citrate normally binds urinary calcium as a soluble calcium citrate salt. Hypocitruria may also have a role in uric acid stone formation. Citrate excretion is impaired by acidosis, hypokalemia, urinary tract infection, and a high animal protein/high acid-ash content diet. Urine citrate levels may also be decreased with severe muscular activity, hypoparathyroidism, diabetes, and chronic renal failure. Urine citrate levels may be increased with high carbohydrate diet, estrogen therapy, and Vitamin D use. Information from emedicine, "Hypocitraturia," by George Bennett Stackhouse IV, MD, and Medline Plus, accessed 2006 10 25 Source: Regenstrief Institute

Fully-Specified Name

Component
Citrate
Property
SCnc
Time
Pt
System
Ser/Plas
Scale
Qn
Method

Basic Attributes

Class
CHEM
Type
Laboratory
First Released
Version 1.0k
Last Updated
Version 2.73 (MIN)
Order vs. Observation
Both
Common Test Rank Get Info
16080

Member of these Panels

LOINCLong Common Name
101455-4Mitochondrial metabolites panel - Serum or Plasma
35866-3Organic acids panel - Serum or Plasma

Member of these Groups Get Info

LOINC GroupGroup Name
LG43059-1Citrate|Pt|Ser/Plas

Language Variants Get Info

TagLanguageTranslation
cs-CZCzech (Czechia)Citrát:Látková koncentrace:Časový bod:Sérum/plazma:Kvantitativní:
de-DEGerman (Germany)Citrat:Stoffmengenkonzentration:Zeitpunkt:Serum oder Plasma:Quantitativ:
el-GRGreek (Greece)Κιτρικό:SCnc:Pt:Ορός/Πλάσμα:Qn:
Synonyms: CHEM Pt Qn SCnc Κιτρικό Ορός Ορός/Πλάσμα Πλάσμα
es-ARSpanish (Argentina)citrato:concentración de sustancia:punto en el tiempo:suero/plasma:cuantitativo:
es-ESSpanish (Spain)Citrato:Concentración de sustancia:Punto temporal:Suero o Plasma:Qn:
Synonyms: Cuantitativo
es-MXSpanish (Mexico)Citrato:Concentración de sustancias:Punto temporal:Suero o Plasma:Cuantitativo:
et-EEEstonian (Estonia)Tsitraat:SCnc:Pt:S/P:Qn:
Synonyms: Aine kontsentratsioon Juhuslik Kvantitatiivne Plasma Seerum Seerum või plasma
fr-CAFrench (Canada)Citrate:Concentration de substance:Temps ponctuel:Sérum/Plasma:Quantitatif:
fr-FRFrench (France)Citrate:Moles/Volume:Ponctuel:Sérum/Plasma:Numérique:
fr-BEFrench (Belgium)Citrate:Concentration de substance:Temps ponctuel:Sérum/Plasma:Quantitatif:
it-ITItalian (Italy)Citrato:SCnc:Pt:Siero/Plasma:Qn:
Synonyms: Chimica Concentrazione di Sostanza Plasma Punto nel tempo (episodio) Siero Siero o Plasma
ko-KRKorean (Korea, Republic Of)구연산:물질농도:검사시점:혈청/혈장:정량:
nl-NLDutch (Netherlands)citraat:mol/volume:moment:serum of plasma:kwantitatief:
pt-BRPortuguese (Brazil)Citrato:SCnc:Pt:Sor/Plas:Qn:
Synonyms: Citric acid; Substance concentration; Level; Point in time; Random; SerPl; SerPlas; SerP; Serum; SR; Plasma; Pl; Plsm; Quantitative; QNT; Quant; Quan; Chemistry
ru-RURussian (Russian Federation)Цитрат:МолКонц:ТчкВрм:Сыв/Плаз:Колич:
Synonyms: Количественный Молярность;Молярная объёмная концентрация Плазма Сыворотка Сыворотка или Плазма Точка во времени;Момент
tr-TRTurkish (Turkey)Sitrat:SubKons:Zmlı:Ser/Plaz:Kant:
uk-UAUkrainian (Ukraine)Цитрат:Молярна Концентрація:МоментЧасу:Сироватка/Плазма:Кількісно:
Synonyms: Chemistry; Citric acid; Level; Pl; Plasma; Plsm; Point in time; QNT; Quan; Quant; Quantitative; Random; SerP; SerPl; SerPlas; Serum; Serum or plasma; SR; Substance concentration
zh-CNChinese (China)柠檬酸:物质的量浓度:时间点:血清/血浆:定量型:
Synonyms: 克分子浓度;克分子浓度(单位体积);摩尔浓度;摩尔浓度(单位体积);物质的量浓度(单位体积) 化学;化学检验项目;化学检验项目类;化学类;化学试验;非刺激耐受型化学检验项目;非刺激耐受型化学检验项目类;非刺激耐受型化学试验;非刺激耐受型化学试验类 可用数量表示的;定量性;数值型;数量型;连续数值型标尺 时刻;随机;随意;瞬间 枸橼酸;枸橼酸根;枸橼酸盐;枸橼酸酯;柠檬酸根;柠檬酸盐;柠檬酸酯 血清或血浆

Example Units

UnitSource
umol/LExample UCUM Units
mcmol/LREGENSTRIEF

2524-7 Lactate [Moles/volume] in Serum or Plasma

Part Descriptions

LP15686-6   Lactate
Lactate is produced via the enzyme lactate dehydrogenase(LDH) during fermentation. Elevated urine lactic acid levels are found in patients with multiple carboxylase deficiency, lactic acidosis, dihydrolipoyl dehydrogenase deficiency, PDH complex (E1, E2,E3),oxidative phosphorylation and respiratory chain defects (e.g., MERRF, MELAS, Kearns-Sayre), Crebs acid cycle defects, gluconeogenesis defects (pyruvate carboxylase, fructose-1,6-dihphosphatase, glycogen storage I disorder), short-branched chain acyl-CoA DH deficiency, severe MAD deficiency, VLCAD deficiency, GA I ,other organic acidurias (MMA,PA,IVA), citrullinemia, glycerol kinase deficiency, HMG-CoA lyase deficiency, or EMA aciduria. (Information from: Kumps A, Duez P, Mardens Y. Metabolic, Nutritional, Iatrogenic, and Artifactual Sources of Urinary Organic Acids: A Comprehensive Table. Clinical Chemistry 2002, 48:708-717.) Source: Regenstrief Institute

LP15686-6   Lactate
Lactic acid is chiral and has two optical isomers. One is known as L-(+)-lactic acid or (S)-lactic acid and the other, its mirror image, is D-(−)-lactic acid or (R)-lactic acid. The L isomer is the biologic one. Copyright Text is available under the Creative Commons Attribution/Share-Alike License. See http://creativecommons.org/licenses/by-sa/3.0/ for details. Source: Wikipedia, Lactate

Fully-Specified Name

Component
Lactate
Property
SCnc
Time
Pt
System
Ser/Plas
Scale
Qn
Method

Basic Attributes

Class
CHEM
Type
Laboratory
First Released
Version 1.0
Last Updated
Version 2.73 (MIN)
Order vs. Observation
Both
Common Test Rank Get Info
298

Member of these Panels

LOINCLong Common Name
101656-7Lactate and pyruvate panel - Serum, Plasma or Blood
97759-5Magnesium and phosphate and lactate panel - Serum or Plasma
101455-4Mitochondrial metabolites panel - Serum or Plasma
35866-3Organic acids panel - Serum or Plasma

Member of these Groups Get Info

LOINC GroupGroup Name
LG48941-5Lactate|Pt|Ser/Plas
LG6039-4Lactate|SCnc|Pt|ANYBldSerPl

Language Variants Get Info

TagLanguageTranslation
cs-CZCzech (Czechia)Laktát:Látková koncentrace:Časový bod:Sérum/plazma:Kvantitativní:
de-ATGerman (Austria)Synonyms: Laktat
de-DEGerman (Germany)Lactat:Stoffmengenkonzentration:Zeitpunkt:Serum oder Plasma:Quantitativ:
Synonyms: Laktat
el-GRGreek (Greece)Γαλακτικό οξύ:SCnc:Pt:Ορός/Πλάσμα:Qn:
Synonyms: CHEM Pt Qn SCnc Γαλακτικό οξύ Ορός Ορός/Πλάσμα Πλάσμα
es-ARSpanish (Argentina)lactato:concentración de sustancia:punto en el tiempo:suero/plasma:cuantitativo:
es-ESSpanish (Spain)Lactato:Concentración de sustancia:Punto temporal:Suero o Plasma:Qn:
Synonyms: Cuantitativo
es-MXSpanish (Mexico)Lactato:Concentración de sustancias:Punto temporal:Suero o Plasma:Cuantitativo:
et-EEEstonian (Estonia)Laktaat:SCnc:Pt:S/P:Qn:
Synonyms: Aine kontsentratsioon Juhuslik Kvantitatiivne Plasma Seerum Seerum või plasma
fr-CAFrench (Canada)Lactate:Concentration de substance:Temps ponctuel:Sérum/Plasma:Quantitatif:
fr-FRFrench (France)Lactates:Moles/Volume:Ponctuel:Sérum/Plasma:Numérique:
fr-BEFrench (Belgium)Lactate:Concentration de substance:Temps ponctuel:Sérum/Plasma:Quantitatif:
it-ITItalian (Italy)Lattato:SCnc:Pt:Siero/Plasma:Qn:
Synonyms: Chimica Concentrazione di Sostanza Plasma Punto nel tempo (episodio) Siero Siero o Plasma
ko-KRKorean (Korea, Republic Of)젖산:물질농도:검사시점:혈청/혈장:정량:
nl-NLDutch (Netherlands)lactaat:mol/volume:moment:serum of plasma:kwantitatief:
pl-PLPolish (Poland)Mleczan:stężenie molowe:punkt w czasie:surowica lub osocze:ilościowy:
pt-BRPortuguese (Brazil)Lactato:SCnc:Pt:Sor/Plas:Qn:
Synonyms: Lact; 2-hydroxy-propionic acid; 2-hydroxy-propionate; Lactic acid; L-lactate; Substance concentration; Level; Point in time; Random; SerPl; SerPlas; SerP; Serum; SR; Plasma; Pl; Plsm; Quantitative; QNT; Quant; Quan; Chemistry
ru-RURussian (Russian Federation)Лактат:МолКонц:ТчкВрм:Сыв/Плаз:Колич:
Synonyms: Количественный Молярность;Молярная объёмная концентрация Плазма Сыворотка Сыворотка или Плазма Точка во времени;Момент
tr-TRTurkish (Turkey)Laktat:SubKons:Zmlı:Ser/Plaz:Kant:
uk-UAUkrainian (Ukraine)Лактат:Молярна Концентрація:МоментЧасу:Сироватка/Плазма:Кількісно:
Synonyms: 2-Hydroxypropanoic acid; 2-hydroxy-propionate; 2-hydroxy-propionic acid; Chemistry; Lact; Lactic acid; Level; L-lactate; Pl; Plasma; Plsm; Point in time; QNT; Quan; Quant; Quantitative; Random; SerP; SerPl; SerPlas; Serum; Serum or plasma; SR; Substance concentration; UniversalLabOrders
zh-CNChinese (China)乳酸:物质的量浓度:时间点:血清/血浆:定量型:
Synonyms: 2-羟基-丙酸;Lact;L-乳酸 克分子浓度;克分子浓度(单位体积);摩尔浓度;摩尔浓度(单位体积);物质的量浓度(单位体积) 化学;化学检验项目;化学检验项目类;化学类;化学试验;非刺激耐受型化学检验项目;非刺激耐受型化学检验项目类;非刺激耐受型化学试验;非刺激耐受型化学试验类 可用数量表示的;定量性;数值型;数量型;连续数值型标尺 时刻;随机;随意;瞬间 血清或血浆

Example Units

UnitSource
mmol/LExample UCUM Units
mmol/LREGENSTRIEF

75068-7 Malate [Moles/volume] in Serum or Plasma

Part Descriptions

LP18441-3   Malate
Malic acid is an organic compound with the formula HO2CCH2CHOHCO2H. This dicarboxylic acid is the active ingredient in many sour or tart foods. Malic acid is found mostly in unripe fruits.

The salts and esters of malic acid are known as malates. The malate anion is an intermediate in the citric acid cycle. Copyright Text is available under the Creative Commons Attribution/Share-Alike License. See http://creativecommons.org/licenses/by-sa/3.0/ for details. Source: Wikipedia, Wikipedia

Fully-Specified Name

Component
Malate
Property
SCnc
Time
Pt
System
Ser/Plas
Scale
Qn
Method

Basic Attributes

Class
CHEM
Type
Laboratory
First Released
Version 2.48
Last Updated
Version 2.52 (MIN)
Order vs. Observation
Both

Member of these Panels

LOINCLong Common Name
101455-4Mitochondrial metabolites panel - Serum or Plasma

Language Variants Get Info

TagLanguageTranslation
cs-CZCzech (Czechia)Malát:Látková koncentrace:Časový bod:Sérum/plazma:Kvantitativní:
el-GRGreek (Greece)Μηλικό:SCnc:Pt:Ορός/Πλάσμα:Qn:
Synonyms: CHEM Pt Qn SCnc Μηλικό Ορός Ορός/Πλάσμα Πλάσμα
es-ESSpanish (Spain)Malato:Concentración de sustancia:Punto temporal:Suero o Plasma:Qn:
Synonyms: Cuantitativo
es-MXSpanish (Mexico)Malato:Concentración de sustancias:Punto temporal:Suero o Plasma:Cuantitativo:
et-EEEstonian (Estonia)Malaat:SCnc:Pt:S/P:Qn:
Synonyms: Aine kontsentratsioon Juhuslik Kvantitatiivne Plasma Seerum Seerum või plasma
fr-CAFrench (Canada)Malate:Concentration de substance:Temps ponctuel:Sérum/Plasma:Quantitatif:
fr-FRFrench (France)Malate:Moles/Volume:Ponctuel:Sérum/Plasma:Numérique:
fr-BEFrench (Belgium)Malate:Concentration de substance:Temps ponctuel:Sérum/Plasma:Quantitatif:
it-ITItalian (Italy)Malate:SCnc:Pt:Siero/Plasma:Qn:
Synonyms: Chimica Concentrazione di Sostanza Plasma Punto nel tempo (episodio) Siero Siero o Plasma
nl-NLDutch (Netherlands)malaat:mol/volume:moment:serum of plasma:kwantitatief:
ru-RURussian (Russian Federation)Малат:МолКонц:ТчкВрм:Сыв/Плаз:Колич:
Synonyms: Количественный Молярность;Молярная объёмная концентрация Плазма Сыворотка Сыворотка или Плазма Точка во времени;Момент
tr-TRTurkish (Turkey)Malat:SubKons:Zmlı:Ser/Plaz:Kant:
zh-CNChinese (China)苹果酸:物质的量浓度:时间点:血清/血浆:定量型:
Synonyms: 克分子浓度;克分子浓度(单位体积);摩尔浓度;摩尔浓度(单位体积);物质的量浓度(单位体积) 化学;化学检验项目;化学检验项目类;化学类;化学试验;非刺激耐受型化学检验项目;非刺激耐受型化学检验项目类;非刺激耐受型化学试验;非刺激耐受型化学试验类 可用数量表示的;定量性;数值型;数量型;连续数值型标尺 时刻;随机;随意;瞬间 苹果酸根;苹果酸盐;苹果酸酯 血清或血浆

Example Units

UnitSource
umol/LExample UCUM Units

32338-6 Pyruvate [Moles/volume] in Serum or Plasma

Part Descriptions

LP15693-2   Pyruvate
Pyruvic acid (CH3COCOOH), an organic acid, is also a ketone and the simplest alpha-keto acid. The carboxylate (COOH) ion (anion) of pyruvic acid, CH3COCOO-, known as pyruvate, is a key intermediary in several metabolic pathways. It can be made from glucose through glycolysis and it supplies energy to living cells via the citric acid cycle. It can also be converted to carbohydrates via gluconeogenesis, fatty acids or generate energy through acetyl-CoA, the amino acid alanine, and ethanol. Copyright Text is available under the Creative Commons Attribution/Share-Alike License. See http://creativecommons.org/licenses/by-sa/3.0/ for details. Source: Wikipedia, Wikipedia

Fully-Specified Name

Component
Pyruvate
Property
SCnc
Time
Pt
System
Ser/Plas
Scale
Qn
Method

Basic Attributes

Class
CHEM
Type
Laboratory
First Released
Version 2.07
Last Updated
Version 2.73 (MIN)
Order vs. Observation
Both
Common Test Rank Get Info
9515

Member of these Panels

LOINCLong Common Name
101656-7Lactate and pyruvate panel - Serum, Plasma or Blood
101455-4Mitochondrial metabolites panel - Serum or Plasma
35866-3Organic acids panel - Serum or Plasma

Member of these Groups Get Info

LOINC GroupGroup Name
LG45784-2Pyruvate|Pt|Ser/Plas|87.054 g/mole
LG2278-2Pyruvate|SCnc|Pt|ANYBldSerPl

Language Variants Get Info

TagLanguageTranslation
cs-CZCzech (Czechia)Pyruvát:Látková koncentrace:Časový bod:Sérum/plazma:Kvantitativní:
de-ATGerman (Austria)Synonyms: Pyruvat
de-DEGerman (Germany)Pyruvat:Stoffmengenkonzentration:Zeitpunkt:Serum oder Plasma:Quantitativ:
el-GRGreek (Greece)Πυροσταφυλικό οξύ:SCnc:Pt:Ορός/Πλάσμα:Qn:
Synonyms: CHEM Pt Qn SCnc Ορός Ορός/Πλάσμα Πλάσμα Πυροσταφυλικό οξύ
es-ARSpanish (Argentina)piruvato:concentración de sustancia:punto en el tiempo:suero/plasma:cuantitativo:
es-ESSpanish (Spain)Piruvato:Concentración de sustancia:Punto temporal:Suero o Plasma:Qn:
Synonyms: Cuantitativo
es-MXSpanish (Mexico)Piruvato:Concentración de sustancias:Punto temporal:Suero o Plasma:Cuantitativo:
et-EEEstonian (Estonia)Püruvaat:SCnc:Pt:S/P:Qn:
Synonyms: Aine kontsentratsioon Juhuslik Kvantitatiivne Plasma Seerum Seerum või plasma
fr-CAFrench (Canada)Pyruvate:Concentration de substance:Temps ponctuel:Sérum/Plasma:Quantitatif:
fr-FRFrench (France)Pyruvate:Moles/Volume:Ponctuel:Sérum/Plasma:Numérique:
fr-BEFrench (Belgium)Pyruvate:Concentration de substance:Temps ponctuel:Sérum/Plasma:Quantitatif:
it-ITItalian (Italy)Piruvato:SCnc:Pt:Siero/Plasma:Qn:
Synonyms: Chimica Concentrazione di Sostanza Plasma Punto nel tempo (episodio) Siero Siero o Plasma
ko-KRKorean (Korea, Republic Of)피루브산염:물질농도:검사시점:혈청/혈장:정량:
nl-NLDutch (Netherlands)pyruvaat:mol/volume:moment:serum of plasma:kwantitatief:
pt-BRPortuguese (Brazil)Piruvato:SCnc:Pt:Sor/Plas:Qn:
Synonyms: Pyruvic acid; Substance concentration; Level; Point in time; Random; SerPl; SerPlas; SerP; Serum; SR; Plasma; Pl; Plsm; Quantitative; QNT; Quant; Quan; Chemistry
ru-RURussian (Russian Federation)Пируват:МолКонц:ТчкВрм:Сыв/Плаз:Колич:
Synonyms: Количественный Молярность;Молярная объёмная концентрация Плазма Сыворотка Сыворотка или Плазма Точка во времени;Момент
tr-TRTurkish (Turkey)Piruvat:SubKons:Zmlı:Ser/Plaz:Kant:
uk-UAUkrainian (Ukraine)Піруват:Молярна Концентрація:МоментЧасу:Сироватка/Плазма:Кількісно:
Synonyms: Chemistry; Level; Pl; Plasma; Plsm; Point in time; Pyruvic acid; QNT; Quan; Quant; Quantitative; Random; SerP; SerPl; SerPlas; Serum; Serum or plasma; SR; Substance concentration
zh-CNChinese (China)丙酮酸:物质的量浓度:时间点:血清/血浆:定量型:
Synonyms: 丙酮酸盐;丙酮酸酯 克分子浓度;克分子浓度(单位体积);摩尔浓度;摩尔浓度(单位体积);物质的量浓度(单位体积) 化学;化学检验项目;化学检验项目类;化学类;化学试验;非刺激耐受型化学检验项目;非刺激耐受型化学检验项目类;非刺激耐受型化学试验;非刺激耐受型化学试验类 可用数量表示的;定量性;数值型;数量型;连续数值型标尺 时刻;随机;随意;瞬间 血清或血浆

Example Units

UnitSource
mmol/LExample UCUM Units
mmol/LeCHN

35871-3 Succinate [Moles/volume] in Serum or Plasma

Part Descriptions

LP15871-4   Succinate
Succinic acid (IUPAC systematic name:butanedioic acid ; historically known as spirit of amber) is a dicarboxylic acid. At room temperature, pure succinic acid is a solid that forms colorless, odorless prisms. It has a melting point of 185°C and a boiling point of 235°C. The anion, succinate, is a component of the citric acid cycle and is capable of donating electrons to the electron transfer chain via the following reaction: succinate + FAD †' fumarate + FADH2 This is catalysed by the enzyme succinate dehydrogenase (or complex II of the mitochondrial ETC). The complex is a 4 subunit membrane-bound lipoprotein which couples the oxidation of succinate to the reduction of ubiquinone. Intermediate electron carriers are FAD and three Fe2 S2 clusters part of subunit B. Esters of succinic acid are called dialkyl succinates. Copyright Text is available under the Creative Commons Attribution/Share-Alike License. See http://creativecommons.org/licenses/by-sa/3.0/ for details. Source: Wikipedia, Succinate (Wikipedia)

LP15871-4   Succinate
Succinic acid is a dicarboxylic acid that increases due to a riboflavin or coenzyme Q-10 deficiency or bacterial conversion of glutamine to succicinic acid in the gastrointestinal tract. Elevated levels may be due to succinic semialdehyde dehydrogenase deficiency, malonic acidura, or fumarase deficiency. Source: Regenstrief Institute

Fully-Specified Name

Component
Succinate
Property
SCnc
Time
Pt
System
Ser/Plas
Scale
Qn
Method

Basic Attributes

Class
CHEM
Type
Laboratory
First Released
Version 2.13
Last Updated
Version 2.73 (MIN)
Order vs. Observation
Both
Common Test Rank Get Info
9521

Member of these Panels

LOINCLong Common Name
101455-4Mitochondrial metabolites panel - Serum or Plasma
35866-3Organic acids panel - Serum or Plasma

Language Variants Get Info

TagLanguageTranslation
cs-CZCzech (Czechia)Sukcinát:Látková koncentrace:Časový bod:Sérum/plazma:Kvantitativní:
el-GRGreek (Greece)Σουκινικό άλας:SCnc:Pt:Ορός/Πλάσμα:Qn:
Synonyms: CHEM Pt Qn SCnc Ορός Ορός/Πλάσμα Πλάσμα Σουκινικό άλας
es-ARSpanish (Argentina)succinato:concentración de sustancia:punto en el tiempo:suero/plasma:cuantitativo:
es-ESSpanish (Spain)Succinato:Concentración de sustancia:Punto temporal:Suero o Plasma:Qn:
Synonyms: Cuantitativo
es-MXSpanish (Mexico)Succinato:Concentración de sustancias:Punto temporal:Suero o Plasma:Cuantitativo:
et-EEEstonian (Estonia)Suksinaat:SCnc:Pt:S/P:Qn:
Synonyms: Aine kontsentratsioon Juhuslik Kvantitatiivne Plasma Seerum Seerum või plasma
fr-CAFrench (Canada)Succinate:Concentration de substance:Temps ponctuel:Sérum/Plasma:Quantitatif:
fr-FRFrench (France)Succinate:Moles/Volume:Ponctuel:Sérum/Plasma:Numérique:
fr-BEFrench (Belgium)Succinate:Concentration de substance:Temps ponctuel:Sérum/Plasma:Quantitatif:
it-ITItalian (Italy)Succinato:SCnc:Pt:Siero/Plasma:Qn:
Synonyms: Chimica Concentrazione di Sostanza Plasma Punto nel tempo (episodio) Siero Siero o Plasma
ko-KRKorean (Korea, Republic Of)숙신산염:물질농도:검사시점:혈청/혈장:정량:
nl-NLDutch (Netherlands)succinaat:mol/volume:moment:serum of plasma:kwantitatief:
pt-BRPortuguese (Brazil)Succinato:SCnc:Pt:Sor/Plas:Qn:
Synonyms: Butanedioic acid; Butanedioate; Succinic acid; Substance concentration; Level; Point in time; Random; SerPl; SerPlas; SerP; Serum; SR; Plasma; Pl; Plsm; Quantitative; QNT; Quant; Quan; Chemistry
ru-RURussian (Russian Federation)Сукцинат:МолКонц:ТчкВрм:Сыв/Плаз:Колич:
Synonyms: Количественный Молярность;Молярная объёмная концентрация Плазма Сыворотка Сыворотка или Плазма Точка во времени;Момент
tr-TRTurkish (Turkey)Süksinat:SubKons:Zmlı:Ser/Plaz:Kant:
uk-UAUkrainian (Ukraine)Сукцинат:Молярна Концентрація:МоментЧасу:Сироватка/Плазма:Кількісно:
Synonyms: Butanedioate; Butanedioic acid; Chemistry; Level; Pl; Plasma; Plsm; Point in time; QNT; Quan; Quant; Quantitative; Random; SerP; SerPl; SerPlas; Serum; Serum or plasma; SR; Substance concentration; Succinic acid
zh-CNChinese (China)琥珀酸:物质的量浓度:时间点:血清/血浆:定量型:
Synonyms: 丁二酸;丁二酸根;丁二酸盐;丁二酸酯;琥珀酸根;琥珀酸盐;琥珀酸酯 克分子浓度;克分子浓度(单位体积);摩尔浓度;摩尔浓度(单位体积);物质的量浓度(单位体积) 化学;化学检验项目;化学检验项目类;化学类;化学试验;非刺激耐受型化学检验项目;非刺激耐受型化学检验项目类;非刺激耐受型化学试验;非刺激耐受型化学试验类 可用数量表示的;定量性;数值型;数量型;连续数值型标尺 时刻;随机;随意;瞬间 血清或血浆

Example Units

UnitSource
umol/LExample UCUM Units
mcmol/LREGENSTRIEF